CHiP Network Congenital Heart Journal Watch – October -2019- Archive

Pediatric Cardiology Featured Articles

Pediatric Cardiology Reviews of August 2019 Manuscripts

Pediatric Cardiology Reviews of August 2019 Manuscripts

mDixon ECG-gated 3-dimensional cardiovascular magnetic resonance angiography in patients with congenital cardiovascular disease.
Kourtidou S, Jones MR, Moore RA, Tretter JT, Ollberding NJ, Crotty EJ, Rattan MS, Fleck RJ, Taylor MD.
J Cardiovasc Magn Reson. 2019 Aug 8;21(1):52. doi: 10.1186/s12968-019-0554-3.
PMID: 31391061 Free PMC Article
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Take Home Points:
• modified Dixon (mDixon) 3D cardiovascular magnetic resonance angiography (CMRA) demonstrates reduced artefact burden and better delineation of head and neck vessels as well as pulmonary veins compared to conventional 3D balanced steady state free precession CMRA.
• mDixon acquisitions might help improving diagnostics in pediatric and adult congenital heart disease patients.

Comment from Dr. Inga Voges (Kiel, Germany), section editor of Pediatric Cardiology Journal Watch: This is a very interesting retrospective cardiovascular magnetic resonance imaging study comparing conventional contrast-enhanced cardiovascular magnetic resonance angiography (CE-CMRA) and non-contrast angiographic techniques (1. conventional 3D balanced steady state free precession CMRA; 3D bSSFP and 2. modified Dixon CMRA; mDixon). As reported by the authors, Dixon-based methods are less susceptible to field inhomogeneities.
24 cardiovascular magnetic resonance (CMR) scans were included. Each patient underwent CE-CMRA followed by 3D bSSFP and mDixon acquisitions. The water images of the mDixon sequence were used for the final analysis.
CMR studies were reviewed by two independent observers who assessed the overall image quality and compared the contrast-to-noise ratio (CNR) and signal-to-noise ratio (SNR) in the myocardium and blood pool. Furthermore, vascular measurements on multiplanar reformatted images were performed and the scan time was recorded. CE-CMRA data were not included in the analysis of SNR, CNR, vascular measurements and scanning time.
The authors found that the image quality of the water images of the mDixon sequence were comparable and for some structures better compared to 3DSSFP images. Bland-Altman analysis revealed acceptable agreement for image quality scores between all three techniques. mDixon images were better in depicting the entire field of view compared to 3D bSSFP and CE-CMRA and demonstrated a better vessel wall sharpness whereas 3D bSSFP images allowed a better intracardiac anatomy and myocardium-blood pool definition. There was no difference for CNR and SNR between 3D bSSFP and mDixon acquisitions. Artefact burden was less in mDixon compared to 3D bSSFP and CE-CMRA. Eight different vessel cross-sectional diameters were measured on 3D bSSFP and mDixon sequences and the analysis showed less than 10% measurement difference between both techniques (Table 3). The scanning time for 3D SSFP and mDixon acquisitions was comparable.
In general, this nice study demonstrates that mDixon might be a superior to the conventionally used 3D SSFP sequence as it also offers an excellent depiction of the cardiovascular anatomy even in complex anatomies with the advantage of reduced artefact burden.

Mental health care for parents of babies with congenital heart disease during intensive care unit admission: Systematic review and statement of best practice.
Kasparian NA, Kan JM, Sood E, Wray J, Pincus HA, Newburger JW.
Early Hum Dev. 2019 Aug 24:104837. doi: 10.1016/j.earlhumdev.2019.104837. [Epub ahead of print]
PMID: 31455569

Take Home Points:
• Congenital heart disease is associated with psychological stress for mothers, fathers and their infants.
• In four of the five trials included, mental health interventions demonstrated some efficacy in reducing maternal anxiety. Mixed results were found for maternal depression and infant feeding.
• Mental health interventions for parents of infants admitted to the intensive care unit (ICU) did not improve quality of life, physical health or infant length of stay.
• An integrated approach is needed to address mental health issues in parents of infants with CHD admitted to the intensive care unit.

Commentary from Dr. Charlotte Van Dorn (Rochester, MN), section editor of Pediatric Cardiology Journal Watch: This is a systematic literature review and statement of best practice addressing mental health interventions and resources for parents of children born with congenital heart disease admitted to the intensive care unit (ICU). The objective of this review was to identify and critically appraise evidence on the efficacy and cost-effectiveness of mental health interventions delivered in the ICU as well as to develop guidelines for advancing health policy and practice.
There are many recognized psychologic and social stressors experienced by parents and infants within the ICU. Up to 30% of parents of infants with complex CHD experience symptoms consistent with post-traumatic stress disorder, another 25-50% experience depression or anxiety and up to 80% report severe psychological distress. Parents with higher distress report poorer physical health, high health service use, more suicidal ideation, and poorer quality of life.

Methods included a search of 6 electronic databases. A total of 289 articles were identified but only 5 were included in this review.

Results: A total of 339 participants (311 mothers, 28 fathers) were included. Interventions varied widely across the studies included. There was high risk of bias in the 3 non-randomized controlled trials.
Discussion: This systematic review of 289 articles resulted in a limited database for analysis and therefore should be approached with caution. Integrated psychotherapeutic interventions within the ICU environment are hypothesized to prevent or minimize severe psychosocial distress in parents of medically fragile infants. Four of the five identified trials demonstrated efficacy in reducing maternal anxiety; however, only a single trial demonstrated a positive effect of psychological intervention for parental depression. Further analysis of the 5 studies included in this review did demonstrate preliminary results showing positive effects of psychosocial interventions on maternal coping, mother-infant attachment, parenting confidence, family function, and communication. In this small review, there was no evidence for efficacy for family quality of life or intensive care unit length of stay. A single trial demonstrated some benefit for infant mental development at 6-months; however, this is difficult to generalize in a complex CHD population given the risks for neurodevelopmental abnormalities.
Limitations: There were multiple limitations to include in this systematic review including small sample size, single center recruitment, and lack of blinding. Some of the included studies relied on self-administered, symptom-based measures without reference to established cut-offs to provide indications of psychological change resulting in the risk for serious bias. There was also substantial variation in the interventions provided across groups.
Next steps: Mental health interventions are needed for parents of infants with CHD and should begin in the ICU. Structured psychosocial screening and a mental health assessment using validated tools is an important first step. This should be followed by an integrated and multidisciplinary approach to improve parental mental health care and therefore outcomes of this vulnerable population.

 

Pediatric cardiology August 2019

  1. Altered 4-D magnetic resonance imaging flow characteristics in complex congenital aortic arch repair.

Desai LP, Berhane H, Husain N, Robinson JD, Rigsby CK, Markl M.

Pediatr Radiol. 2019 Aug 31. doi: 10.1007/s00247-019-04507-0. [Epub ahead of print]

PMID: 31473788

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  1. Development of a clinician-parent home care education intervention.

Lane B, Hanke SP, Giambra B, Madsen NL, Staveski SL.

Cardiol Young. 2019 Aug 30:1-6. doi: 10.1017/S1047951119001318. [Epub ahead of print]

PMID: 31469062

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  1. Exploring Shared Susceptibility between Two Neural Crest Cells Originating Conditions: Neuroblastoma and Congenital Heart Disease.

Testori A, Lasorsa VA, Cimmino F, Cantalupo S, Cardinale A, Avitabile M, Limongelli G, Russo MG, Diskin S, Maris J, Devoto M, Keavney B, Cordell HJ, Iolascon A, Capasso M.

Genes (Basel). 2019 Aug 30;10(9). pii: E663. doi: 10.3390/genes10090663.

PMID: 31480262 Free Article

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  1. Early Neurodevelopmental Outcomes in Children with Hypoplastic Left Heart Syndrome and Related Anomalies After Hybrid Procedure.

Khalid OM, Harrison TM.

Pediatr Cardiol. 2019 Aug 30. doi: 10.1007/s00246-019-02191-3. [Epub ahead of print]

PMID: 31471627

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  1. Costello Syndrome.

Gripp KW, Rauen KA.

In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019.

2006 Aug 29 [updated 2019 Aug 29].

PMID: 20301680 Free Books & Documents

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  1. Motion robust respiratory-resolved 3D radial flow MRI and its application in neonatal congenital heart disease.

Schrauben EM, Lim JM, Goolaub DS, Marini D, Seed M, Macgowan CK.

Magn Reson Med. 2019 Aug 29. doi: 10.1002/mrm.27945. [Epub ahead of print]

PMID: 31464030

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  1. Minimum Travel Distance Among Publicly Insured Infants with Severe Congenital Heart Disease: Potential Impact of In-state Restrictions.

Woo JL, Anderson BR, Gruenstein D, Conti R, Chua KP.

Pediatr Cardiol. 2019 Aug 28. doi: 10.1007/s00246-019-02193-1. [Epub ahead of print]

PMID: 31463514

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  1. Comprehensive literature review of anomalies of the coronary arteries.

Harky A, Noshirwani A, Karadakhy O, Ang J.

J Card Surg. 2019 Aug 26. doi: 10.1111/jocs.14228. [Epub ahead of print] Review.

PMID: 31449703

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  1. Estimating the effect size of the 15Q11.2 BP1-BP2 deletion and its contribution to neurodevelopmental symptoms: recommendations for practice.

Jønch AE, Douard E, Moreau C, Van Dijck A, Passeggeri M, Kooy F, Puechberty J, Campbell C, Sanlaville D, Lefroy H, Richetin S, Pain A, Geneviève D, Kini U, Le Caignec C, Lespinasse J, Skytte AB, Isidor B, Zweier C, Caberg JH, Delrue MA, Møller RS, Bojesen A, Hjalgrim H, Brasch-Andersen C, Lemyre E, Ousager LB, Jacquemont S; 15q11.2 Working Group.

J Med Genet. 2019 Aug 26. pii: jmedgenet-2018-105879. doi: 10.1136/jmedgenet-2018-105879. [Epub ahead of print]

PMID: 31451536 Free Article

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  1. Mental health care for parents of babies with congenital heart disease during intensive care unit admission: Systematic review and statement of best practice.

Kasparian NA, Kan JM, Sood E, Wray J, Pincus HA, Newburger JW.

Early Hum Dev. 2019 Aug 24:104837. doi: 10.1016/j.earlhumdev.2019.104837. [Epub ahead of print]

PMID: 31455569

SMyocarditis in the pediatric population: A review.

Dasgupta S, Iannucci G, Mao C, Clabby M, Oster ME.

Congenit Heart Dis. 2019 Aug 21. doi: 10.1111/chd.12835. [Epub ahead of print]

PMID: 31432626

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  1. Brain Injury in Infants with Critical Congenital Heart Disease: Insights from Two Clinical Cohorts with Different Practice Approaches.

Claessens NHP, Chau V, de Vries LS, Jansen NJG, Au-Young SH, Stegeman R, Blaser S, Shroff M, Haas F, Marini D, Breur JMPJ, Seed M, Benders MJNL, Miller SP.

J Pediatr. 2019 Aug 23. pii: S0022-3476(19)30869-8. doi: 10.1016/j.jpeds.2019.07.017. [Epub ahead of print]

PMID: 31451185

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  1. Dual-source computed tomography coronary artery imaging in children.

Secinaro A, Curione D, Mortensen KH, Santangelo TP, Ciancarella P, Napolitano C, Del Pasqua A, Taylor AM, Ciliberti P.

Pediatr Radiol. 2019 Aug 22. doi: 10.1007/s00247-019-04494-2. [Epub ahead of print]

PMID: 31440884

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  1. Myocarditis in the pediatric population: A review.

Dasgupta S, Iannucci G, Mao C, Clabby M, Oster ME.

Congenit Heart Dis. 2019 Aug 21. doi: 10.1111/chd.12835. [Epub ahead of print]

PMID: 31432626

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  1. Delivery room asphyxia in neonates with ductal-dependent congenital heart disease: a retrospective cohort study.

Boos V, Kocjancic L, Berger F, Bührer C.

J Perinatol. 2019 Aug 21. doi: 10.1038/s41372-019-0474-y. [Epub ahead of print]

PMID: 31434996

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  1. Identification of risk factors affecting catch-up growth after infant congenital heart disease surgery: rationale and design of a multicentre prospective cohort study in China.

Li L, Li K, An C, Fan J, Guo C, Liang S, Guo Y, Xia H, Chen X, Zhu Y, Hu C, Si W, Liang H, Cui Y.

BMJ Open. 2019 Aug 20;9(8):e030084. doi: 10.1136/bmjopen-2019-030084.

PMID: 31434778 Free PMC Article

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  1. Comparison of Two Measurement Devices for Pulse Wave Velocity in Children: Which Tool Is Useful to Detect Vascular Alterations Caused by Overweight?

Elmenhorst J, Weberruss H, Mayr M, Pfister K, Oberhoffer R.

Front Pediatr. 2019 Aug 20;7:334. doi: 10.3389/fped.2019.00334. eCollection 2019.

PMID: 31482076 Free PMC Article

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  1. Circulating plasma circular RNAs as novel diagnostic biomarkers for congenital heart disease in children.

Wu J, Li J, Liu H, Yin J, Zhang M, Yu Z, Miao H.

J Clin Lab Anal. 2019 Aug 20:e22998. doi: 10.1002/jcla.22998. [Epub ahead of print]

PMID: 31429492

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  1. Feasibility study assessing equitable delivery of newborn pulse oximetry screening in New Zealand’s midwifery-led maternity setting.

Cloete E, Gentles TL, Dixon LA, Webster DR, Agnew JD, Davidkova S, Alsweiler JM, Rogers J, Bloomfield FH; Pulse Oximetry Screening Steering Committee.

BMJ Open. 2019 Aug 18;9(8):e030506. doi: 10.1136/bmjopen-2019-030506.

PMID: 31427341 Free PMC Article

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  1. First-Year Outcomes of Critical Congenital Heart Disease Screening in Maryland.

Badawi D, Watson J, Maschke S, Reid L.

Glob Pediatr Health. 2019 Aug 18;6:2333794X19868226. doi: 10.1177/2333794X19868226. eCollection 2019.

PMID: 31453268 Free PMC Article

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  1. Increased risk of pulmonary hypertension following premature birth.

Naumburg E, Söderström L.

BMC Pediatr. 2019 Aug 17;19(1):288. doi: 10.1186/s12887-019-1665-6.

PMID: 31421674 Free PMC Article

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  1. Guideline implementation and early risk assessment in pulmonary arterial hypertension associated with congenital heart disease: A retrospective cohort study.

Deng X, Jin B, Li S, Li Y, Zhou H, Wu Y, Yan M, Hu Y, Qiu Q, Zhang G, Zheng X.

Clin Respir J. 2019 Aug 16. doi: 10.1111/crj.13076. [Epub ahead of print]

PMID: 31419027

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  1. Spontaneous Closure Rates of Ventricular Septal Defects (6,750 Consecutive Neonates).

Zhao QM, Niu C, Liu F, Wu L, Ma XJ, Huang GY.

Am J Cardiol. 2019 Aug 15;124(4):613-617. doi: 10.1016/j.amjcard.2019.05.022. Epub 2019 May 25.

PMID: 31208700

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  1. Meaningful and feasible composite clinical worsening definitions in paediatric pulmonary arterial hypertension: An analysis of the TOPP registry.

Beghetti M, Brand M, Berger RMF, Humpl T, Wheeler JG, Ivy DD, Bonnet D; TOPP investigators.

Int J Cardiol. 2019 Aug 15;289:110-115. doi: 10.1016/j.ijcard.2019.04.062. Epub 2019 Apr 25.

PMID: 31072635 Free Article

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  1. Left ventricular mass estimation by real-time 3D echocardiography favourably competes with CMR in congenital left ventricular disease.

Michel M, Shabanah W, Körperich H, Kelter-Klöpping A, Entenmann A, Racolta A, Laser KT.

Sci Rep. 2019 Aug 15;9(1):11888. doi: 10.1038/s41598-019-48375-y.

PMID: 31417137 Free PMC Article

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  1. A case report of T-box 1 mutation causing phenotypic features of chromosome 22q11.2 deletion syndrome.

Haddad RA, Clines GA, Wyckoff JA.

Clin Diabetes Endocrinol. 2019 Aug 13;5:13. doi: 10.1186/s40842-019-0087-6. eCollection 2019.

PMID: 31428446 Free PMC Article

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  1. Hypoplastic left heart syndrome: From bedside to bench and back.

Saraf A, Book WM, Nelson TJ, Xu C.

J Mol Cell Cardiol. 2019 Aug 13;135:109-118. doi: 10.1016/j.yjmcc.2019.08.005. [Epub ahead of print] Review.

PMID: 31419439

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  1. A multi-national trial of a direct oral anticoagulant in children with cardiac disease: Design and rationale of the Safety of ApiXaban On Pediatric Heart disease On the preventioN of Embolism (SAXOPHONE) study.

Payne RM, Burns KM, Glatz AC, Li D, Li X, Monagle P, Newburger JW, Swan EA, Wheaton O, Male C; Pediatric Heart Network Investigators.

Am Heart J. 2019 Aug 9;217:52-63. doi: 10.1016/j.ahj.2019.08.002. [Epub ahead of print]

PMID: 31493728

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  1. Detrimental Effects of Chemotherapy on Human Coronary Microvascular Function.

Hader SN, Zinkevich NS, Norwood Toro LE, Kriegel AJ, Kong A, Freed JK, Gutterman DD, Beyer AM.

Am J Physiol Heart Circ Physiol. 2019 Aug 9. doi: 10.1152/ajpheart.00370.2019. [Epub ahead of print]

PMID: 31397169

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  1. Trajectory of right ventricular indices is an early predictor of outcomes in hypoplastic left heart syndrome.

Kim AS, Witzenburg CM, Conaway M, Vergales JE, Holmes JW, L’Ecuyer TJ, Dean PN.

Congenit Heart Dis. 2019 Aug 8. doi: 10.1111/chd.12834. [Epub ahead of print]

PMID: 31393088

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Select item 31440271

 

  1. Efficient Mining of Variants From Trios for Ventricular Septal Defect Association Study.

Jiang P, Hu Y, Wang Y, Zhang J, Zhu Q, Bai L, Tong Q, Li T, Zhao L.

Front Genet. 2019 Aug 8;10:670. doi: 10.3389/fgene.2019.00670. eCollection 2019.

PMID: 31440271 Free PMC Article

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  1. mDixon ECG-gated 3-dimensional cardiovascular magnetic resonance angiography in patients with congenital cardiovascular disease.

Kourtidou S, Jones MR, Moore RA, Tretter JT, Ollberding NJ, Crotty EJ, Rattan MS, Fleck RJ, Taylor MD.

J Cardiovasc Magn Reson. 2019 Aug 8;21(1):52. doi: 10.1186/s12968-019-0554-3.

PMID: 31391061 Free PMC Article

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Select item 31402138

 

  1. The Impact of Neurobehavior on Feeding Outcomes in Neonates with Congenital Heart Disease.

Gakenheimer-Smith L, Glotzbach K, Ou Z, Presson AP, Puchalski M, Jones C, Lambert L, Delgado-Corcoran C, Eckhauser A, Miller T.

J Pediatr. 2019 Aug 8. pii: S0022-3476(19)30811-X. doi: 10.1016/j.jpeds.2019.06.047. [Epub ahead of print]

PMID: 31402138

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  1. Highlights of Current Research in Congenital Heart Disease: Presenting Abstracts From the 2019 Congenital Cardiac Anesthesia Society (CCAS) Annual Meeting.

Latham GJ.

Semin Cardiothorac Vasc Anesth. 2019 Aug 8:1089253219867696. doi: 10.1177/1089253219867696. [Epub ahead of print] No abstract available.

PMID: 31390945

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  1. Congenital Hypothyroidism: 8-Year Experience Using 2 Newborn Screens in Alabama.

Pitts L, McCormick W, Mick GJ.

Horm Res Paediatr. 2019 Aug 7:1-10. doi: 10.1159/000501395. [Epub ahead of print]

PMID: 31390650

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  1. Enhancing efficiency and scientific impact of a clinical trials network: the Pediatric Heart Network Integrated CARdiac Data and Outcomes (iCARD) Collaborative.

Pasquali SK, Kaltman JR, Gaynor JW, McCrindle BW, Newburger JW, Anderson BR, Scheurer MA, Pinto NM, Anderson JB, Oster ME, Jacobs JP, Marino BS, Mery CM, Pearson GD.

Cardiol Young. 2019 Aug 6:1-6. doi: 10.1017/S104795111900163X. [Epub ahead of print]

PMID: 31385565

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  1. The Functional Polymorphism R129W in the BVES Gene Is Associated with Sporadic Tetralogy of Fallot in the Han Chinese Population.

Shi Y, Li Y, Wang Y, Zhuang J, Wang H, Hu M, Mo X, Yue S, Chen Y, Fan X, Chen J, Cai W, Zhu X, Wan Y, Zhong Y, Ye X, Li F, Zhou Z, Dai G, Luo R, Ocorr K, Jiang Z, Li X, Zhu P, Wu X, Yuan W.

Genet Test Mol Biomarkers. 2019 Aug 6. doi: 10.1089/gtmb.2019.0085. [Epub ahead of print]

PMID: 31386585

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  1. RIKADA Study Reveals Risk Factors in Pediatric Primary Cardiomyopathy.

Al-Wakeel-Marquard N, Degener F, Herbst C, Kühnisch J, Dartsch J, Schmitt B, Kuehne T, Messroghli D, Berger F, Klaassen S.

J Am Heart Assoc. 2019 Aug 6;8(15):e012531. doi: 10.1161/JAHA.119.012531. Epub 2019 Jul 23.

PMID: 31333075 Free Article

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  1. Treatment With Tetrahydrobiopterin Improves White Matter Maturation in a Mouse Model for Prenatal Hypoxia in Congenital Heart Disease.

Romanowicz J, Leonetti C, Dhari Z, Korotcova L, Ramachandra SD, Saric N, Morton PD, Bansal S, Cheema A, Gallo V, Jonas RA, Ishibashi N.

J Am Heart Assoc. 2019 Aug 6;8(15):e012711. doi: 10.1161/JAHA.119.012711. Epub 2019 Jul 23.

PMID: 31331224 Free Article

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  1. Third time lucky: challenging secundum atrial septal defect.

Ordoñez MV, Moharem-Elgamal S, Bedair R.

Cardiol Young. 2019 Aug 5:1-4. doi: 10.1017/S1047951119001677. [Epub ahead of print]

PMID: 31379319

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  1. Left ventricular non-compaction in a child with bicuspid aortic valve and aortic coarctation.

Karatza A, Mylonas KS, Tzifa A.

Cardiol Young. 2019 Aug 5:1-3. doi: 10.1017/S1047951119001707. [Epub ahead of print]

PMID: 31379312

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  1. CHIP-Family intervention to improve the psychosocial well-being of young children with congenital heart disease and their families: results of a randomised controlled trial.

van der Mheen M, Meentken MG, van Beynum IM, van der Ende J, van Galen E, Zirar A, Aendekerk EWC, van den Adel TPL, Bogers AJJC, McCusker CG, Hillegers MHJ, Helbing WA, Utens EMWJ.

Cardiol Young. 2019 Aug 5:1-11. doi: 10.1017/S1047951119001732. [Epub ahead of print]

PMID: 31378215

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  1. Hospital-Acquired Pressure Injuries in Children With Congenital Heart Disease: Prevalence and Associated Factors.

Kulik LA, Hasbani NR, Stellar JJ, Quigley SM, Shelley SS, Wypij D, Curley MAQ; for Braden QD Study Group.

Pediatr Crit Care Med. 2019 Aug 5. doi: 10.1097/PCC.0000000000002077. [Epub ahead of print]

PMID: 31385861

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  1. Impact of feeding mode on neurodevelopmental outcome in infants and children with congenital heart disease.

Holst LM, Serrano F, Shekerdemian L, Ravn HB, Guffey D, Ghanayem NS, Monteiro S.

Congenit Heart Dis. 2019 Aug 2. doi: 10.1111/chd.12827. [Epub ahead of print]

PMID: 31373176

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  1. Cardiac rhabdomyomas with atrial septal defect and tricuspid insufficiency: A case report.

Wu C, Wang Y, Su W, Xia J, Dong N, Wang G.

J Card Surg. 2019 Aug 2. doi: 10.1111/jocs.14191. [Epub ahead of print]

PMID: 31374583

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  1. The expression of survivin in irreversible pulmonary arterial hypertension rats and its value in evaluating the reversibility of pulmonary arterial hypertension secondary to congenital heart disease.

Li G, Zhang H, Zhao L, Zhang Y, Yan D, Liu Y, Su J, Fan X.

Pulm Circ. 2019 Aug 2;9(3):2045894019859480. doi: 10.1177/2045894019859480. eCollection 2019 Jul-Sep.

PMID: 31428312 Free PMC Article

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  1. Glycogen Storage Disease Type IV.

Magoulas PL, El-Hattab AW.

In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019.

2013 Jan 3 [updated 2019 Aug 1].

PMID: 23285490 Free Books & Documents

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  1. MCP-1 promotes detrimental cardiac physiology, pulmonary edema, and death in the cpk model of polycystic kidney disease.

Salah SM, Meisenheimer JD, Rao R, Peda JD, Wallace DP, Foster D, Li X, Li X, Zhou X, Vallejo JA, Wacker MJ, Fields TA, Swenson-Fields KI.

Am J Physiol Renal Physiol. 2019 Aug 1;317(2):F343-F360. doi: 10.1152/ajprenal.00240.2018. Epub 2019 May 15.

PMID: 31091126

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  1. Accuracy of a portable pulse oximeter in monitoring hypoxemic infants with cyanotic heart disease.

Harris BU, Stewart S, Verma A, Hoen H, Stein ML, Wright G, Ramamoorthy C.

Cardiol Young. 2019 Aug;29(8):1025-1029. doi: 10.1017/S1047951119001355. Epub 2019 Jul 15.

PMID: 31304897

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Select item 31288878

 

  1. Elevated plasma Pim-1 and its clinical significance in patients with pulmonary arterial hypertension.

Zhu T, Luo J, Wang Y, Xiong X, Sheng B, Yang X, Ndongala NAMT, Li J.

Clin Exp Pharmacol Physiol. 2019 Aug;46(8):752-760. doi: 10.1111/1440-1681.13102. Epub 2019 May 29.

PMID: 31066078

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  1. Relationship between pulmonary artery acceleration time and pulmonary artery pressures in infants.

Gaulton JS, Mercer-Rosa LM, Glatz AC, Jensen EA, Capone V, Scott C, Appel SM, Stoller JZ, Fraga MV.

Echocardiography. 2019 Aug;36(8):1524-1531. doi: 10.1111/echo.14430. Epub 2019 Jul 1.

PMID: 31260138

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  1. The year 2018 in the European Heart Journal – Cardiovascular Imaging: Part I.

Edvardsen T, Haugaa KH, Petersen SE, Gimelli A, Donal E, Maurer G, Popescu BA, Cosyns B.

Eur Heart J Cardiovasc Imaging. 2019 Aug 1;20(8):858-865. doi: 10.1093/ehjci/jez133.

PMID: 31211353

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  1. Ten-year trend in prevalence and outcome of Down syndrome with congenital heart disease in a middle-income country.

Zahari N, Mat Bah MN, A Razak H, Thong MK.

Eur J Pediatr. 2019 Aug;178(8):1267-1274. doi: 10.1007/s00431-019-03403-x. Epub 2019 Jun 20.

PMID: 31222391

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Select item 31384332

 

  1. Challenges to the improvement of Colombian medical brigades aimed at the diagnosis of congenital heart disease: A qualitative approach.

Rubio MA, Dennis R, Dominguez MT, Suarez R, Olarte-Sierra MF, Palacio D, Ronderos M.

Glob Public Health. 2019 Aug;14(8):1193-1203. doi: 10.1080/17441692.2018.1549266. Epub 2018 Nov 23.

PMID: 30468098

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Select item 31171629

 

  1. CMR feature tracking left ventricular strain-rate predicts ventricular tachyarrhythmia, but not deterioration of ventricular function in patients with repaired tetralogy of Fallot.

Hagdorn QAJ, Vos JDL, Beurskens NEG, Gorter TM, Meyer SL, van Melle JP, Berger RMF, Willems TP.

Int J Cardiol. 2019 Aug 1. pii: S0167-5273(19)30911-8. doi: 10.1016/j.ijcard.2019.07.097. [Epub ahead of print]

PMID: 31402156 Free Article

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Select item 31029496

 

  1. Cross-sectional imaging of congenital pulmonary artery anomalies.

Zucker EJ.

Int J Cardiovasc Imaging. 2019 Aug;35(8):1535-1548. doi: 10.1007/s10554-019-01643-4. Epub 2019 Jun 7. Review.

PMID: 31175525

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Select item 30937683

 

  1. Left Atrial Volumes and Phasic Function in Healthy Children: Reference Values Using Real-Time Three-Dimensional Echocardiography.

Linden K, Goldschmidt F, Laser KT, Winkler C, Körperich H, Dalla-Pozza R, Breuer J, Herberg U.

J Am Soc Echocardiogr. 2019 Aug;32(8):1036-1045.e9. doi: 10.1016/j.echo.2019.03.018. Epub 2019 May 27.

PMID: 31147145 Free Article

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Select item 30917407

 

  1. A rare cause of desaturation in a ‘healthy child’.

Fabi M, Greco L, Gargiulo G, Donti A, Lanari M.

J Cardiovasc Med (Hagerstown). 2019 Aug;20(8):564-565. doi: 10.2459/JCM.0000000000000793. No abstract available.

PMID: 31259859

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Select item 30635921

 

  1. Left ventricular outflow tract obstruction: Uptake of familial cardiac screening and parental knowledge from a single tertiary care center.

Shikany AR, Parrott A, James J, Madueme P, Nicole Weaver K, Cassidy C, Khoury PR, Miller EM.

J Genet Couns. 2019 Aug;28(4):779-789. doi: 10.1002/jgc4.1117. Epub 2019 Mar 25.

PMID: 30907979

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Select item 30950974

 

  1. Increased blood pressure is associated with increased carotid artery intima-media thickness in children with repaired coarctation of the aorta.

Dempsey AA, Parraga G, Altamirano-Diaz L, Welisch E, Park TS, Grattan M, Al-Khazraji BK, Norozi K.

J Hypertens. 2019 Aug;37(8):1689-1698. doi: 10.1097/HJH.0000000000002077.

PMID: 30950974

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Select item 31038380

 

  1. Racial and Ethnic Differences in Pediatric Pulmonary Hypertension: An Analysis of the Pediatric Pulmonary Hypertension Network Registry.

Ong MS, Abman S, Austin ED, Feinstein JA, Hopper RK, Krishnan US, Mullen MP, Natter MD, Raj JU, Rosenzweig EB, Mandl KD; Pediatric Pulmonary Hypertension Network and National Heart, Lung, and Blood Institute Pediatric Pulmonary Vascular Disease Outcomes Bioinformatics Clinical Coordinating Center Investigators.

J Pediatr. 2019 Aug;211:63-71.e6. doi: 10.1016/j.jpeds.2019.04.046. Epub 2019 Jun 5.

PMID: 31176455

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Select item 30982588

 

  1. Evaluation of pulmonary endothelial function in Fontan patients.

Latus H, Lederle A, Khalil M, Kerst G, Schranz D, Apitz C.

J Thorac Cardiovasc Surg. 2019 Aug;158(2):523-531.e1. doi: 10.1016/j.jtcvs.2018.11.144. Epub 2019 Mar 9.

PMID: 30954300

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Select item 31209650

 

  1. Coronary artery fistulae.

Ali M, Kassem KM, Osei K, Effat M.

J Thromb Thrombolysis. 2019 Aug;48(2):345-351. doi: 10.1007/s11239-019-01897-8. Review.

PMID: 31209650

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Select item 30561065

 

  1. Assessment of muscle oxygenation in children with congenital heart disease.

Ross FJ, Arakaki LSL, Ciesielski WA, McMullan DM, Richards MJ, Geiduschek J, Latham G, Hsieh V, Schenkman KA.

Paediatr Anaesth. 2019 Aug;29(8):850-857. doi: 10.1111/pan.13668. Epub 2019 Jun 19.

PMID: 31125476

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Select item 31342114

 

  1. Utility of 3D Printed Cardiac Models for Medical Student Education in Congenital Heart Disease: Across a Spectrum of Disease Severity.

Smerling J, Marboe CC, Lefkowitch JH, Pavlicova M, Bacha E, Einstein AJ, Naka Y, Glickstein J, Farooqi KM.

Pediatr Cardiol. 2019 Aug;40(6):1258-1265. doi: 10.1007/s00246-019-02146-8. Epub 2019 Jun 25.

PMID: 31240370

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Select item 31230092

 

  1. Comparative Cardiorespiratory Fitness in Children: Racial Disparity May Begin Early in Childhood.

Bansal N, Mahadin DR, Smith R, French M, Karpawich PP, Aggarwal S.

Pediatr Cardiol. 2019 Aug;40(6):1183-1189. doi: 10.1007/s00246-019-02129-9. Epub 2019 Jun 8.

PMID: 31177302

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Select item 31087143

 

  1. Critical association of Pallister-Hall syndrome and congenital heart disease.

Ochiai M, Nagata H, Tanaka K, Ihara K, Ohga S.

Pediatr Int. 2019 Aug;61(8):827-828. doi: 10.1111/ped.13945. Epub 2019 Aug 27. No abstract available.

PMID: 31456264

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Select item 31165901

 

  1. Characterisation of computed tomography angiography findings in paediatric patients with heterotaxy.

Ugas Charcape CF, Alpaca Rodriguez LR, Matos Rojas IA, Lazarte Rantes CI, Valdez Quintana M, Katekaru Tokeshi DA, Epelman M.

Pediatr Radiol. 2019 Aug;49(9):1142-1151. doi: 10.1007/s00247-019-04434-0. Epub 2019 Jun 5.

PMID: 31165901

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Select item 31203209

 

  1. Diffusion tensor cardiovascular magnetic resonance.

Khalique Z, Pennell D.

Postgrad Med J. 2019 Aug;95(1126):433-438. doi: 10.1136/postgradmedj-2019-136429. Epub 2019 Jun 15. Review.

PMID: 31203209 Free Article

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Select item 31087396

 

  1. Coexistence an aberrant right subclavian artery with other congenital anomalies: case report and review of the literature.

Mrochek AG, Kabak SL, Haidzel IK, Melnichenko YM, Kalenchic TI.

Surg Radiol Anat. 2019 Aug;41(8):963-967. doi: 10.1007/s00276-019-02206-x. Epub 2019 Feb 8.

PMID: 30737539

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Select item 31462599

 

  1. Pediatric Malignancies: Is the Prechemotherapy Left Ventricular Function Normal?

Akam-Venkata J, Kadiu G, Galas J, Aggarwal S.

Echocardiography. 2019 Aug 31. doi: 10.1111/echo.14461. [Epub ahead of print]

PMID: 31471982

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Select item 31470900

 

  1. Relation Between Exercise Capacity and Extracardiac Conduit Size in Patients with Fontan Circulation.

Lee SY, Song MK, Kim GB, Bae EJ, Kim SH, Jang SI, Cho SK, Kawk JG, Kim WH, Lee CH, Kim HJ, Kim J.

Pediatr Cardiol. 2019 Aug 31. doi: 10.1007/s00246-019-02190-4. [Epub ahead of print]

PMID: 31473799

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Select item 31466543

 

  1. Anxiety, depression, and behavioural rating scales in children with non-cardiac chest pain.

Kenar A, Örün UA, Yoldaş T, Kayalı Ş, Bodur Ş, Karademir S.

Cardiol Young. 2019 Aug 30:1-4. doi: 10.1017/S1047951119001896. [Epub ahead of print]

PMID: 31466543

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Select item 31471941

 

  1. The effectiveness of enzyme replacement therapy on cardiac findings in patients with mucopolysaccharidosis.

Bilginer Gurbuz B, Aypar E, Coskun T, Alehan D, Dursun A, Tokatli A, Sivri HS.

J Pediatr Endocrinol Metab. 2019 Aug 30. pii: /j/jpem.ahead-of-print/jpem-2019-0293/jpem-2019-0293.xml. doi: 10.1515/jpem-2019-0293. [Epub ahead of print]

PMID: 31469658

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Select item 31468697

 

  1. Comparison of intranasal midazolam, intranasal ketamine, and oral chloral hydrate for conscious sedation during paediatric echocardiography: results of a prospective randomised study.

Alp H, Elmacı AM, Alp EK, Say B.

Cardiol Young. 2019 Aug 27:1-7. doi: 10.1017/S1047951119001835. [Epub ahead of print]

PMID: 31451130

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Select item 31451126

 

  1. The long-term outcome of an isolated vascular ring – A single-center experience.

Depypere A, Proesmans M, Cools B, Vermeulen F, Daenen W, Meyns B, Rega F, Boon M.

Pediatr Pulmonol. 2019 Aug 27. doi: 10.1002/ppul.24490. [Epub ahead of print]

PMID: 31456344

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Select item 31452268

 

  1. Base excess and hematocrit predict response to indomethacin in very low birth weight infants with patent ductus arteriosus.

Mydam J, Rastogi A, Naheed ZJ.

Ital J Pediatr. 2019 Aug 22;45(1):107. doi: 10.1186/s13052-019-0706-y.

PMID: 31439021 Free PMC Article

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Select item 31440767

 

  1. Herniated Liver Mimicking Right Atrial Mass.

Stefan KK, Gernot G, Martin K, Michael R.

Pediatr Cardiol. 2019 Aug 22. doi: 10.1007/s00246-019-02186-0. [Epub ahead of print]

PMID: 31440767

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Select item 31440766

 

  1. Cardiac CT in the Preoperative Diagnostics of Neonates with Congenital Heart Disease: Radiation Dose Optimization by Omitting Test Bolus or Bolus Tracking.

Schindler P, Kehl HG, Wildgruber M, Heindel W, Schülke C.

Acad Radiol. 2019 Aug 20. pii: S1076-6332(19)30368-X. doi: 10.1016/j.acra.2019.07.019. [Epub ahead of print]

PMID: 31444109 Free Article

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Select item 31432551

 

  1. Vascular Health of Children Conceived via In Vitro Fertilization.

Zhang WY, Selamet Tierney ES, Chen AC, Ling AY, Fleischmann RR, Baker VL.

J Pediatr. 2019 Aug 20. pii: S0022-3476(19)30885-6. doi: 10.1016/j.jpeds.2019.07.033. [Epub ahead of print]

PMID: 31443895

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Select item 31429918

 

  1. Coronary artery assessment in Kawasaki disease with dual-source CT angiography to uncover vascular pathology.

van Stijn-Bringas Dimitriades D, Planken RN, Groenink M, Streekstra GJ, Kuijpers TW, Kuipers IM.

Eur Radiol. 2019 Aug 19. doi: 10.1007/s00330-019-06367-6. [Epub ahead of print]

PMID: 31428828

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Select item 31426113

 

  1. Prevalence of Pulmonary Hypertension in Pediatric Patients With Obstructive Sleep Apnea and a Cardiology Evaluation: A Retrospective Analysis.

Burns AT, Hansen SL, Turner ZS, Aden JK, Black AB, Hsu DP.

J Clin Sleep Med. 2019 Aug 15;15(8):1081-1087. doi: 10.5664/jcsm.7794.

PMID: 31482829

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Select item 31414622

 

  1. Bodyweight-adjusted rivaroxaban for children with venous thromboembolism (EINSTEIN-Jr): results from three multicentre, single-arm, phase 2 studies.

Monagle P, Lensing AWA, Thelen K, Martinelli I, Male C, Santamaría A, Samochatova E, Kumar R, Holzhauer S, Saracco P, Simioni P, Robertson J, Grangl G, Halton J, Connor P, Young G, Molinari AC, Nowak-Göttl U, Kenet G, Kapsa S, Willmann S, Pap AF, Becka M, Twomey T, Beyer-Westendorf J, Prins MH, Kubitza D; EINSTEIN-Jr Phase 2 Investigators.

Lancet Haematol. 2019 Aug 13. pii: S2352-3026(19)30161-9. doi: 10.1016/S2352-3026(19)30161-9. [Epub ahead of print]

PMID: 31420317

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Select item 31412610

 

 

  1. Discovering dad: paternal roles, responsibilities, and support needs as defined by fathers of children with complex cardiac conditions perioperatively.

Robinson J, Huskey D, Schalley S, Wratchford D, Hammel J, Weaver MS.

Cardiol Young. 2019 Aug 8:1-6. doi: 10.1017/S1047951119001586. [Epub ahead of print]

PMID: 31391137

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Select item 31393559

 

  1. Acute Abdomen in Kawasaki Disease.

Velez-Tirado N, Ridaura-Sanz C, Venegas-Montoya E, Scheffler-Mendoza S, Camacho-Moreno R, Otero-Mendoza F, Medina-Vega FA, Garrido-García LM, Rivas-Larrauri F, Nakashimada MAY.

Indian J Pediatr. 2019 Aug 7. doi: 10.1007/s12098-019-03048-6. [Epub ahead of print] No abstract available.

PMID: 31388920

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Select item 31392380

 

  1. Correlation of Echocardiogram and Exercise Test Data in Children with Aortic Stenosis.

Santana S, Gidding SS, Xie S, Jiang T, Kharouf R, Robinson BW.

Pediatr Cardiol. 2019 Aug 7. doi: 10.1007/s00246-019-02177-1. [Epub ahead of print]

PMID: 31392379

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Select item 31389740

 

  1. RIKADA Study Reveals Risk Factors in Pediatric Primary Cardiomyopathy.

Al-Wakeel-Marquard N, Degener F, Herbst C, Kühnisch J, Dartsch J, Schmitt B, Kuehne T, Messroghli D, Berger F, Klaassen S.

J Am Heart Assoc. 2019 Aug 6;8(15):e012531. doi: 10.1161/JAHA.119.012531. Epub 2019 Jul 23.

PMID: 31333075 Free Article

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Select item 31388700

 

  1. Bands in the Heart: Multimodality Imaging Review.

Rajiah P, MacNamara J, Chaturvedi A, Ashwath R, Fulton NL, Goerne H.

Radiographics. 2019 Aug 2:180176. doi: 10.1148/rg.2019180176. [Epub ahead of print]

PMID: 31373865

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Select item 31089779

 

  1. Familial aggregation of “apple peel” intestinal atresia and cardiac left-sided obstructive lesions: A possible causal relationship with NOTCH1 gene mutations.

Digilio MC, Magliozzi M, Di Pede A, Valfrè L, Dentici ML, Auriti C, Marino B, Novelli A, Dallapiccola B.

Am J Med Genet A. 2019 Aug;179(8):1570-1574. doi: 10.1002/ajmg.a.61195. Epub 2019 May 20.

PMID: 31111652

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Select item 31375646

 

  1. A case of right aortic arch with isolated left innominate artery and global cerebral white matter atrophy.

Binka E, Sun LR, Gailloud P, Chiu JS.

Cardiol Young. 2019 Aug;29(8):1107-1109. doi: 10.1017/S1047951119001537. Epub 2019 Jul 10.

PMID: 31288876

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Select item 31287039

 

  1. Anomalous single trunk coronary artery from the right pulmonary artery.

Donmez YN, Aykan HH, Yilmaz M.

Cardiol Young. 2019 Aug;29(8):1088-1090. doi: 10.1017/S1047951119001379. Epub 2019 Jun 28.

PMID: 31250782

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Select item 31244446

 

  1. Isolated retroaortic innominate vein and right aortic arch: a case report and review of literature.

Kohli U.

Cardiol Young. 2019 Aug;29(8):1091-1093. doi: 10.1017/S1047951119001380. Epub 2019 Jun 21.

PMID: 31221230

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Select item 31208473

 

  1. A standardized imaging protocol improves quality and reduces practice variability in echocardiographic assessment of ventricular function by first-year pediatric cardiology fellows.

White BR, Ho DY, Rogers LS, Natarajan SS.

Echocardiography. 2019 Aug;36(8):1515-1523. doi: 10.1111/echo.14441. Epub 2019 Aug 5.

PMID: 31385382

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Select item 31260138

 

  1. Systematic literature review on the economic, humanistic, and societal burden of heart failure in children and adolescents.

Burch M, Nallagangula TK, Nic Lochlainn E, Severin T, Thakur L, Jaecklin T, George AT, Solar-Yohay S, Rossano JW, Shaddy RE.

Expert Rev Pharmacoecon Outcomes Res. 2019 Aug;19(4):397-408. doi: 10.1080/14737167.2019.1579645. Epub 2019 Mar 5.

PMID: 30747011

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Select item 30675029

 

  1. Correction: Arterial tortuosity syndrome: 40 new families and literature review.

Beyens A, Albuisson J, Boel A, Al-Essa M, Al-Manea W, Bonnet D, Bostan O, Boute O, Busa T, Canham N, Cil E, Coucke PJ, Cousin MA, Dasouki M, De Backer J, De Paepe A, De Schepper S, De Silva D, Devriendt K, De Wandele I, Deyle DR, Dietz H, Dupuis-Girod S, Fontenot E, Fischer-Zirnsak B, Gezdirici A, Ghoumid J, Giuliano F, Baena N, Haider MZ, Hardin JS, Jeunemaitre X, Klee EW, Kornak U, Landecho MF, Legrand A, Loeys B, Lyonnet S, Michael H, Moceri P, Mohammed S, Muiño-Mosquera L, Nampoothiri S, Pichler K, Prescott K, Rajeb A, Ramos-Arroyo M, Rossi M, Salih M, Seidahmed MZ, Schaefer E, Steichen-Gersdorf E, Temel S, Uysal F, Vanhomwegen M, Van Laer L, Van Maldergem L, Warner D, Willaert A, Collins Ii TR, Taylor A, Davis EC, Zarate Y, Callewaert B.

Genet Med. 2019 Aug;21(8):1894-1895. doi: 10.1038/s41436-018-0035-3.

PMID: 30201961

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Select item 30916392

 

  1. Biallelic mutation in MYH7 and MYBPC3 leads to severe cardiomyopathy with left ventricular noncompaction phenotype.

Kolokotronis K, Kühnisch J, Klopocki E, Dartsch J, Rost S, Huculak C, Mearini G, Störk S, Carrier L, Klaassen S, Gerull B.

Hum Mutat. 2019 Aug;40(8):1101-1114. doi: 10.1002/humu.23757. Epub 2019 Apr 24.

PMID: 30924982

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Select item 31020596

 

  1. Association of left ventricular size with regional right ventricular mechanics in Hypoplastic Left Heart Syndrome.

Forsha D, Li L, Joseph N, Kutty S, Friedberg MK.

Int J Cardiol. 2019 Aug 1. pii: S0167-5273(19)33278-4. doi: 10.1016/j.ijcard.2019.07.090. [Epub ahead of print]

PMID: 31402159

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Select item 31402156

 

  1. Improvement of the outcome in patients with infantile dilated cardiomyopathy over three decades – The usefulness of long-term gradually medical supportive care.

Tsuda E, Yamada O, Kitano M.

J Cardiol. 2019 Aug;74(2):189-194. doi: 10.1016/j.jjcc.2019.02.005. Epub 2019 Mar 12.

PMID: 30876708

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Select item 30852093

 

  1. Neonatal Marfan Syndrome: A Rare, Severe, and Life-Threatening Genetic Disease.

Solé-Ribalta A, Rodríguez-Fanjul X, Carretero-Bellon JM, Pascual-Sala C, Martorell-Sampol L, Bobillo-Pérez S, Morillo-Palomo AM.

J Pediatr. 2019 Aug;211:221-221.e2. doi: 10.1016/j.jpeds.2019.03.033. Epub 2019 Apr 30. No abstract available.

PMID: 31053350

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Select item 30952511

 

  1. Evaluation of pulmonary endothelial function in Fontan patients.

Latus H, Lederle A, Khalil M, Kerst G, Schranz D, Apitz C.

J Thorac Cardiovasc Surg. 2019 Aug;158(2):523-531.e1. doi: 10.1016/j.jtcvs.2018.11.144. Epub 2019 Mar 9.

PMID: 30954300

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Select item 30536443

 

  1. In reply-Strategies of Screening for Fabry Disease in Patients With Unexplained Left Ventricular Hypertrophy.

Newman DB, Ackerman MJ.

Mayo Clin Proc. 2019 Aug;94(8):1646. doi: 10.1016/j.mayocp.2019.05.004. No abstract available.

PMID: 31378242

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Select item 31266678

 

  1. Through Tricuspid Closure for Doubly Committed Subarterial Ventricular Septal Defect with Right Vertical Subaxillary Mini-incision: A Matched-Pair Analysis.

Liu R, Rui L, Zhang B, Lin Y, Li S, Hua Z.

Pediatr Cardiol. 2019 Aug;40(6):1247-1252. doi: 10.1007/s00246-019-02144-w. Epub 2019 Jul 23.

PMID: 31338560

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Select item 31317219

 

  1. Superior Vena Cava Inflow Following Repair for Anomalous Right Pulmonary Venous Drainage in Children.

Federspiel JM, Das De S, Lilley S, Smith B, Danton M, McLean A, MacArthur K, Peng E.

Pediatr Cardiol. 2019 Aug;40(6):1275-1283. doi: 10.1007/s00246-019-02148-6. Epub 2019 Jul 12.

PMID: 31300841

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Select item 31263917

 

  1. Saline Contrast Transesophageal Echocardiography in Fontan Patients: Assessment of the Presence, Type, and Size of Right to Left Shunts.

Zaidi SJ, Adhikari RR, Patel DR, Cui VW, Javois AJ, Roberson DA.

Pediatr Cardiol. 2019 Aug;40(6):1199-1207. doi: 10.1007/s00246-019-02132-0. Epub 2019 Jun 19.

PMID: 31218373

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Select item 31218372

 

  1. Comparison Between Nomograms Used to Define Pediatric Aortic Arch Hypoplasia: Retrospective Evaluation Among Patients Less Than 1 Year Old with Coarctation of the Aorta.

Şişli E, Kalın S, Tuncer ON, Ayık MF, Alper H, Levent RE, Şahin H, Atay Y.

Pediatr Cardiol. 2019 Aug;40(6):1190-1198. doi: 10.1007/s00246-019-02130-2. Epub 2019 Jun 5.

PMID: 31165902

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Select item 31152185

 

  1. Thenar Muscle Oxygen Saturation Using Vascular Occlusion Test: A Novel Technique to Study Microcirculatory Abnormalities in Pediatric Heart Failure Patients.

Samraj RS, Lopez-Colon D, Kerrigan M, Fricker FJ, Pietra BA, Bleiweis M, Gupta D.

Pediatr Cardiol. 2019 Aug;40(6):1151-1158. doi: 10.1007/s00246-019-02118-y. Epub 2019 May 16.

PMID: 31098675

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Select item 31087144

 

  1. Excessive soft drink may induce pulmonary hypertension via thiamine deficiency.

Sakurai K, Fujiwara N, Takahashi K, Nakayashiro M.

Pediatr Int. 2019 Aug;61(8):823-824. doi: 10.1111/ped.13913. Epub 2019 Aug 1. No abstract available.

PMID: 31373121

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Select item 31172686

 

  1. The Thoracic and Cardiovascular Surgeon and the Pediatric Cardiologist.

Dittrich S.

Thorac Cardiovasc Surg. 2019 Aug;67(5):330. doi: 10.1055/s-0039-1693656. Epub 2019 Aug 9. No abstract available.

PMID: 31398729

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Select item 31082372

 

  1. [Clinical effect and safety of clopidogrel combined with aspirin in antithrombotic therapy for children with Kawasaki disease complicated by small/medium-sized coronary arteryPediatric cardiology August 2019
    1. Altered 4-D magnetic resonance imaging flow characteristics in complex congenital aortic arch repair.

    Desai LP, Berhane H, Husain N, Robinson JD, Rigsby CK, Markl M.

    Pediatr Radiol. 2019 Aug 31. doi: 10.1007/s00247-019-04507-0. [Epub ahead of print]

    PMID: 31473788

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    Select item 31469062

     

    1. Development of a clinician-parent home care education intervention.

    Lane B, Hanke SP, Giambra B, Madsen NL, Staveski SL.

    Cardiol Young. 2019 Aug 30:1-6. doi: 10.1017/S1047951119001318. [Epub ahead of print]

    PMID: 31469062

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    Select item 31469384

     

    1. Exploring Shared Susceptibility between Two Neural Crest Cells Originating Conditions: Neuroblastoma and Congenital Heart Disease.

    Testori A, Lasorsa VA, Cimmino F, Cantalupo S, Cardinale A, Avitabile M, Limongelli G, Russo MG, Diskin S, Maris J, Devoto M, Keavney B, Cordell HJ, Iolascon A, Capasso M.

    Genes (Basel). 2019 Aug 30;10(9). pii: E663. doi: 10.3390/genes10090663.

    PMID: 31480262 Free Article

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    Select item 31471763

     

    1. Early Neurodevelopmental Outcomes in Children with Hypoplastic Left Heart Syndrome and Related Anomalies After Hybrid Procedure.

    Khalid OM, Harrison TM.

    Pediatr Cardiol. 2019 Aug 30. doi: 10.1007/s00246-019-02191-3. [Epub ahead of print]

    PMID: 31471627

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    Select item 31471626

     

    1. Costello Syndrome.

    Gripp KW, Rauen KA.

    In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019.

    2006 Aug 29 [updated 2019 Aug 29].

    PMID: 20301680 Free Books & Documents

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    Select item 31462608

     

    1. Motion robust respiratory-resolved 3D radial flow MRI and its application in neonatal congenital heart disease.

    Schrauben EM, Lim JM, Goolaub DS, Marini D, Seed M, Macgowan CK.

    Magn Reson Med. 2019 Aug 29. doi: 10.1002/mrm.27945. [Epub ahead of print]

    PMID: 31464030

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    Select item 31462289

     

    1. Minimum Travel Distance Among Publicly Insured Infants with Severe Congenital Heart Disease: Potential Impact of In-state Restrictions.

    Woo JL, Anderson BR, Gruenstein D, Conti R, Chua KP.

    Pediatr Cardiol. 2019 Aug 28. doi: 10.1007/s00246-019-02193-1. [Epub ahead of print]

    PMID: 31463514

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    Select item 31461203

     

    1. Comprehensive literature review of anomalies of the coronary arteries.

    Harky A, Noshirwani A, Karadakhy O, Ang J.

    J Card Surg. 2019 Aug 26. doi: 10.1111/jocs.14228. [Epub ahead of print] Review.

    PMID: 31449703

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    1. Estimating the effect size of the 15Q11.2 BP1-BP2 deletion and its contribution to neurodevelopmental symptoms: recommendations for practice.

    Jønch AE, Douard E, Moreau C, Van Dijck A, Passeggeri M, Kooy F, Puechberty J, Campbell C, Sanlaville D, Lefroy H, Richetin S, Pain A, Geneviève D, Kini U, Le Caignec C, Lespinasse J, Skytte AB, Isidor B, Zweier C, Caberg JH, Delrue MA, Møller RS, Bojesen A, Hjalgrim H, Brasch-Andersen C, Lemyre E, Ousager LB, Jacquemont S; 15q11.2 Working Group.

    J Med Genet. 2019 Aug 26. pii: jmedgenet-2018-105879. doi: 10.1136/jmedgenet-2018-105879. [Epub ahead of print]

    PMID: 31451536 Free Article

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    1. Mental health care for parents of babies with congenital heart disease during intensive care unit admission: Systematic review and statement of best practice.

    Kasparian NA, Kan JM, Sood E, Wray J, Pincus HA, Newburger JW.

    Early Hum Dev. 2019 Aug 24:104837. doi: 10.1016/j.earlhumdev.2019.104837. [Epub ahead of print]

    PMID: 31455569

    SMyocarditis in the pediatric population: A review.

    Dasgupta S, Iannucci G, Mao C, Clabby M, Oster ME.

    Congenit Heart Dis. 2019 Aug 21. doi: 10.1111/chd.12835. [Epub ahead of print]

    PMID: 31432626

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    Select item 31446473

     

    1. Brain Injury in Infants with Critical Congenital Heart Disease: Insights from Two Clinical Cohorts with Different Practice Approaches.

    Claessens NHP, Chau V, de Vries LS, Jansen NJG, Au-Young SH, Stegeman R, Blaser S, Shroff M, Haas F, Marini D, Breur JMPJ, Seed M, Benders MJNL, Miller SP.

    J Pediatr. 2019 Aug 23. pii: S0022-3476(19)30869-8. doi: 10.1016/j.jpeds.2019.07.017. [Epub ahead of print]

    PMID: 31451185

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    1. Dual-source computed tomography coronary artery imaging in children.

    Secinaro A, Curione D, Mortensen KH, Santangelo TP, Ciancarella P, Napolitano C, Del Pasqua A, Taylor AM, Ciliberti P.

    Pediatr Radiol. 2019 Aug 22. doi: 10.1007/s00247-019-04494-2. [Epub ahead of print]

    PMID: 31440884

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    Select item 31432626

     

    1. Myocarditis in the pediatric population: A review.

    Dasgupta S, Iannucci G, Mao C, Clabby M, Oster ME.

    Congenit Heart Dis. 2019 Aug 21. doi: 10.1111/chd.12835. [Epub ahead of print]

    PMID: 31432626

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    1. Delivery room asphyxia in neonates with ductal-dependent congenital heart disease: a retrospective cohort study.

    Boos V, Kocjancic L, Berger F, Bührer C.

    J Perinatol. 2019 Aug 21. doi: 10.1038/s41372-019-0474-y. [Epub ahead of print]

    PMID: 31434996

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    Select item 31444109

     

    1. Identification of risk factors affecting catch-up growth after infant congenital heart disease surgery: rationale and design of a multicentre prospective cohort study in China.

    Li L, Li K, An C, Fan J, Guo C, Liang S, Guo Y, Xia H, Chen X, Zhu Y, Hu C, Si W, Liang H, Cui Y.

    BMJ Open. 2019 Aug 20;9(8):e030084. doi: 10.1136/bmjopen-2019-030084.

    PMID: 31434778 Free PMC Article

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    Select item 30586772

     

    1. Comparison of Two Measurement Devices for Pulse Wave Velocity in Children: Which Tool Is Useful to Detect Vascular Alterations Caused by Overweight?

    Elmenhorst J, Weberruss H, Mayr M, Pfister K, Oberhoffer R.

    Front Pediatr. 2019 Aug 20;7:334. doi: 10.3389/fped.2019.00334. eCollection 2019.

    PMID: 31482076 Free PMC Article

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    Select item 30412710

     

    1. Circulating plasma circular RNAs as novel diagnostic biomarkers for congenital heart disease in children.

    Wu J, Li J, Liu H, Yin J, Zhang M, Yu Z, Miao H.

    J Clin Lab Anal. 2019 Aug 20:e22998. doi: 10.1002/jcla.22998. [Epub ahead of print]

    PMID: 31429492

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    Select item 31432385

     

    1. Feasibility study assessing equitable delivery of newborn pulse oximetry screening in New Zealand’s midwifery-led maternity setting.

    Cloete E, Gentles TL, Dixon LA, Webster DR, Agnew JD, Davidkova S, Alsweiler JM, Rogers J, Bloomfield FH; Pulse Oximetry Screening Steering Committee.

    BMJ Open. 2019 Aug 18;9(8):e030506. doi: 10.1136/bmjopen-2019-030506.

    PMID: 31427341 Free PMC Article

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    Select item 31453268

     

    1. First-Year Outcomes of Critical Congenital Heart Disease Screening in Maryland.

    Badawi D, Watson J, Maschke S, Reid L.

    Glob Pediatr Health. 2019 Aug 18;6:2333794X19868226. doi: 10.1177/2333794X19868226. eCollection 2019.

    PMID: 31453268 Free PMC Article

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    Select item 31423753

     

    1. Increased risk of pulmonary hypertension following premature birth.

    Naumburg E, Söderström L.

    BMC Pediatr. 2019 Aug 17;19(1):288. doi: 10.1186/s12887-019-1665-6.

    PMID: 31421674 Free PMC Article

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    1. Guideline implementation and early risk assessment in pulmonary arterial hypertension associated with congenital heart disease: A retrospective cohort study.

    Deng X, Jin B, Li S, Li Y, Zhou H, Wu Y, Yan M, Hu Y, Qiu Q, Zhang G, Zheng X.

    Clin Respir J. 2019 Aug 16. doi: 10.1111/crj.13076. [Epub ahead of print]

    PMID: 31419027

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    Select item 31420818

     

    1. Spontaneous Closure Rates of Ventricular Septal Defects (6,750 Consecutive Neonates).

    Zhao QM, Niu C, Liu F, Wu L, Ma XJ, Huang GY.

    Am J Cardiol. 2019 Aug 15;124(4):613-617. doi: 10.1016/j.amjcard.2019.05.022. Epub 2019 May 25.

    PMID: 31208700

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    1. Meaningful and feasible composite clinical worsening definitions in paediatric pulmonary arterial hypertension: An analysis of the TOPP registry.

    Beghetti M, Brand M, Berger RMF, Humpl T, Wheeler JG, Ivy DD, Bonnet D; TOPP investigators.

    Int J Cardiol. 2019 Aug 15;289:110-115. doi: 10.1016/j.ijcard.2019.04.062. Epub 2019 Apr 25.

    PMID: 31072635 Free Article

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    Select item 31414622

     

    1. Left ventricular mass estimation by real-time 3D echocardiography favourably competes with CMR in congenital left ventricular disease.

    Michel M, Shabanah W, Körperich H, Kelter-Klöpping A, Entenmann A, Racolta A, Laser KT.

    Sci Rep. 2019 Aug 15;9(1):11888. doi: 10.1038/s41598-019-48375-y.

    PMID: 31417137 Free PMC Article

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    Select item 31421105

     

    1. A case report of T-box 1 mutation causing phenotypic features of chromosome 22q11.2 deletion syndrome.

    Haddad RA, Clines GA, Wyckoff JA.

    Clin Diabetes Endocrinol. 2019 Aug 13;5:13. doi: 10.1186/s40842-019-0087-6. eCollection 2019.

    PMID: 31428446 Free PMC Article

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    Select item 31419439

     

    1. Hypoplastic left heart syndrome: From bedside to bench and back.

    Saraf A, Book WM, Nelson TJ, Xu C.

    J Mol Cell Cardiol. 2019 Aug 13;135:109-118. doi: 10.1016/j.yjmcc.2019.08.005. [Epub ahead of print] Review.

    PMID: 31419439

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    1. A multi-national trial of a direct oral anticoagulant in children with cardiac disease: Design and rationale of the Safety of ApiXaban On Pediatric Heart disease On the preventioN of Embolism (SAXOPHONE) study.

    Payne RM, Burns KM, Glatz AC, Li D, Li X, Monagle P, Newburger JW, Swan EA, Wheaton O, Male C; Pediatric Heart Network Investigators.

    Am Heart J. 2019 Aug 9;217:52-63. doi: 10.1016/j.ahj.2019.08.002. [Epub ahead of print]

    PMID: 31493728

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    1. Detrimental Effects of Chemotherapy on Human Coronary Microvascular Function.

    Hader SN, Zinkevich NS, Norwood Toro LE, Kriegel AJ, Kong A, Freed JK, Gutterman DD, Beyer AM.

    Am J Physiol Heart Circ Physiol. 2019 Aug 9. doi: 10.1152/ajpheart.00370.2019. [Epub ahead of print]

    PMID: 31397169

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    1. Trajectory of right ventricular indices is an early predictor of outcomes in hypoplastic left heart syndrome.

    Kim AS, Witzenburg CM, Conaway M, Vergales JE, Holmes JW, L’Ecuyer TJ, Dean PN.

    Congenit Heart Dis. 2019 Aug 8. doi: 10.1111/chd.12834. [Epub ahead of print]

    PMID: 31393088

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    1. Efficient Mining of Variants From Trios for Ventricular Septal Defect Association Study.

    Jiang P, Hu Y, Wang Y, Zhang J, Zhu Q, Bai L, Tong Q, Li T, Zhao L.

    Front Genet. 2019 Aug 8;10:670. doi: 10.3389/fgene.2019.00670. eCollection 2019.

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    Select item 31391061

     

    1. mDixon ECG-gated 3-dimensional cardiovascular magnetic resonance angiography in patients with congenital cardiovascular disease.

    Kourtidou S, Jones MR, Moore RA, Tretter JT, Ollberding NJ, Crotty EJ, Rattan MS, Fleck RJ, Taylor MD.

    J Cardiovasc Magn Reson. 2019 Aug 8;21(1):52. doi: 10.1186/s12968-019-0554-3.

    PMID: 31391061 Free PMC Article

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    1. The Impact of Neurobehavior on Feeding Outcomes in Neonates with Congenital Heart Disease.

    Gakenheimer-Smith L, Glotzbach K, Ou Z, Presson AP, Puchalski M, Jones C, Lambert L, Delgado-Corcoran C, Eckhauser A, Miller T.

    J Pediatr. 2019 Aug 8. pii: S0022-3476(19)30811-X. doi: 10.1016/j.jpeds.2019.06.047. [Epub ahead of print]

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    1. Highlights of Current Research in Congenital Heart Disease: Presenting Abstracts From the 2019 Congenital Cardiac Anesthesia Society (CCAS) Annual Meeting.

    Latham GJ.

    Semin Cardiothorac Vasc Anesth. 2019 Aug 8:1089253219867696. doi: 10.1177/1089253219867696. [Epub ahead of print] No abstract available.

    PMID: 31390945

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    Select item 31492419

     

    1. Congenital Hypothyroidism: 8-Year Experience Using 2 Newborn Screens in Alabama.

    Pitts L, McCormick W, Mick GJ.

    Horm Res Paediatr. 2019 Aug 7:1-10. doi: 10.1159/000501395. [Epub ahead of print]

    PMID: 31390650

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    Select item 31389639

     

    1. Enhancing efficiency and scientific impact of a clinical trials network: the Pediatric Heart Network Integrated CARdiac Data and Outcomes (iCARD) Collaborative.

    Pasquali SK, Kaltman JR, Gaynor JW, McCrindle BW, Newburger JW, Anderson BR, Scheurer MA, Pinto NM, Anderson JB, Oster ME, Jacobs JP, Marino BS, Mery CM, Pearson GD.

    Cardiol Young. 2019 Aug 6:1-6. doi: 10.1017/S104795111900163X. [Epub ahead of print]

    PMID: 31385565

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    1. The Functional Polymorphism R129W in the BVES Gene Is Associated with Sporadic Tetralogy of Fallot in the Han Chinese Population.

    Shi Y, Li Y, Wang Y, Zhuang J, Wang H, Hu M, Mo X, Yue S, Chen Y, Fan X, Chen J, Cai W, Zhu X, Wan Y, Zhong Y, Ye X, Li F, Zhou Z, Dai G, Luo R, Ocorr K, Jiang Z, Li X, Zhu P, Wu X, Yuan W.

    Genet Test Mol Biomarkers. 2019 Aug 6. doi: 10.1089/gtmb.2019.0085. [Epub ahead of print]

    PMID: 31386585

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    1. RIKADA Study Reveals Risk Factors in Pediatric Primary Cardiomyopathy.

    Al-Wakeel-Marquard N, Degener F, Herbst C, Kühnisch J, Dartsch J, Schmitt B, Kuehne T, Messroghli D, Berger F, Klaassen S.

    J Am Heart Assoc. 2019 Aug 6;8(15):e012531. doi: 10.1161/JAHA.119.012531. Epub 2019 Jul 23.

    PMID: 31333075 Free Article

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    1. Treatment With Tetrahydrobiopterin Improves White Matter Maturation in a Mouse Model for Prenatal Hypoxia in Congenital Heart Disease.

    Romanowicz J, Leonetti C, Dhari Z, Korotcova L, Ramachandra SD, Saric N, Morton PD, Bansal S, Cheema A, Gallo V, Jonas RA, Ishibashi N.

    J Am Heart Assoc. 2019 Aug 6;8(15):e012711. doi: 10.1161/JAHA.119.012711. Epub 2019 Jul 23.

    PMID: 31331224 Free Article

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    1. Third time lucky: challenging secundum atrial septal defect.

    Ordoñez MV, Moharem-Elgamal S, Bedair R.

    Cardiol Young. 2019 Aug 5:1-4. doi: 10.1017/S1047951119001677. [Epub ahead of print]

    PMID: 31379319

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    1. Left ventricular non-compaction in a child with bicuspid aortic valve and aortic coarctation.

    Karatza A, Mylonas KS, Tzifa A.

    Cardiol Young. 2019 Aug 5:1-3. doi: 10.1017/S1047951119001707. [Epub ahead of print]

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    1. CHIP-Family intervention to improve the psychosocial well-being of young children with congenital heart disease and their families: results of a randomised controlled trial.

    van der Mheen M, Meentken MG, van Beynum IM, van der Ende J, van Galen E, Zirar A, Aendekerk EWC, van den Adel TPL, Bogers AJJC, McCusker CG, Hillegers MHJ, Helbing WA, Utens EMWJ.

    Cardiol Young. 2019 Aug 5:1-11. doi: 10.1017/S1047951119001732. [Epub ahead of print]

    PMID: 31378215

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    1. Hospital-Acquired Pressure Injuries in Children With Congenital Heart Disease: Prevalence and Associated Factors.

    Kulik LA, Hasbani NR, Stellar JJ, Quigley SM, Shelley SS, Wypij D, Curley MAQ; for Braden QD Study Group.

    Pediatr Crit Care Med. 2019 Aug 5. doi: 10.1097/PCC.0000000000002077. [Epub ahead of print]

    PMID: 31385861

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    1. Impact of feeding mode on neurodevelopmental outcome in infants and children with congenital heart disease.

    Holst LM, Serrano F, Shekerdemian L, Ravn HB, Guffey D, Ghanayem NS, Monteiro S.

    Congenit Heart Dis. 2019 Aug 2. doi: 10.1111/chd.12827. [Epub ahead of print]

    PMID: 31373176

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    1. Cardiac rhabdomyomas with atrial septal defect and tricuspid insufficiency: A case report.

    Wu C, Wang Y, Su W, Xia J, Dong N, Wang G.

    J Card Surg. 2019 Aug 2. doi: 10.1111/jocs.14191. [Epub ahead of print]

    PMID: 31374583

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    1. The expression of survivin in irreversible pulmonary arterial hypertension rats and its value in evaluating the reversibility of pulmonary arterial hypertension secondary to congenital heart disease.

    Li G, Zhang H, Zhao L, Zhang Y, Yan D, Liu Y, Su J, Fan X.

    Pulm Circ. 2019 Aug 2;9(3):2045894019859480. doi: 10.1177/2045894019859480. eCollection 2019 Jul-Sep.

    PMID: 31428312 Free PMC Article

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    1. Glycogen Storage Disease Type IV.

    Magoulas PL, El-Hattab AW.

    In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019.

    2013 Jan 3 [updated 2019 Aug 1].

    PMID: 23285490 Free Books & Documents

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    1. MCP-1 promotes detrimental cardiac physiology, pulmonary edema, and death in the cpk model of polycystic kidney disease.

    Salah SM, Meisenheimer JD, Rao R, Peda JD, Wallace DP, Foster D, Li X, Li X, Zhou X, Vallejo JA, Wacker MJ, Fields TA, Swenson-Fields KI.

    Am J Physiol Renal Physiol. 2019 Aug 1;317(2):F343-F360. doi: 10.1152/ajprenal.00240.2018. Epub 2019 May 15.

    PMID: 31091126

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    1. Accuracy of a portable pulse oximeter in monitoring hypoxemic infants with cyanotic heart disease.

    Harris BU, Stewart S, Verma A, Hoen H, Stein ML, Wright G, Ramamoorthy C.

    Cardiol Young. 2019 Aug;29(8):1025-1029. doi: 10.1017/S1047951119001355. Epub 2019 Jul 15.

    PMID: 31304897

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    1. Elevated plasma Pim-1 and its clinical significance in patients with pulmonary arterial hypertension.

    Zhu T, Luo J, Wang Y, Xiong X, Sheng B, Yang X, Ndongala NAMT, Li J.

    Clin Exp Pharmacol Physiol. 2019 Aug;46(8):752-760. doi: 10.1111/1440-1681.13102. Epub 2019 May 29.

    PMID: 31066078

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    1. Relationship between pulmonary artery acceleration time and pulmonary artery pressures in infants.

    Gaulton JS, Mercer-Rosa LM, Glatz AC, Jensen EA, Capone V, Scott C, Appel SM, Stoller JZ, Fraga MV.

    Echocardiography. 2019 Aug;36(8):1524-1531. doi: 10.1111/echo.14430. Epub 2019 Jul 1.

    PMID: 31260138

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    1. The year 2018 in the European Heart Journal – Cardiovascular Imaging: Part I.

    Edvardsen T, Haugaa KH, Petersen SE, Gimelli A, Donal E, Maurer G, Popescu BA, Cosyns B.

    Eur Heart J Cardiovasc Imaging. 2019 Aug 1;20(8):858-865. doi: 10.1093/ehjci/jez133.

    PMID: 31211353

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    1. Ten-year trend in prevalence and outcome of Down syndrome with congenital heart disease in a middle-income country.

    Zahari N, Mat Bah MN, A Razak H, Thong MK.

    Eur J Pediatr. 2019 Aug;178(8):1267-1274. doi: 10.1007/s00431-019-03403-x. Epub 2019 Jun 20.

    PMID: 31222391

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    1. Challenges to the improvement of Colombian medical brigades aimed at the diagnosis of congenital heart disease: A qualitative approach.

    Rubio MA, Dennis R, Dominguez MT, Suarez R, Olarte-Sierra MF, Palacio D, Ronderos M.

    Glob Public Health. 2019 Aug;14(8):1193-1203. doi: 10.1080/17441692.2018.1549266. Epub 2018 Nov 23.

    PMID: 30468098

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    1. CMR feature tracking left ventricular strain-rate predicts ventricular tachyarrhythmia, but not deterioration of ventricular function in patients with repaired tetralogy of Fallot.

    Hagdorn QAJ, Vos JDL, Beurskens NEG, Gorter TM, Meyer SL, van Melle JP, Berger RMF, Willems TP.

    Int J Cardiol. 2019 Aug 1. pii: S0167-5273(19)30911-8. doi: 10.1016/j.ijcard.2019.07.097. [Epub ahead of print]

    PMID: 31402156 Free Article

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    1. Cross-sectional imaging of congenital pulmonary artery anomalies.

    Zucker EJ.

    Int J Cardiovasc Imaging. 2019 Aug;35(8):1535-1548. doi: 10.1007/s10554-019-01643-4. Epub 2019 Jun 7. Review.

    PMID: 31175525

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    1. Left Atrial Volumes and Phasic Function in Healthy Children: Reference Values Using Real-Time Three-Dimensional Echocardiography.

    Linden K, Goldschmidt F, Laser KT, Winkler C, Körperich H, Dalla-Pozza R, Breuer J, Herberg U.

    J Am Soc Echocardiogr. 2019 Aug;32(8):1036-1045.e9. doi: 10.1016/j.echo.2019.03.018. Epub 2019 May 27.

    PMID: 31147145 Free Article

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    1. A rare cause of desaturation in a ‘healthy child’.

    Fabi M, Greco L, Gargiulo G, Donti A, Lanari M.

    J Cardiovasc Med (Hagerstown). 2019 Aug;20(8):564-565. doi: 10.2459/JCM.0000000000000793. No abstract available.

    PMID: 31259859

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    Select item 30635921

     

    1. Left ventricular outflow tract obstruction: Uptake of familial cardiac screening and parental knowledge from a single tertiary care center.

    Shikany AR, Parrott A, James J, Madueme P, Nicole Weaver K, Cassidy C, Khoury PR, Miller EM.

    J Genet Couns. 2019 Aug;28(4):779-789. doi: 10.1002/jgc4.1117. Epub 2019 Mar 25.

    PMID: 30907979

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    Select item 30950974

     

    1. Increased blood pressure is associated with increased carotid artery intima-media thickness in children with repaired coarctation of the aorta.

    Dempsey AA, Parraga G, Altamirano-Diaz L, Welisch E, Park TS, Grattan M, Al-Khazraji BK, Norozi K.

    J Hypertens. 2019 Aug;37(8):1689-1698. doi: 10.1097/HJH.0000000000002077.

    PMID: 30950974

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    Select item 31038380

     

    1. Racial and Ethnic Differences in Pediatric Pulmonary Hypertension: An Analysis of the Pediatric Pulmonary Hypertension Network Registry.

    Ong MS, Abman S, Austin ED, Feinstein JA, Hopper RK, Krishnan US, Mullen MP, Natter MD, Raj JU, Rosenzweig EB, Mandl KD; Pediatric Pulmonary Hypertension Network and National Heart, Lung, and Blood Institute Pediatric Pulmonary Vascular Disease Outcomes Bioinformatics Clinical Coordinating Center Investigators.

    J Pediatr. 2019 Aug;211:63-71.e6. doi: 10.1016/j.jpeds.2019.04.046. Epub 2019 Jun 5.

    PMID: 31176455

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    Select item 30982588

     

    1. Evaluation of pulmonary endothelial function in Fontan patients.

    Latus H, Lederle A, Khalil M, Kerst G, Schranz D, Apitz C.

    J Thorac Cardiovasc Surg. 2019 Aug;158(2):523-531.e1. doi: 10.1016/j.jtcvs.2018.11.144. Epub 2019 Mar 9.

    PMID: 30954300

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    Select item 31209650

     

    1. Coronary artery fistulae.

    Ali M, Kassem KM, Osei K, Effat M.

    J Thromb Thrombolysis. 2019 Aug;48(2):345-351. doi: 10.1007/s11239-019-01897-8. Review.

    PMID: 31209650

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    Select item 30561065

     

    1. Assessment of muscle oxygenation in children with congenital heart disease.

    Ross FJ, Arakaki LSL, Ciesielski WA, McMullan DM, Richards MJ, Geiduschek J, Latham G, Hsieh V, Schenkman KA.

    Paediatr Anaesth. 2019 Aug;29(8):850-857. doi: 10.1111/pan.13668. Epub 2019 Jun 19.

    PMID: 31125476

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    Select item 31342114

     

    1. Utility of 3D Printed Cardiac Models for Medical Student Education in Congenital Heart Disease: Across a Spectrum of Disease Severity.

    Smerling J, Marboe CC, Lefkowitch JH, Pavlicova M, Bacha E, Einstein AJ, Naka Y, Glickstein J, Farooqi KM.

    Pediatr Cardiol. 2019 Aug;40(6):1258-1265. doi: 10.1007/s00246-019-02146-8. Epub 2019 Jun 25.

    PMID: 31240370

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    Select item 31230092

     

    1. Comparative Cardiorespiratory Fitness in Children: Racial Disparity May Begin Early in Childhood.

    Bansal N, Mahadin DR, Smith R, French M, Karpawich PP, Aggarwal S.

    Pediatr Cardiol. 2019 Aug;40(6):1183-1189. doi: 10.1007/s00246-019-02129-9. Epub 2019 Jun 8.

    PMID: 31177302

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    Select item 31087143

     

    1. Critical association of Pallister-Hall syndrome and congenital heart disease.

    Ochiai M, Nagata H, Tanaka K, Ihara K, Ohga S.

    Pediatr Int. 2019 Aug;61(8):827-828. doi: 10.1111/ped.13945. Epub 2019 Aug 27. No abstract available.

    PMID: 31456264

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    Select item 31165901

     

    1. Characterisation of computed tomography angiography findings in paediatric patients with heterotaxy.

    Ugas Charcape CF, Alpaca Rodriguez LR, Matos Rojas IA, Lazarte Rantes CI, Valdez Quintana M, Katekaru Tokeshi DA, Epelman M.

    Pediatr Radiol. 2019 Aug;49(9):1142-1151. doi: 10.1007/s00247-019-04434-0. Epub 2019 Jun 5.

    PMID: 31165901

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    Select item 31203209

     

    1. Diffusion tensor cardiovascular magnetic resonance.

    Khalique Z, Pennell D.

    Postgrad Med J. 2019 Aug;95(1126):433-438. doi: 10.1136/postgradmedj-2019-136429. Epub 2019 Jun 15. Review.

    PMID: 31203209 Free Article

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    Select item 31087396

     

    1. Coexistence an aberrant right subclavian artery with other congenital anomalies: case report and review of the literature.

    Mrochek AG, Kabak SL, Haidzel IK, Melnichenko YM, Kalenchic TI.

    Surg Radiol Anat. 2019 Aug;41(8):963-967. doi: 10.1007/s00276-019-02206-x. Epub 2019 Feb 8.

    PMID: 30737539

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    1. Pediatric Malignancies: Is the Prechemotherapy Left Ventricular Function Normal?

    Akam-Venkata J, Kadiu G, Galas J, Aggarwal S.

    Echocardiography. 2019 Aug 31. doi: 10.1111/echo.14461. [Epub ahead of print]

    PMID: 31471982

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    Select item 31470900

     

    1. Relation Between Exercise Capacity and Extracardiac Conduit Size in Patients with Fontan Circulation.

    Lee SY, Song MK, Kim GB, Bae EJ, Kim SH, Jang SI, Cho SK, Kawk JG, Kim WH, Lee CH, Kim HJ, Kim J.

    Pediatr Cardiol. 2019 Aug 31. doi: 10.1007/s00246-019-02190-4. [Epub ahead of print]

    PMID: 31473799

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    Select item 31466543

     

    1. Anxiety, depression, and behavioural rating scales in children with non-cardiac chest pain.

    Kenar A, Örün UA, Yoldaş T, Kayalı Ş, Bodur Ş, Karademir S.

    Cardiol Young. 2019 Aug 30:1-4. doi: 10.1017/S1047951119001896. [Epub ahead of print]

    PMID: 31466543

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    Select item 31471941

     

    1. The effectiveness of enzyme replacement therapy on cardiac findings in patients with mucopolysaccharidosis.

    Bilginer Gurbuz B, Aypar E, Coskun T, Alehan D, Dursun A, Tokatli A, Sivri HS.

    J Pediatr Endocrinol Metab. 2019 Aug 30. pii: /j/jpem.ahead-of-print/jpem-2019-0293/jpem-2019-0293.xml. doi: 10.1515/jpem-2019-0293. [Epub ahead of print]

    PMID: 31469658

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    Select item 31468697

     

    1. Comparison of intranasal midazolam, intranasal ketamine, and oral chloral hydrate for conscious sedation during paediatric echocardiography: results of a prospective randomised study.

    Alp H, Elmacı AM, Alp EK, Say B.

    Cardiol Young. 2019 Aug 27:1-7. doi: 10.1017/S1047951119001835. [Epub ahead of print]

    PMID: 31451130

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    Select item 31451126

     

    1. The long-term outcome of an isolated vascular ring – A single-center experience.

    Depypere A, Proesmans M, Cools B, Vermeulen F, Daenen W, Meyns B, Rega F, Boon M.

    Pediatr Pulmonol. 2019 Aug 27. doi: 10.1002/ppul.24490. [Epub ahead of print]

    PMID: 31456344

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    Select item 31452268

     

    1. Base excess and hematocrit predict response to indomethacin in very low birth weight infants with patent ductus arteriosus.

    Mydam J, Rastogi A, Naheed ZJ.

    Ital J Pediatr. 2019 Aug 22;45(1):107. doi: 10.1186/s13052-019-0706-y.

    PMID: 31439021 Free PMC Article

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    Select item 31440767

     

    1. Herniated Liver Mimicking Right Atrial Mass.

    Stefan KK, Gernot G, Martin K, Michael R.

    Pediatr Cardiol. 2019 Aug 22. doi: 10.1007/s00246-019-02186-0. [Epub ahead of print]

    PMID: 31440767

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    Select item 31440766

     

    1. Cardiac CT in the Preoperative Diagnostics of Neonates with Congenital Heart Disease: Radiation Dose Optimization by Omitting Test Bolus or Bolus Tracking.

    Schindler P, Kehl HG, Wildgruber M, Heindel W, Schülke C.

    Acad Radiol. 2019 Aug 20. pii: S1076-6332(19)30368-X. doi: 10.1016/j.acra.2019.07.019. [Epub ahead of print]

    PMID: 31444109 Free Article

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    Select item 31432551

     

    1. Vascular Health of Children Conceived via In Vitro Fertilization.

    Zhang WY, Selamet Tierney ES, Chen AC, Ling AY, Fleischmann RR, Baker VL.

    J Pediatr. 2019 Aug 20. pii: S0022-3476(19)30885-6. doi: 10.1016/j.jpeds.2019.07.033. [Epub ahead of print]

    PMID: 31443895

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    Select item 31429918

     

    1. Coronary artery assessment in Kawasaki disease with dual-source CT angiography to uncover vascular pathology.

    van Stijn-Bringas Dimitriades D, Planken RN, Groenink M, Streekstra GJ, Kuijpers TW, Kuipers IM.

    Eur Radiol. 2019 Aug 19. doi: 10.1007/s00330-019-06367-6. [Epub ahead of print]

    PMID: 31428828

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    Select item 31426113

     

    1. Prevalence of Pulmonary Hypertension in Pediatric Patients With Obstructive Sleep Apnea and a Cardiology Evaluation: A Retrospective Analysis.

    Burns AT, Hansen SL, Turner ZS, Aden JK, Black AB, Hsu DP.

    J Clin Sleep Med. 2019 Aug 15;15(8):1081-1087. doi: 10.5664/jcsm.7794.

    PMID: 31482829

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    Select item 31414622

     

    1. Bodyweight-adjusted rivaroxaban for children with venous thromboembolism (EINSTEIN-Jr): results from three multicentre, single-arm, phase 2 studies.

    Monagle P, Lensing AWA, Thelen K, Martinelli I, Male C, Santamaría A, Samochatova E, Kumar R, Holzhauer S, Saracco P, Simioni P, Robertson J, Grangl G, Halton J, Connor P, Young G, Molinari AC, Nowak-Göttl U, Kenet G, Kapsa S, Willmann S, Pap AF, Becka M, Twomey T, Beyer-Westendorf J, Prins MH, Kubitza D; EINSTEIN-Jr Phase 2 Investigators.

    Lancet Haematol. 2019 Aug 13. pii: S2352-3026(19)30161-9. doi: 10.1016/S2352-3026(19)30161-9. [Epub ahead of print]

    PMID: 31420317

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    Select item 31412610

     

    1. Discovering dad: paternal roles, responsibilities, and support needs as defined by fathers of children with complex cardiac conditions perioperatively.

    Robinson J, Huskey D, Schalley S, Wratchford D, Hammel J, Weaver MS.

    Cardiol Young. 2019 Aug 8:1-6. doi: 10.1017/S1047951119001586. [Epub ahead of print]

    PMID: 31391137

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    Select item 31393559

     

    1. Acute Abdomen in Kawasaki Disease.

    Velez-Tirado N, Ridaura-Sanz C, Venegas-Montoya E, Scheffler-Mendoza S, Camacho-Moreno R, Otero-Mendoza F, Medina-Vega FA, Garrido-García LM, Rivas-Larrauri F, Nakashimada MAY.

    Indian J Pediatr. 2019 Aug 7. doi: 10.1007/s12098-019-03048-6. [Epub ahead of print] No abstract available.

    PMID: 31388920

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    Select item 31392380

     

    1. Correlation of Echocardiogram and Exercise Test Data in Children with Aortic Stenosis.

    Santana S, Gidding SS, Xie S, Jiang T, Kharouf R, Robinson BW.

    Pediatr Cardiol. 2019 Aug 7. doi: 10.1007/s00246-019-02177-1. [Epub ahead of print]

    PMID: 31392379

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    Select item 31389740

     

    1. RIKADA Study Reveals Risk Factors in Pediatric Primary Cardiomyopathy.

    Al-Wakeel-Marquard N, Degener F, Herbst C, Kühnisch J, Dartsch J, Schmitt B, Kuehne T, Messroghli D, Berger F, Klaassen S.

    J Am Heart Assoc. 2019 Aug 6;8(15):e012531. doi: 10.1161/JAHA.119.012531. Epub 2019 Jul 23.

    PMID: 31333075 Free Article

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    Select item 31388700

     

    1. Bands in the Heart: Multimodality Imaging Review.

    Rajiah P, MacNamara J, Chaturvedi A, Ashwath R, Fulton NL, Goerne H.

    Radiographics. 2019 Aug 2:180176. doi: 10.1148/rg.2019180176. [Epub ahead of print]

    PMID: 31373865

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    Select item 31089779

     

    1. Familial aggregation of “apple peel” intestinal atresia and cardiac left-sided obstructive lesions: A possible causal relationship with NOTCH1 gene mutations.

    Digilio MC, Magliozzi M, Di Pede A, Valfrè L, Dentici ML, Auriti C, Marino B, Novelli A, Dallapiccola B.

    Am J Med Genet A. 2019 Aug;179(8):1570-1574. doi: 10.1002/ajmg.a.61195. Epub 2019 May 20.

    PMID: 31111652

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    Select item 31375646

     

    1. A case of right aortic arch with isolated left innominate artery and global cerebral white matter atrophy.

    Binka E, Sun LR, Gailloud P, Chiu JS.

    Cardiol Young. 2019 Aug;29(8):1107-1109. doi: 10.1017/S1047951119001537. Epub 2019 Jul 10.

    PMID: 31288876

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    Select item 31287039

     

    1. Anomalous single trunk coronary artery from the right pulmonary artery.

    Donmez YN, Aykan HH, Yilmaz M.

    Cardiol Young. 2019 Aug;29(8):1088-1090. doi: 10.1017/S1047951119001379. Epub 2019 Jun 28.

    PMID: 31250782

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    Select item 31244446

     

    1. Isolated retroaortic innominate vein and right aortic arch: a case report and review of literature.

    Kohli U.

    Cardiol Young. 2019 Aug;29(8):1091-1093. doi: 10.1017/S1047951119001380. Epub 2019 Jun 21.

    PMID: 31221230

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    Select item 31208473

     

    1. A standardized imaging protocol improves quality and reduces practice variability in echocardiographic assessment of ventricular function by first-year pediatric cardiology fellows.

    White BR, Ho DY, Rogers LS, Natarajan SS.

    Echocardiography. 2019 Aug;36(8):1515-1523. doi: 10.1111/echo.14441. Epub 2019 Aug 5.

    PMID: 31385382

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    Select item 31260138

     

    1. Systematic literature review on the economic, humanistic, and societal burden of heart failure in children and adolescents.

    Burch M, Nallagangula TK, Nic Lochlainn E, Severin T, Thakur L, Jaecklin T, George AT, Solar-Yohay S, Rossano JW, Shaddy RE.

    Expert Rev Pharmacoecon Outcomes Res. 2019 Aug;19(4):397-408. doi: 10.1080/14737167.2019.1579645. Epub 2019 Mar 5.

    PMID: 30747011

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    Select item 30675029

     

    1. Correction: Arterial tortuosity syndrome: 40 new families and literature review.

    Beyens A, Albuisson J, Boel A, Al-Essa M, Al-Manea W, Bonnet D, Bostan O, Boute O, Busa T, Canham N, Cil E, Coucke PJ, Cousin MA, Dasouki M, De Backer J, De Paepe A, De Schepper S, De Silva D, Devriendt K, De Wandele I, Deyle DR, Dietz H, Dupuis-Girod S, Fontenot E, Fischer-Zirnsak B, Gezdirici A, Ghoumid J, Giuliano F, Baena N, Haider MZ, Hardin JS, Jeunemaitre X, Klee EW, Kornak U, Landecho MF, Legrand A, Loeys B, Lyonnet S, Michael H, Moceri P, Mohammed S, Muiño-Mosquera L, Nampoothiri S, Pichler K, Prescott K, Rajeb A, Ramos-Arroyo M, Rossi M, Salih M, Seidahmed MZ, Schaefer E, Steichen-Gersdorf E, Temel S, Uysal F, Vanhomwegen M, Van Laer L, Van Maldergem L, Warner D, Willaert A, Collins Ii TR, Taylor A, Davis EC, Zarate Y, Callewaert B.

    Genet Med. 2019 Aug;21(8):1894-1895. doi: 10.1038/s41436-018-0035-3.

    PMID: 30201961

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    Select item 30916392

     

    1. Biallelic mutation in MYH7 and MYBPC3 leads to severe cardiomyopathy with left ventricular noncompaction phenotype.

    Kolokotronis K, Kühnisch J, Klopocki E, Dartsch J, Rost S, Huculak C, Mearini G, Störk S, Carrier L, Klaassen S, Gerull B.

    Hum Mutat. 2019 Aug;40(8):1101-1114. doi: 10.1002/humu.23757. Epub 2019 Apr 24.

    PMID: 30924982

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    Select item 31020596

     

    1. Association of left ventricular size with regional right ventricular mechanics in Hypoplastic Left Heart Syndrome.

    Forsha D, Li L, Joseph N, Kutty S, Friedberg MK.

    Int J Cardiol. 2019 Aug 1. pii: S0167-5273(19)33278-4. doi: 10.1016/j.ijcard.2019.07.090. [Epub ahead of print]

    PMID: 31402159

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    Select item 31402156

     

    1. Improvement of the outcome in patients with infantile dilated cardiomyopathy over three decades – The usefulness of long-term gradually medical supportive care.

    Tsuda E, Yamada O, Kitano M.

    J Cardiol. 2019 Aug;74(2):189-194. doi: 10.1016/j.jjcc.2019.02.005. Epub 2019 Mar 12.

    PMID: 30876708

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    Select item 30852093

     

    1. Neonatal Marfan Syndrome: A Rare, Severe, and Life-Threatening Genetic Disease.

    Solé-Ribalta A, Rodríguez-Fanjul X, Carretero-Bellon JM, Pascual-Sala C, Martorell-Sampol L, Bobillo-Pérez S, Morillo-Palomo AM.

    J Pediatr. 2019 Aug;211:221-221.e2. doi: 10.1016/j.jpeds.2019.03.033. Epub 2019 Apr 30. No abstract available.

    PMID: 31053350

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    Select item 30952511

     

    1. Evaluation of pulmonary endothelial function in Fontan patients.

    Latus H, Lederle A, Khalil M, Kerst G, Schranz D, Apitz C.

    J Thorac Cardiovasc Surg. 2019 Aug;158(2):523-531.e1. doi: 10.1016/j.jtcvs.2018.11.144. Epub 2019 Mar 9.

    PMID: 30954300

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    Select item 30536443

     

    1. In reply-Strategies of Screening for Fabry Disease in Patients With Unexplained Left Ventricular Hypertrophy.

    Newman DB, Ackerman MJ.

    Mayo Clin Proc. 2019 Aug;94(8):1646. doi: 10.1016/j.mayocp.2019.05.004. No abstract available.

    PMID: 31378242

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    Select item 31266678

     

    1. Through Tricuspid Closure for Doubly Committed Subarterial Ventricular Septal Defect with Right Vertical Subaxillary Mini-incision: A Matched-Pair Analysis.

    Liu R, Rui L, Zhang B, Lin Y, Li S, Hua Z.

    Pediatr Cardiol. 2019 Aug;40(6):1247-1252. doi: 10.1007/s00246-019-02144-w. Epub 2019 Jul 23.

    PMID: 31338560

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    Select item 31317219

     

    1. Superior Vena Cava Inflow Following Repair for Anomalous Right Pulmonary Venous Drainage in Children.

    Federspiel JM, Das De S, Lilley S, Smith B, Danton M, McLean A, MacArthur K, Peng E.

    Pediatr Cardiol. 2019 Aug;40(6):1275-1283. doi: 10.1007/s00246-019-02148-6. Epub 2019 Jul 12.

    PMID: 31300841

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    Select item 31263917

     

    1. Saline Contrast Transesophageal Echocardiography in Fontan Patients: Assessment of the Presence, Type, and Size of Right to Left Shunts.

    Zaidi SJ, Adhikari RR, Patel DR, Cui VW, Javois AJ, Roberson DA.

    Pediatr Cardiol. 2019 Aug;40(6):1199-1207. doi: 10.1007/s00246-019-02132-0. Epub 2019 Jun 19.

    PMID: 31218373

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    Select item 31218372

     

    1. Comparison Between Nomograms Used to Define Pediatric Aortic Arch Hypoplasia: Retrospective Evaluation Among Patients Less Than 1 Year Old with Coarctation of the Aorta.

    Şişli E, Kalın S, Tuncer ON, Ayık MF, Alper H, Levent RE, Şahin H, Atay Y.

    Pediatr Cardiol. 2019 Aug;40(6):1190-1198. doi: 10.1007/s00246-019-02130-2. Epub 2019 Jun 5.

    PMID: 31165902

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    Select item 31152185

     

    1. Thenar Muscle Oxygen Saturation Using Vascular Occlusion Test: A Novel Technique to Study Microcirculatory Abnormalities in Pediatric Heart Failure Patients.

    Samraj RS, Lopez-Colon D, Kerrigan M, Fricker FJ, Pietra BA, Bleiweis M, Gupta D.

    Pediatr Cardiol. 2019 Aug;40(6):1151-1158. doi: 10.1007/s00246-019-02118-y. Epub 2019 May 16.

    PMID: 31098675

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    Select item 31087144

     

    1. Excessive soft drink may induce pulmonary hypertension via thiamine deficiency.

    Sakurai K, Fujiwara N, Takahashi K, Nakayashiro M.

    Pediatr Int. 2019 Aug;61(8):823-824. doi: 10.1111/ped.13913. Epub 2019 Aug 1. No abstract available.

    PMID: 31373121

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    Select item 31172686

     

    1. The Thoracic and Cardiovascular Surgeon and the Pediatric Cardiologist.

    Dittrich S.

    Thorac Cardiovasc Surg. 2019 Aug;67(5):330. doi: 10.1055/s-0039-1693656. Epub 2019 Aug 9. No abstract available.

    PMID: 31398729

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    Select item 31082372

     

    1. [Clinical effect and safety of clopidogrel combined with aspirin in antithrombotic therapy for children with Kawasaki disease complicated by small/medium-sized coronary artery aneurysms].

    Liu YL, Wang XM, Chen TT, Shi K, Lu YH, Guo YH, Li Y.

    Zhongguo Dang Dai Er Ke Za Zhi. 2019 Aug;21(8):801-805. Chinese.

    PMID: 31416506

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    aneurysms].

Liu YL, Wang XM, Chen TT, Shi K, Lu YH, Guo YH, Li Y.

Zhongguo Dang Dai Er Ke Za Zhi. 2019 Aug;21(8):801-805. Chinese.

PMID: 31416506

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ACHD Featured Articles in association with ISACHD

Adult Congenital Heart Reviews of August 2019 manuscripts (sponsored by ISACHD)

 

Relation of Magnetic Resonance Elastography to Fontan Failure and Portal Hypertension.
Alsaied T, Possner M, Lubert AM, Trout AT, Szugye C, Palermo JJ, Lorts A, Goldstein BH, Veldtman GR, Anwar N, Dillman JR.
Am J Cardiol. 2019 Aug 7. pii: S0002-9149(19)30883-5. doi: 10.1016/j.amjcard.2019.07.052. [Epub ahead of print]
PMID: 31474329
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Select item 31400339

Take Home Points:
• Magnetic resonance elastography (MRE) is a non-invasive method of assessing liver stiffness and liver fibrosis.
• In this study of 70 adult Fontan patients, all had increased MRE liver stiffness (greater than 2.9 kPa is the cutoff used as this institution).
• Liver stiffness of 4.5 kPa or greater is associated with Fontan failure (sensitivity of 77% and specificity of 77%) and radiologic signs of portal hypertension (sensitivity of 69% and specificity of 65%).
• MRE-derived liver stiffness is associated with adverse hemodynamics, liver function, and clinical outcomes in Fontan circulation.

Commentary from Dr. Maan Jokhadar (Atlanta GA), section editor of ACHD Journal Watch:
Fontan associated liver disease (FALD) is associated with Fontan failure (FF) and appears to be multifactorial with contributing factors that include elevated central venous pressure and chronic liver congestion, low cardiac output, abnormal liver lymphatic drainage, and other factors. Assessing FALD and FF with liver biopsy is of limited reliability due to the non-uniform nature of fibrosis in this population. Noninvasive assessment of liver stiffness including magnetic resonance elastography (MRE) has shown mixed results.
Dr. Alsaied and colleagues from the University of Cincinnati performed a retrospective cohort analysis of 70 adult Fontan patients who were evaluated between 2012 and 2018 to determine the role of MRE as a measure of liver stiffness and its relationship to hemodynamics, liver enzymes, portal hypertension, and FF. In this study, FF was defined as death, heart transplant listing, or heart failure symptoms requiring escalation and diuretic therapy. The upper limit for normal liver stiffness at this institution is 2.9 kPa.
The median age was almost 25 years and 52% were men. The median follow-up from the time of MRE was 3.9 years. There is no significant correlation between MRE liver stiffness and age or time since Fontan. There was one case of hepatocellular carcinoma detected with MRE screening.
There was a moderate negative correlation of liver stiffness with ventricular ejection fraction and ventricular end diastolic volume. Patients with moderate to severe atrioventricular valve regurgitation had significantly higher liver stiffness compared to patients with no or mild regurgitation. Also, patients with a history of thromboembolism had higher liver stiffness compared to patients without prior thromboembolism. There was a very mild positive correlation between liver enzyme elevations and liver stiffness. There was no difference in laboratory values in patients with or without FF.
Patients with features of portal hypertension including splenomegaly, varices, or ascites had higher liver stiffness compared to patients without these features. Liver stiffness had a weak negative correlation with platelet count. Using ROC analysis liver stiffness had an area under the curve of 0.69 to differentiate portal hypertension and it should be noted that liver stiffness above 4.5 K PA differentiated portal hypertension with the sensitivity of 69% and specificity of 65%.
FF was present in 19 patients (4 deaths, 1 heart transplant, and 8 with worsening heart failure, 1 of whom received LVAD. FF patients had higher liver stiffness. A liver stiffness above 4.5 kPa differentiated FF with sensitivity of 77% and specificity of 77%.
All adult Fontan patients in this study had increased liver stiffness by MRE and this correlated with increased Fontan pressure, lower ventricular ejection fraction, atrioventricular valve regurgitation severity, FF, elevated liver enzymes, and radiologic signs of portal hypertension.
Liver stiffness in FALD is a function of both congestion and fibrosis and this may explain previous studies showing discrepant data regarding the correlation of MRE and biopsy measures of fibrosis. In contrast with previous studies, this study of adult Fontan patient showed that MRE liver stiffness was not associated with time since Fontan.
The study authors suggest that MRE could be used routinely in Fontan patients as part of routine assessment cardiac and liver “health”, which could be used as a global assessment of the Fontan circulation that correlates with the development of clinical symptoms and outcomes. Abnormal MRE liver stiffness could then trigger more detailed evaluation.
Additional prospective, multi centered studies with longer serial follow-up and changes with medication and/or intervention are needed before recommending routine MRE surveillance for Fontan patients. using this technique. Cost effectiveness should also be considered.

Creatinine versus cystatin C to estimate glomerular filtration rate in adults with congenital heart disease: Results of the Boston Adult Congenital Heart Disease Biobank.
Opotowsky AR, Carazo M, Singh MN, Dimopoulos K, Cardona-Estrada DA, Elantably A, Waikar SS, McCausland FR, Veldtman G, Grewal J, Gray C, Loukas BN, Rajpal S.
Am Heart J. 2019 Aug;214:142-155. doi: 10.1016/j.ahj.2019.04.018. Epub 2019 May 22.
PMID: 31203159
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Select item 31204032

Take Home Points:
• Chronic kidney disease, defined by reduced estimated glomerular filtration rate (eGFR), is associated with worse prognosis, and is common among adults with congenital heart disease compared to similarly aged peers
• eGFR calculations using creatinine can be inaccurate when actual muscle mass differs from expected population-based norms, as is seen in some adult CHD subjects – especially the single-ventricle Fontan population
• In a heterogenous cohort of 911 adults with CHD, cystatin C-based eGFR (CKD-EPICysC) classified a larger proportion of patients as having moderate or severely reduced eGFR as compared to creatinine-based eGFR (CKD-EPICr)
• CKD-EPICr tended to overestimate eGFR in the low to mid-range and underestimate eGFR at the higher end of the range, compared with CKD-EPICysC
• Cystatin C-based eGFR better predicted all-cause mortality, and the composite of death or non-elective cardiovascular hospitalization.
• In the single-ventricle Fontan circulation subset there was poor agreement between creatinine-based and cystatin C-based eGFR.
• Measurement of cystatin C to better estimate eGFR should be considered in those with mildly reduced eGFR, and single-ventricle Fontan circulation patients.

Commentary from Dr. Timothy Roberts (Melbourne), section editor of ACHD Journal Watch:
The aim of this study was (1) to determine the correlation and agreement between various eGFR equations and (2) to compare the prognostic value of creatinine and cystatin C-based eGFR equations.
The primary outcomes of interest were (1) all-cause mortality and (2) a composite outcome of either all-cause mortality or non-elective cardiovascular hospitalization.
Adult patients were recruited from Boston Children’s or Brigham and Women’s Hospitals between 2012 – 2017. Patients were classified into different CHD pathophysiologic groups, New York Heart Association (NYHA) functional class, presence of cyanosis, diagnosis severity, and the presence of a single-ventricle versus biventricular circulation. Average age was 38.6 +/- 13.6 years, and 49.2 % were female. The majority (78.3 %) of subjects had moderate or severe complexity of CHD. The most common underlying diagnoses were:
• left-sided obstructive lesions (n=200, 22.0%),
• tetralogy of Fallot (n=187, 20.5%),
• single-ventricle physiology with a Fontan palliation (n=131, 14.4%),
• simple shunt lesion without clinical sequelae (n=122, 13.4%), and
• transposition of the great arteries with a systemic right ventricle (n=84, 9.2%).
Hypertension was present in 144 (14.6%) and diabetes in 38 (4.6%) patients.
The prevalence of chronic kidney disease according to eGFR is shown below in Figure 1 using various equations:

GFR category was classified differently in 228 of the 911 patients by the CKD-EPICr and CKD-EPICysC equations. For both CKD-EPI equations, lower eGFR was associated with older age, higher BMI, hypertension, diabetes, atrial arrhythmias, pulmonary hypertension, cyanosis, and functional class. Average eGFR was similar for both CKD-EPI methods, however there was heterogeneity between different types of CHD. In particular, in the 131 patients with a single-ventricle Fontan circulation, creatinine-based eGFR was, on average, 10.3 +/- 19.3 higher with 95 % limits of agreement -28.2 to +48.8 ml/min/1.73 m2. For both single-ventricle Fontan and biventricular circulations, CKD-EPICr tended to overestimate eGFR in the low to mid-range and underestimate eGFR at the higher end of the range, compared with CKD-EPICysC.

In univariate analysis, there was a higher risk for both all-cause mortality and the composite outcome for patients categorized in the lowest eGFR category for all eGFR equations. There was a clear stepwise increase in risk for adverse outcomes across the 3 eGFR categories for CKD-EPICysC (figure 4, below). Multivariate adjustment was not performed for all-cause mortality due to low event numbers (n=34, 3.1%); however, for the composite outcome, only the CKD-EPICysC eGFR category remained a significant predictor on multivariate analysis. In the single-ventricle Fontan circulation cohort, higher CKD-EPICysC eGFR was associated with lower risk of the composite outcome (41 events in 131 patients; HR = 0.85 [0.76-0.95], P=0.005, C-statistic 0.652) whereas neither of the purely creatinine-based eGFR methods was significantly associated with the risk of the composite outcome.

The authors conclude that more accurate identification of renal dysfunction could enable earlier intervention targeted at mechanisms of kidney disease, more appropriate drug dosing for renally cleared cardiovascular medications, assessment of risk when using iodinated contrast media for CT and catheterization, identification of patients at highest risk for acute kidney injury after surgery involving cardiopulmonary bypass, and more informed consideration during heart transplant evaluation.
It should be noted that cystatin C levels can be affected by other variables which were not assessed in the current study. Only a single measurement was considered, without factoring in the time since surgery nor changes on repeated measurements. The cost-benefit balance of measuring cystatin C is also unclear. Nonetheless, the study ultimately raises concern for the reliance on creatinine-based eGFR calculations, especially for single-ventricle Fontan circulation patients.

Echocardiographic predictors of elevated left ventricular end diastolic pressure in adolescent and adult patients with repaired tetralogy of Fallot.
Lubert AM, Cotts TB, Zampi JD, Yu S, Norris MD.
Cardiol Young. 2019 Aug;29(8):1020-1024. doi: 10.1017/S1047951119001331. Epub 2019 Jun 18.
PMID: 31208473
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Select item 31067002

Take Home Points:
 Elevated LVEDP is a risk factor for ventricular arrhythmias in patients with Tetralogy of Fallot.
 Small retrospective study of patients > 13 yrs old (n=94) who had a left heart catheter within 7 days of TTE.
 Univariable comparison made between TTE and clinical variables in patients with LVEDP >12mmHg and <12mmHg.
 Patients with LVEDP >12mmHg were older, more likely to have a history of aortopulmonary shunt and hypertension compared to patients with an LVEDP <12mmHg.
 Patients with LVEDP >12mmHg have larger left atrial areas (mean 17.7 vs 14 cm2, p=0.03).
 No significant differences in E/A ration, annular e’ velocity, or E/e’ ratio between patients with LVEDP >12mmHg vs < 12mmHg.
 In this small study in patients with TOF, typical measures of diastolic dysfunction on TTE were unreliable in predicting patients who had elevated LVEDP. Larger prospective studies are required to investigate this further.

Commentary from Dr. Damien Cullington (Liverpool, United Kingdom), section editor of ACHD Journal Watch: LVEDP has been shown to be a risk factor for ventricular arrhythmias and worse survival in patients with TOF. The only sure-fire way to measure LVEDP is to perform a cardiac catheter study – obviously this is an invasive test requiring significant resources to perform. For some patients, it is unpleasant plus anxiety provoking so any way of avoiding would be preferable.
Over decades of research, mostly in the non-congenital cardiac population, a number of echocardiographic measures have been investigated as surrogate measures of raised LVEDP such as E/A, E/e’ and LA volume.
This small retrospective study sought to correlate non-invasive TTE measures of raised LVEDP with direct catheter measurement in a group of young patients with tetralogy of Fallot. Compared with other analyses, in the non ACHD population, LVEDP measured by catheter did not seem to correlate with usual surrogates of LVEDP measured on TTE. It is unknown how many patients with TOF have elevated LVEDP on catheter but normal TTE diastology indices.

This analysis collated data over 16 years (2001-2017) in patients > 13 years old with TOF or pulmonary atresia with VSD. All patients had a TTE within 7 days of a cardiac catheter study. The clinical characteristics of the cohort are shown in Table 1.

Salient points to note from the clinical characteristics of the cohort are that almost half of patients had had an aorto-pulmonary shunt and 60% had a transannular patch with 18% having experienced ventricular arrhythmias. A quarter of patients required loop diuretics suggesting these patients had established heart failure. The characteristics differ from a contemporary cohort of TOF patients whom would have far fewer numbers of patients with transannular patches and shunts.
Just over a third of patients (n=34) had an LVEDP >12mmHg. Univariable factors associated with LVEDP >12mmHg were age, weight, previous aortopulmonary shunt, a pacemaker and hypertension – Table 2.

The most reliable predictors of a LVEDP >12mmHg were measures of LA size – Doppler measures, were not.
There is fertile ground here for further investigation, ideally with a much larger sample size. Over half of the patients with a LVEDP >12mmHg had severe PR plus proportionally greater numbers with > moderate TR. It would certainly be of interest to understand the influence of PR on LVEDP and whether in patients who had undergone PVR had lower LVEDPs.

CMR feature tracking left ventricular strain-rate predicts ventricular tachyarrhythmia, but not deterioration of ventricular function in patients with repaired tetralogy of Fallot.
Hagdorn QAJ, Vos JDL, Beurskens NEG, Gorter TM, Meyer SL, van Melle JP, Berger RMF, Willems TP.
Int J Cardiol. 2019 Aug 1. pii: S0167-5273(19)30911-8. doi: 10.1016/j.ijcard.2019.07.097. [Epub ahead of print]
PMID: 31402156 Free Article
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Select item 31161492

Take Home Points:
 CMR-feature tracking derived measures of myocardial deformation are valuable for the prediction of VT or deterioration of ventricular function in patients with repaired TOF.
 LV systolic and diastolic circumferential strain-rate are identified as strong predictors of VT, of which LV systolic circumferential strain-rate was an independent predictor.
 No association between strain and strain-rate parameters and deterioration of ventricular function.

Commentary from Dr. Soha Romeih (Aswan, Egypt), section editor of ACHD Journal Watch:
TOF is one of the most common CHD, with excellent survival into adulthood when surgical repair is performed early in childhood. However, progressive RV dysfunction, due to residual pulmonary incompetence, and LV dysfunction are believed to from a substrate for electrical instability, resulting in both atrial and ventricular tachyarrhythmias.
Ventricular strain is a measure of relative deformation in a certain direction, with the unit percentage. In contrast, strain-rate measures the rate of this deformation, and therefore provides conceptually different information regarding myocardial performance. Furthermore, strain rate can be measured during both contraction phase and relaxation phase, providing information on systolic and diastolic function. The predictive value of CMR derived strain-rate parameters has not been reported previously in patients with repaired TOF. Thus, it remains unknown whether the conceptual differences between strain and strain-rate translate into different prognostic potential.
The aim of this study was to investigate the value of both CMR-feature tracking derived strain and strain-rate as predictors for VT, and additionally as a predictor for deterioration of ventricular function on CMR in patients with repaired TOF.

Patients with repaired TOF who underwent CMR investigation were included. Strain and strain-rate of both ventricles were assessed using CMR feature tracking.
The primary outcome was a composite of the occurrence of sustained VT or non-sustained VT requiring invasive therapy. The secondary outcome was analyzed in patients that underwent a second CMR after 1.5 to 3.5 years. Deterioration was defined as reduction (≥10%) in right ventricular (RV) ejection fraction, reduction (≥10%) in left ventricular (LV) ejection fraction or increase (≥30mL/m2) in indexed RV end-diastolic volume compared to baseline.

In total, 172 patients were included in this study, with a median age at the time of CMR examination of 24.3 years (interquartile range (IQR)15.9–35.4). Due to significant artifacts, 11 patients were excluded.
Of the included patients, 54 patients (31%) were pediatric (>18 years). Mass and volume measurements could be performed in 169 patients(98%), pulmonary flow measurements could be performed in 166 patients (97%), and strain measurements could be performed in 166 patients (97%). Within the predefined timeframe, a baseline echocardiographic examination was available for 143 patients (83%), and a baseline ECG examination was available for 162 patients (94%).

1. Primary endpoint: Ventricular tachyarrhythmias

9 patients (4.5%) experienced the primary outcome. Univariate Cox-regression analysis showed no significant associations between RV-strain variables and primary outcome. However, a significant association of both systolic and diastolic LV circumferential strain-rate with primary outcome was demonstrated.

2. Secondary endpoint: ventricular deterioration

70 patients were included for secondary endpoint analysis. Of these, 14 patients were classified as deteriorated and 56 as not deteriorated. At baseline, RV EDVi and RV mass index were significantly different between the deteriorated and not-deteriorated group (145.7 ± 29.3 vs. 121.1 ± 32.4 mL/m2, p = 0.012 and 47.0 ± 8.1 vs.41.5 ± 9.3 g/m2, p = 0.048 respectively).
Using logistic regression, only RV EDVi at baseline appeared significantly associated with deterioration (p = 0.018, odds ratio 1.26, 95% CI 1.04–1.51 per 10 mL/m2 increase) whereas for RV mass index, there was a borderline significant association (p=0.055, odds ratio 1.37, 95% CI 1.00–1.88 per 5 g/m2 increase). None of the strain or strain-rate variables were associated with deterioration.

Conclusion:

The present study shows that systolic LV circumferential strain-rate is a strong predictor for the primary endpoint of VT, independent of conventional variables in a population of both children and adults with repaired TOF.
Furthermore, RV EDVi was associated with deterioration of ventricular function. On the contrary, no association could be demonstrated between strain and strain-rate parameters and deterioration of ventricular function.
As surveillance for potentially life-threatening arrhythmias and ventricular deterioration is key in the long-term clinical follow-up of repaired TOF, the current study suggests that strain-rate parameters may improve risk stratification in these patients.

ACHD August 2019

 

 

  1. Clinical impact of cardiac computed tomography derived three-dimensional strain for adult congenital heart disease: a pilot study.

Shiina Y, Inai K, Takahashi T, Shimomiya Y, Nagao M.

Int J Cardiovasc Imaging. 2019 Aug 30. doi: 10.1007/s10554-019-01691-w. [Epub ahead of print]

PMID: 31471763

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Select item 31468697

 

  1. Peripartum Management of Pregnant Women With Congenital Heart Disease.

Yamasaki K, Sawatari H, Konagai N, Kamiya CA, Yoshimatsu J, Muneuchi J, Watanabe M, Fukuda T, Mizuno A, Sakamoto I, Yamamura K, Ohkusa T, Tsutsui H, Niwa K, Chishaki A.

Circ J. 2019 Aug 29. doi: 10.1253/circj.CJ-19-0369. [Epub ahead of print]

PMID: 31462608 Free Article

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Select item 31464030

 

  1. BNP Level in Pregnant Women with Congenital Heart Disease Predicts SGA Offspring.

Ishida S, Uchiyama A, Imai K, Kusuda S.

Pediatr Int. 2019 Aug 28. doi: 10.1111/ped.13997. [Epub ahead of print]

PMID: 31461203

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Select item 31454161

 

  1. Tricuspid regurgitation severity after atrial septal defect closure or pulmonic valve replacement.

Martin-Garcia AC, Dimopoulos K, Boutsikou M, Martin-Garcia A, Kempny A, Alonso-Gonzalez R, Swan L, Uebing A, Babu-Narayan SV, Sanchez PL, Li W, Shore D, Gatzoulis MA.

Heart. 2019 Aug 23. pii: heartjnl-2019-315287. doi: 10.1136/heartjnl-2019-315287. [Epub ahead of print]

PMID: 31444268

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Select item 31451185

 

  1. Psycho-affective pathology in adults with congenital heart disease: Important progress is being made within a challenging field.

Wallert J, Held C, Madison G, Olsson E.

Eur J Prev Cardiol. 2019 Aug 21:2047487319871629. doi: 10.1177/2047487319871629. [Epub ahead of print] No abstract available.

PMID: 31433667

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Select item 31434996

 

  1. Prevalence and risk factors for low bone density in adults with a Fontan circulation.

D’Ambrosio P, Tran D, Verrall CE, Attard C, Singh MF, Ayer J, d’Udekem Y, Twigg S, Celermajer DS, Cordina R.

Congenit Heart Dis. 2019 Aug 20. doi: 10.1111/chd.12836. [Epub ahead of print]

PMID: 31430042

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Select item 31482076

 

  1. Clinical Outcomes During Admissions for Heart Failure Among Adults With Congenital Heart Disease.

Agarwal A, Dudley CW, Nah G, Hayward R, Tseng ZH.

J Am Heart Assoc. 2019 Aug 20;8(16):e012595. doi: 10.1161/JAHA.119.012595. Epub 2019 Aug 17.

PMID: 31423885 Free Article

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Select item 31429492

 

  1. Oral Health in Adults with Congenital Heart Disease.

Folwaczny M, Wilberg S, Bumm C, Hollatz S, Oberhoffer R, Neidenbach RC, Kaemmerer H, Frasheri I.

J Clin Med. 2019 Aug 19;8(8). pii: E1255. doi: 10.3390/jcm8081255.

PMID: 31430933 Free Article

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Select item 31427341

 

  1. Recognition and management of adults with Turner syndrome: From the transition of adolescence through the senior years.

Lin AE, Prakash SK, Andersen NH, Viuff MH, Levitsky LL, Rivera-Davila M, Crenshaw ML, Hansen L, Colvin MK, Hayes FJ, Lilly E, Snyder EA, Nader-Eftekhari S, Aldrich MB, Bhatt AB, Prager LM, Arenivas A, Skakkebaek A, Steeves MA, Kreher JB, Gravholt CH.

Am J Med Genet A. 2019 Aug 16. doi: 10.1002/ajmg.a.61310. [Epub ahead of print]

PMID: 31418527

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Select item 31419019

 

  1. Prevalence of Mental Illness in Adolescents and Adults With Congenital Heart Disease from the Colorado Congenital Heart Defect Surveillance System.

Khanna AD, Duca LM, Kay JD, Shore J, Kelly SL, Crume T.

Am J Cardiol. 2019 Aug 15;124(4):618-626. doi: 10.1016/j.amjcard.2019.05.023. Epub 2019 Jun 11.

PMID: 31303246

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Select item 31208700

 

  1. Hippocampal alterations and functional correlates in adolescents and young adults with congenital heart disease.

Fontes K, Rohlicek CV, Saint-Martin C, Gilbert G, Easson K, Majnemer A, Marelli A, Chakravarty MM, Brossard-Racine M.

Hum Brain Mapp. 2019 Aug 15;40(12):3548-3560. doi: 10.1002/hbm.24615. Epub 2019 May 9.

PMID: 31070841

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Select item 31072635

 

  1. Body composition changes assessment by bioelectrical impedance vectorial analysis in right heart failure and left heart failure.

González-Islas D, Arámbula-Garza E, Orea-Tejeda A, Castillo-Martínez L, Keirns-Davies C, Salgado-Fernández F, Hernández-Urquieta L, Hernández-López S, Pilotzi-Montiel Y.

Heart Lung. 2019 Aug 14. pii: S0147-9563(19)30234-1. doi: 10.1016/j.hrtlng.2019.07.003. [Epub ahead of print]

PMID: 31421949

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Select item 31439426

 

  1. Sarcopenia: An unrecognized, but important factor for adults with congenital heart disease.

Maurer SJ, Tutarel O.

Int J Cardiol. 2019 Aug 14. pii: S0167-5273(19)33022-0. doi: 10.1016/j.ijcard.2019.08.030. [Epub ahead of print] No abstract available.

PMID: 31439426

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Select item 31421934

 

  1. Impact of facilities accredited by both adult and pediatric cardiology societies on the outcome of patients with adult congenital heart disease.

Mizuno A, Niwa K, Ochiai R, Shiraishi I, Sumita Y, Daida H, Fukuda T, Miyamoto Y, Nishimura K, Ogawa H, Yasuda S.

J Cardiol. 2019 Aug 14. pii: S0914-5087(19)30217-5. doi: 10.1016/j.jjcc.2019.06.010. [Epub ahead of print]

PMID: 31421934

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Select item 31421069

 

  1. Right-sided aortic arch with mirror image branching and situs solitus: a case of a 79 years old woman.

Morosetti D, Di Stefano C, Mondillo M, Pensabene MC, De Corato L, Bizzaglia M, Di Martino A, Floris R.

Radiol Case Rep. 2019 Aug 13;14(10):1246-1251. doi: 10.1016/j.radcr.2019.07.014. eCollection 2019 Oct.

PMID: 31462948 Free PMC Article

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Select item 31420306

 

  1. Adult congenital heart disease with pulmonary arterial hypertension: mechanisms and management.

Papamichalis M, Xanthopoulos A, Papamichalis P, Skoularigis J, Triposkiadis F.

Heart Fail Rev. 2019 Aug 12. doi: 10.1007/s10741-019-09847-5. [Epub ahead of print] Review.

PMID: 31407139

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Select item 31415819

 

  1. Reducing radiation dose from myocardial perfusion imaging in subjects with complex congenital heart disease.

Partington SL, Valente AM, Bruyere J Jr, Rosica D, Shafer KM, Landzberg MJ, Taqueti VR, Blankstein R, Skali H, Kwatra N, DiCarli MF, Grant FD, Dorbala S.

J Nucl Cardiol. 2019 Aug 12. doi: 10.1007/s12350-019-01811-y. [Epub ahead of print]

PMID: 31407235

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Select item 31408642

 

  1. Palliative Care Opportunities Among Adults With Congenital Heart Disease-A Systematic Review.

Ludmir J, Steiner JM, Wong HN, Kloosterboer A, Leong J, Aslakson RA.

J Pain Symptom Manage. 2019 Aug 9. pii: S0885-3924(19)30439-7. doi: 10.1016/j.jpainsymman.2019.07.025. [Epub ahead of print]

PMID: 31404639

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Select item 31399615

 

  1. Maternal Exposure to Housing Renovation During Pregnancy and Risk of Offspring with Congenital Malformation: The Japan Environment and Children’s Study.

Motoki N, Inaba Y, Shibazaki T, Misawa Y, Ohira S, Kanai M, Kurita H, Nakazawa Y, Tsukahara T, Nomiyama T; Japan Environment & Children’s Study (JECS) Group.

Sci Rep. 2019 Aug 9;9(1):11564. doi: 10.1038/s41598-019-47925-8.

PMID: 31399615 Free PMC Article

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Select item 20301303

 

  1. Noonan Syndrome.

Allanson JE, Roberts AE.

In: Adam MP, Ardinger HH, Pagon RA, Wallace SE, Bean LJH, Stephens K, Amemiya A, editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2019.

2001 Nov 15 [updated 2019 Aug 8].

PMID: 20301303 Free Books & Documents

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Select item 31393088

 

  1. Relation of Magnetic Resonance Elastography to Fontan Failure and Portal Hypertension.

Alsaied T, Possner M, Lubert AM, Trout AT, Szugye C, Palermo JJ, Lorts A, Goldstein BH, Veldtman GR, Anwar N, Dillman JR.

Am J Cardiol. 2019 Aug 7. pii: S0002-9149(19)30883-5. doi: 10.1016/j.amjcard.2019.07.052. [Epub ahead of print]

PMID: 31474329

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Select item 31400339

 

  1. Heart disease in pregnancy-clinical pattern and prevalence: initial data from the first cardio-maternal unit in Iraq.

Farhan HA, Yaseen IF.

BMC Res Notes. 2019 Aug 7;12(1):491. doi: 10.1186/s13104-019-4523-6.

PMID: 31391105 Free PMC Article

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Select item 31393254

 

  1. Exercise Capacity in Asymptomatic Adult Patients Treated for Coarctation of the Aorta.

Dijkema EJ, Sieswerda GT, Breur JMPJ, Haas F, Slieker MG, Takken T.

Pediatr Cardiol. 2019 Aug 7. doi: 10.1007/s00246-019-02173-5. [Epub ahead of print]

PMID: 31392380

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Select item 31398358

 

  1. Ischemic Stroke in Adults With Congenital Heart Disease: A Population-Based Cohort Study.

Pedersen MGB, Olsen MS, Schmidt M, Johnsen SP, Learn C, Laursen HB, Madsen NL.

J Am Heart Assoc. 2019 Aug 6;8(15):e011870. doi: 10.1161/JAHA.118.011870. Epub 2019 Jul 18.

PMID: 31315496 Free Article

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Select item 31257961

 

  1. Transition program for adolescents with congenital heart disease in transition to adulthood: protocol for a mixed-method process evaluation study (the STEPSTONES project).

Saarijärvi M, Wallin L, Moons P, Gyllensten H, Bratt EL.

BMJ Open. 2019 Aug 2;9(8):e028229. doi: 10.1136/bmjopen-2018-028229.

PMID: 31377699 Free PMC Article

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Select item 31373176

 

  1. A Systematic Review of 4D-Flow MRI Derived Mitral Regurgitation Quantification Methods.

Fidock B, Barker N, Balasubramanian N, Archer G, Fent G, Al-Mohammad A, Richardson J, O’Toole L, Briffa N, Rothman A, van der Geest R, Hose R, Wild JM, Swift AJ, Garg P.

Front Cardiovasc Med. 2019 Aug 2;6:103. doi: 10.3389/fcvm.2019.00103. eCollection 2019.

PMID: 31428619 Free PMC Article

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Select item 31400887

 

  1. The art of caring for adults with congenital heart disease in the face of imperfect data.

Menachem JN, Opotowsky AR.

Int J Cardiol. 2019 Aug 2. pii: S0167-5273(19)33166-3. doi: 10.1016/j.ijcard.2019.07.100. [Epub ahead of print] No abstract available.

PMID: 31400887

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Select item 31382048

 

  1. Ten-year Experience of Q Fever Endocarditis in a Tertiary Cardiac Center in Saudi Arabia.

Elzein FE, Alsherbeeni N, Alnajashi K, Alsufyani E, Akhta MY, Albalaw R, Albarra AM, Kaabi N, Mehd S, Alzahran A, Raoult D.

Int J Infect Dis. 2019 Aug 2. pii: S1201-9712(19)30321-2. doi: 10.1016/j.ijid.2019.07.035. [Epub ahead of print]

PMID: 31382048 Free Article

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Select item 31374584

 

  1. Impact of Disease Complexity on Cardiovascular Events after the Transition to an Adult Congenital Heart Disease Specialized Medical Unit.

Takahashi S, Akagi T, Toh N, Takaya Y, Nakagawa K, Nishii N, Ito H.

Acta Med Okayama. 2019 Aug;73(4):307-313. doi: 10.18926/AMO/56932.

PMID: 31439953 Free Article

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Select item 31203159

 

  1. Creatinine versus cystatin C to estimate glomerular filtration rate in adults with congenital heart disease: Results of the Boston Adult Congenital Heart Disease Biobank.

Opotowsky AR, Carazo M, Singh MN, Dimopoulos K, Cardona-Estrada DA, Elantably A, Waikar SS, Mc Causland FR, Veldtman G, Grewal J, Gray C, Loukas BN, Rajpal S.

Am Heart J. 2019 Aug;214:142-155. doi: 10.1016/j.ahj.2019.04.018. Epub 2019 May 22.

PMID: 31203159

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Select item 31204032

 

  1. Exploring associations of maternal sleep during periconceptional period with congenital heart disease in offspring.

Zhao A, Zhao K, Xia Y, Yin Y, Zhu J, Hong H, Li S.

Birth Defects Res. 2019 Aug 1;111(13):920-931. doi: 10.1002/bdr2.1536. Epub 2019 Jun 17.

PMID: 31206252

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Select item 30868706

 

  1. Outcome of pregnancies in women with pulmonary hypertension: a single-centre experience from South India.

Keepanasseril A, Pillai AA, Yavanasuriya J, Raj A, Satheesh S, Kundra P.

BJOG. 2019 Aug;126 Suppl 4:43-49. doi: 10.1111/1471-0528.15681. Epub 2019 Jul 18.

PMID: 30868706

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Select item 31383248

 

  1. Long-term outcomes in adults with repaired tetralogy of Fallot and pulmonary atresia.

Egbe AC, Crestanello J, Dearani JA, Osman K, Banala K, Angirekula M, Najam M, Ammash NM.

Cardiol Young. 2019 Aug;29(8):1078-1081. doi: 10.1017/S1047951119001598. Epub 2019 Jul 10.

PMID: 31288878

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Select item 31287033

 

  1. Echocardiographic predictors of elevated left ventricular end diastolic pressure in adolescent and adult patients with repaired tetralogy of Fallot.

Lubert AM, Cotts TB, Zampi JD, Yu S, Norris MD.

Cardiol Young. 2019 Aug;29(8):1020-1024. doi: 10.1017/S1047951119001331. Epub 2019 Jun 18.

PMID: 31208473

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Select item 31067002

 

  1. Assessing hepatic impairment in Fontan-associated liver disease using the HepQuant SHUNT test.

Lemmer A, VanWagner L, Gasanova Z, Helmke S, Everson GT, Ganger D.

Congenit Heart Dis. 2019 Aug 1. doi: 10.1111/chd.12831. [Epub ahead of print]

PMID: 31369200

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Select item 31368206

 

  1. Utility of machine learning algorithms in assessing patients with a systemic right ventricle.

Diller GP, Babu-Narayan S, Li W, Radojevic J, Kempny A, Uebing A, Dimopoulos K, Baumgartner H, Gatzoulis MA, Orwat S.

Eur Heart J Cardiovasc Imaging. 2019 Aug 1;20(8):925-931. doi: 10.1093/ehjci/jey211.

PMID: 30629127

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Select item 30534951

 

  1. Patient-reported outcomes of adults with congenital heart disease from eight European countries: scrutinising the association with healthcare system performance.

Van Bulck L, Luyckx K, Goossens E, Apers S, Kovacs AH, Thomet C, Budts W, Sluman MA, Eriksen K, Dellborg M, Berghammer M, Johansson B, Caruana M, Soufi A, Callus E, Moons P.

Eur J Cardiovasc Nurs. 2019 Aug;18(6):465-473. doi: 10.1177/1474515119834484. Epub 2019 Feb 26.

PMID: 30808198

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Select item 31119575

 

  1. Cor triatriatum sinistrum diagnosed in the adulthood: a systematic review.

Rudienė V, Hjortshøj CMS, Glaveckaitė S, Zakarkaitė D, Petrulionienė Ž, Gumbienė L, Aidietis A, Søndergaard L.

Heart. 2019 Aug;105(15):1197-1202. doi: 10.1136/heartjnl-2019-314714. Epub 2019 Jun 5. Review.

PMID: 31171629

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Select item 30923175

 

  1. Long-term mortality and cardiovascular burden for adult survivors of coarctation of the aorta.

Lee MGY, Babu-Narayan SV, Kempny A, Uebing A, Montanaro C, Shore DF, d’Udekem Y, Gatzoulis MA.

Heart. 2019 Aug;105(15):1190-1196. doi: 10.1136/heartjnl-2018-314257. Epub 2019 Mar 28.

PMID: 30923175

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Select item 30826770

 

  1. Impact of a centre and home-based cardiac rehabilitation program on the quality of life of teenagers and young adults with congenital heart disease: the QUALI- REHAB study rationale, design and methods.

Frigiola A.

Int J Cardiol. 2019 Aug 1;288:70-71. doi: 10.1016/j.ijcard.2019.03.006. Epub 2019 Mar 9. No abstract available.

PMID: 30879939

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Select item 30808604

 

  1. Ready for Transfer to Adult Care? A Triadic Evaluation of Transition Readiness in Adolescents With Congenital Heart Disease and Their Parents.

Burström Å, Acuña Mora M, Öjmyr-Joelsson M, Sparud-Lundin C, Rydberg A, Hanseus K, Frenckner B, Nisell M, Moons P, Bratt EL.

J Fam Nurs. 2019 Aug;25(3):447-468. doi: 10.1177/1074840719864255. Epub 2019 Jul 25.

PMID: 31342815

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Select item 30907979

 

 

  1. Long-term health-related burden of adult congenital heart diseases in Hong Kong.

Lee VWY, Yan BP, Fong TMC, Fung AKP, Cheng FWT.

J Med Econ. 2019 Aug;22(8):814-817. doi: 10.1080/13696998.2019.1613239. Epub 2019 May 23.

PMID: 31038380

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Select item 31431764

 

  1. Association between maternal exposure to pollutant particulate matter 2.5 and congenital heart defects: a systematic review.

Hall KC, Robinson JC.

JBI Database System Rev Implement Rep. 2019 Aug;17(8):1695-1716. doi: 10.11124/JBISRIR-2017-003881.

PMID: 31021973

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Select item 31347322

 

  1. Metabolic Syndrome in Adult Congenital Heart Disease.

Niwa K.

Korean Circ J. 2019 Aug;49(8):691-708. doi: 10.4070/kcj.2019.0187. Epub 2019 Jul 5. Review.

PMID: 31347322 Free PMC Article

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Select item 31347320

 

  1. Impact of Pregnancy on Aortic Root in Women with Repaired Conotruncal Anomalies.

Horiuchi C, Kamiya CA, Ohuchi H, Nakanishi A, Tsuritani M, Iwanaga N, Kurosaki K, Niwa K, Ikeda T, Yoshimatsu J.

Pediatr Cardiol. 2019 Aug;40(6):1134-1143. doi: 10.1007/s00246-019-02112-4. Epub 2019 May 13.

PMID: 31087143

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Select item 31169761

 

  1. Preconception Assessment of Women of Childbearing Age With Congenital Heart Disease.

Rodríguez Martín M, Martín García AC, García-Cuenllas L, Castro-Garay JC, Plata B, Sánchez PL.

Rev Esp Cardiol (Engl Ed). 2019 Aug;72(8):683-684. doi: 10.1016/j.rec.2018.07.015. Epub 2018 Sep 24. English, Spanish. No abstract available.

PMID: 30262425

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Select item 30737539

 

  1. Clinical impact of cardiac computed tomography derived three-dimensional strain for adult congenital heart disease: a pilot study.

Shiina Y, Inai K, Takahashi T, Shimomiya Y, Nagao M.

Int J Cardiovasc Imaging. 2019 Aug 30. doi: 10.1007/s10554-019-01691-w. [Epub ahead of print]

PMID: 31471763

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Select item 31469658

 

  1. Acute Hemodynamic Effects of Negative Extrathoracic Pressure in Fontan Physiology.

Peng DM, Zampi JD, Smith SM, Yu S, Rottach N, Lowery R, Lim HM, Riegger LQ, Schumacher KR, Rocchini A.

Pediatr Cardiol. 2019 Aug 29. doi: 10.1007/s00246-019-02197-x. [Epub ahead of print]

PMID: 31468061

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  1. Natural History of Cardiomyopathy in Adult Dogs With Golden Retriever Muscular Dystrophy.

Guo LJ, Soslow JH, Bettis AK, Nghiem PP, Cummings KJ, Lenox MW, Miller MW, Kornegay JN, Spurney CF.

J Am Heart Assoc. 2019 Aug 20;8(16):e012443. doi: 10.1161/JAHA.119.012443. Epub 2019 Aug 14.

PMID: 31411085 Free Article

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  1. The placenta: A site of end-organ damage after Fontan operation. A case series.

Phillips AL, Cetta F, Kerr SE, Cheek EH, Rose CH, Bonnichsen CR, Phillips SD.

Int J Cardiol. 2019 Aug 15;289:52-55. doi: 10.1016/j.ijcard.2019.02.002. Epub 2019 Feb 5.

PMID: 30765280

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  1. Impact of facilities accredited by both adult and pediatric cardiology societies on the outcome of patients with adult congenital heart disease.

Mizuno A, Niwa K, Ochiai R, Shiraishi I, Sumita Y, Daida H, Fukuda T, Miyamoto Y, Nishimura K, Ogawa H, Yasuda S.

J Cardiol. 2019 Aug 14. pii: S0914-5087(19)30217-5. doi: 10.1016/j.jjcc.2019.06.010. [Epub ahead of print]

PMID: 31421934

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  1. CMR feature tracking left ventricular strain-rate predicts ventricular tachyarrhythmia, but not deterioration of ventricular function in patients with repaired tetralogy of Fallot.

Hagdorn QAJ, Vos JDL, Beurskens NEG, Gorter TM, Meyer SL, van Melle JP, Berger RMF, Willems TP.

Int J Cardiol. 2019 Aug 1. pii: S0167-5273(19)30911-8. doi: 10.1016/j.ijcard.2019.07.097. [Epub ahead of print]

PMID: 31402156 Free Article

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  1. Impact of Pregnancy on Aortic Root in Women with Repaired Conotruncal Anomalies.

Horiuchi C, Kamiya CA, Ohuchi H, Nakanishi A, Tsuritani M, Iwanaga N, Kurosaki K, Niwa K, Ikeda T, Yoshimatsu J.

Pediatr Cardiol. 2019 Aug;40(6):1134-1143. doi: 10.1007/s00246-019-02112-4. Epub 2019 May 13.

PMID: 31087143

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ACHD Electrophysiology Featured Articles

Congenital and Pediatric Cardiac EP Reviews of August 2019 Manuscripts

Improvement in ventricular function with rhythm control of atrial arrhythmias may delay the need for atrioventricular valve surgery in adults with congenital heart disease.
Zielonka B, Kim YY, Supple GE, Partington SL, Ruckdeschel ES, Marchlinski FE, Frankel DS.
Congenit Heart Dis. 2019 Aug 5. doi: 10.1111/chd.12833. [Epub ahead of print]
PMID: 31385437
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Take Home Points:
• Atrial arrhythmias in ACHD patients is known to increase with age, disease severity and hemodynamic burden (i.e. atrioventricular valve regurgitation – AVVR).
• Improvements in hemodynamic burden can reduce arrhythmia burden but not always due to adverse atrial remodeling.
• Rhythm control of atrial arrhythmias in ACHD patients with moderate to severe AVVR resulted in improved ventricular function – increase in LV EF of ~5% or reduction of 1 grade of qualitative RV function severity.
• Overall, rhythm control was superior to rate control for avoidance of surgery at 4 years (89% vs 33%).
• Use of catheter ablation and/or AADs for rhythm control resulted in a reduction in arrhythmia burden of 67% (no recurrence or conversion from persistent to paroxysmal) in this cohort.
• Overall recurrence of arrhythmias still remained high at 75%.
• Atrial arrhythmia management with the goal of rhythm control may provide an alternative treatment approach to delay the need for surgical intervention in a subset of patients.

Comment from Dr. Akash Patel (San Francisco), section editor of Congenital Electrophysiology Journal Watch. Atrial arrhythmias are a common complication in patients with adult congenital heart disease and increase with age, lesion severity, and hemodynamic burden such as atrioventricular valvar regurgitation (AVVR). Correction of underlying hemodynamic burden (i.e. AV valve surgery) has classically been thought to improve arrhythmia burden but this is not always true due to adverse atrial remodeling. Conversely, it remains unclear if there is benefit of arrhythmia control for improvement on atrioventricular valvar regurgitation in ACHD patients which could potentially delay the need for AV valve surgery. This study aimed to assess the impact of rhythm control of atrial arrhythmias in AVVR in adults with congenital heart disease.

This was a retrospective single center study of all patients with adult congenital heart disease who were seen by both, electrophysiology and adult congenital heart disease specialists, with at least moderate to severe AVVR and atrial arrhythmias from January 2004 to July 2017. The rhythm control group was defined as those who underwent catheter ablation or on antiarrhythmic medications (Class I or Class III). The rate control group was defined as all others. Baseline clinical, arrhythmia, echocardiographic and follow-up data were included.

The study group included 24 patients who had at least moderate-severe AVVR out of 229 ACHD patients with atrial arrhythmias. There were 9 patients in the rhythm control group of whom 8 (89%) were free from valve surgery at last follow-up. There were 15 patients in the rate control group of whom 5 (33%) were free from valve surgery at last follow-up. See Figure Below.

The mean age of the cohort was 47 years with no difference in gender, age, congenital heart disease, lesion severity, prior operations, CEIDs, and comorbidities between the rhythm and rate control groups. See Table Below.

The most common cardiac diagnoses were atrial septal/ventricular septal defects (25%), tetralogy of Fallot (25%), D-TGA (17%), AV Canal (13%), Ebstein (8%), and other (13%).
The atrial arrhythmias were IART (58%), atrial fibrillation (58%),] focal atrial tachycardia (29%), and AVNRT (4%). There were significantly more patients with IART in the rhythm control group which is likely more amenable to antiarrhythmic therapies. The arrhythmias were paroxysmal (<7 days) in 38% and persistent (≥ 7 days or cardioversion) in 63%. There was no difference in average heart rate between the groups. See Table Below.

There was some form of recurrence (paroxysmal or persistence) seen in 75% overall with no difference between the rhythm and rate control groups. There was a significant reduction in arrhythmia burden in the rhythm control group, 6 (67%) vs. 3(20%), p =0.04. Reduction was defined as no recurrence or a decrease in pattern from persistence to paroxysmal.

The antiarrhythmics used in the rhythm control group included dofetilide (78%), amiodarone (44%), sotalol (33%), and propafenone (11%) with 1.8±1.1 antiarrhythmic drugs used.

Echocardiographic findings showed that baseline atrial sizes, ventricular sizes, ventricular function, and AVVR were the same in both groups. There was moderate to severe left atrial dilation in 46%, right atrial dilation 63%. There was tricuspid valve regurgitation in 79% and mitral valve regurgitation in 21% with moderate-severe regurgitation in 54% and severe in 46%. See Table Below.

Follow echocardiographic data at a mean of ~2 years showed overall atrial sizes, ventricular sizes, ventricular function, and AVVR were the same in both groups. There was moderate to severe left atrial dilation in 42%, right atrial dilation 63%. There was moderate-severe regurgitation in 38% and severe in 38%. See Table Below.

In the rhythm control group, the mean LV ejection fraction improved from 54.4 ± 12.4% to 60.0 ± 11.5%, p=0.02 and the mean RV systolic function improved ~ 1 grade classification, p=0.02. There was no significant change in LV ejection fraction or RV systolic function in the rate control group. (See Below). There was also no significant change in AVVR severity.

The overall AV valve operation and transplant free survival at 4 years was 88% in the rhythm group and 31% in the rate control group (log-rank p=0.04). See Figure Below.

This study demonstrates an association between rhythm control and a small but significant increase in ventricular function without change in AVVR severity. This was associated with the need for less AVV surgery in the rhythm control group (11% vs. 60%). Clearly, atrial arrhythmias are associated with increased comorbidities including heart failure. This study demonstrated that even a reduction in arrhythmia burden despite a high recurrence rate of 75% still resulted in change ventricular function and reinforces the importance of sinus rhythm and AV synchrony in the setting of moderate to severe AVVR.
This study raises an interesting option for patients with significant AVVR and adds to the data supporting the importance of rhythm control over rate control in ACHD patients.
Clearly more data is needed in a larger sample size to determine the impact on ventricular function as the change in this study was only noted ~5% increase in LV EF or qualitative RV function. In addition, it is unclear based on the sample size, if the impact would be the same for failing systemic RV vs LV in biventricular circulation, single ventricle (RV vs LV), or failing subpulmonary ventricle with concordant AVVR. In addition, it remains unclear the impact how the anatomic valve morphology plays in the tolerance of AVVR as this population skewed heavily toward tricuspid regurgitation (79% of total cohort). Finally, the type of arrhythmia such as atrial fibrillation which is less amenable to rhythm control vs flutter and impact of persistence vs paroxysmal arrhythmias requires further evaluation.

Management of atrial arrhythmias in ACHD patients is critically important to reduce associated comorbidities such as stroke, heart failure and death. Further improvements in ablation therapy may provide more long-term success and potentially could show even more benefit than was noted in this study in whom patients had a high recurrence rate.
CHD EP August 2019

 

  1. 2018 ACC/AHA/HRS Guideline on the Evaluation and Management of Patients With Bradycardia and Cardiac Conduction Delay: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines and the Heart Rhythm Society.

Kusumoto FM, Schoenfeld MH, Barrett C, Edgerton JR, Ellenbogen KA, Gold MR, Goldschlager NF, Hamilton RM, Joglar JA, Kim RJ, Lee R, Marine JE, McLeod CJ, Oken KR, Patton KK, Pellegrini CN, Selzman KA, Thompson A, Varosy PD.

Circulation. 2019 Aug 20;140(8):e382-e482. doi: 10.1161/CIR.0000000000000628. Epub 2018 Nov 6. No abstract available. Erratum in: Circulation. 2019 Aug 20;140(8):e506-e508.

PMID: 30586772

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  1. 2018 ACC/AHA/HRS Guideline on the Evaluation and Management of Patients With Bradycardia and Cardiac Conduction Delay: Executive Summary: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines, and the Heart Rhythm Society.

Kusumoto FM, Schoenfeld MH, Barrett C, Edgerton JR, Ellenbogen KA, Gold MR, Goldschlager NF, Hamilton RM, Joglar JA, Kim RJ, Lee R, Marine JE, McLeod CJ, Oken KR, Patton KK, Pellegrini CN, Selzman KA, Thompson A, Varosy PD.

Circulation. 2019 Aug 20;140(8):e333-e381. doi: 10.1161/CIR.0000000000000627. Epub 2018 Nov 6. No abstract available. Erratum in: Circulation. 2019 Aug 20;140(8):e504-e505.

PMID: 30586771

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Select item 31430042

 

  1. 2018 ACC/AHA/HRS Guideline on the Evaluation and Management of Patients With Bradycardia and Cardiac Conduction Delay: Executive Summary: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines, and the Heart Rhythm Society.

Kusumoto FM, Schoenfeld MH, Barrett C, Edgerton JR, Ellenbogen KA, Gold MR, Goldschlager NF, Hamilton RM, Joglar JA, Kim RJ, Lee R, Marine JE, McLeod CJ, Oken KR, Patton KK, Pellegrini CN, Selzman KA, Thompson A, Varosy PD.

J Am Coll Cardiol. 2019 Aug 20;74(7):932-987. doi: 10.1016/j.jacc.2018.10.043. Epub 2018 Nov 6. No abstract available. Erratum in: J Am Coll Cardiol. 2019 Aug 20;74(7):1014-1016.

PMID: 30412710

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Select item 30412709

 

  1. 2018 ACC/AHA/HRS Guideline on the Evaluation and Management of Patients With Bradycardia and Cardiac Conduction Delay: A Report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines and the Heart Rhythm Society.

Kusumoto FM, Schoenfeld MH, Barrett C, Edgerton JR, Ellenbogen KA, Gold MR, Goldschlager NF, Hamilton RM, Joglar JA, Kim RJ, Lee R, Marine JE, McLeod CJ, Oken KR, Patton KK, Pellegrini CN, Selzman KA, Thompson A, Varosy PD.

J Am Coll Cardiol. 2019 Aug 20;74(7):e51-e156. doi: 10.1016/j.jacc.2018.10.044. Epub 2018 Nov 6. No abstract available. Erratum in: J Am Coll Cardiol. 2019 Aug 20;74(7):1016-1018.

PMID: 30412709

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  1. Single- and dual-site ventricular pacing entirely through the coronary sinus for patients with prior tricuspid valve surgery.

Lee CC, Do K, Patel S, Carlson SK, Konecny T, Chang PM, Doshi RN.

J Interv Card Electrophysiol. 2019 Aug 20. doi: 10.1007/s10840-019-00599-8. [Epub ahead of print]

PMID: 31432385

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  1. Aetiologies and temporal trends of atrioventricular block in young patients: a 20-year nationwide study.

Rudbeck-Resdal J, Christiansen MK, Johansen JB, Nielsen JC, Bundgaard H, Jensen HK.

Europace. 2019 Aug 19. pii: euz206. doi: 10.1093/europace/euz206. [Epub ahead of print]

PMID: 31424500

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  1. Sudden cardiac death and valvular pathology.

Henriques de Gouveia RHAM, Corte Real Gonçalves FMA.

Forensic Sci Res. 2019 Aug 19;4(3):280-286. doi: 10.1080/20961790.2019.1595351. eCollection 2019.

PMID: 31489394

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  1. Plasma natriuretic peptide levels reflect the status of the heart failure in fetuses with arrhythmia.

Miyoshi T, Hosoda H, Kurosaki KI, Shiraishi I, Nakai M, Nishimura K, Miyazato M, Kangawa K, Yoshimatsu J, Minamino N.

J Matern Fetal Neonatal Med. 2019 Aug 15:1-7. doi: 10.1080/14767058.2019.1651271. [Epub ahead of print]

PMID: 31414622

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  1. Catheter ablation in children and patients with congenital heart disease: Review of 1021 procedures at a high-volume single center in Japan.

Kato Y, Suzuki T, Yoshida Y, Ozaki N, Aoki H, Kishimoto S, Yoshida S, Watanabe S, Nakamura Y.

Heart Rhythm. 2019 Aug 12. pii: S1547-5271(19)30734-9. doi: 10.1016/j.hrthm.2019.08.013. [Epub ahead of print]

PMID: 31415819

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  1. Sudden Cardiac Deaths in Adults with Congenital Heart Disease with Structural Abnormalities: A Retrospective Review of Cases in the Cook County Medical Examiner’s Office.

Gitto L, Serinelli S, Arunkumar P, White SM.

J Forensic Sci. 2019 Aug 12. doi: 10.1111/1556-4029.14165. [Epub ahead of print]

PMID: 31404479

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  1. Improvement in ventricular function with rhythm control of atrial arrhythmias may delay the need for atrioventricular valve surgery in adults with congenital heart disease.

Zielonka B, Kim YY, Supple GE, Partington SL, Ruckdeschel ES, Marchlinski FE, Frankel DS.

Congenit Heart Dis. 2019 Aug 5. doi: 10.1111/chd.12833. [Epub ahead of print]

PMID: 31385437

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  1. Comparison of Electrophysiologic Profiles in Pediatric Patients with Incidentally Identified Pre-Excitation Compared with Wolff-Parkinson-White Syndrome.

LaRocca TJ, Beyersdorf GB, Li W, Foltz R, Patel AR, Tanel RE.

Am J Cardiol. 2019 Aug 1;124(3):389-395. doi: 10.1016/j.amjcard.2019.04.053. Epub 2019 May 10.

PMID: 31204032

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  1. Causes of fetal third-degree atrioventricular block and use of hydroxychloroquine in pregnant women with Ro/La antibodies.

Mollerach FB, Scolnik M, Catoggio LJ, Rosa J, Soriano ER.

Clin Rheumatol. 2019 Aug;38(8):2211-2217. doi: 10.1007/s10067-019-04556-8. Epub 2019 Apr 17.

PMID: 30997589

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  1. Evaluating the response to cardiac resynchronization therapy performed with a new ventricular morphology-based strategy for congenital heart disease.

Miyazaki A, Negishi J, Hayama Y, Baba S, Matsumura Y, Shima Y, Tsuda E, Sakaguchi H, Hoashi T, Kagisaki K, Noda T, Doi H, Ichikawa H, Ohuchi H.

Heart Vessels. 2019 Aug;34(8):1340-1350. doi: 10.1007/s00380-019-01369-2. Epub 2019 Mar 12.

PMID: 30863899

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  1. Prediction and prevention of sudden cardiac death in transposition of the great arteries: A step closer.

Kharbanda RK, de Groot NMS.

Int J Cardiol. 2019 Aug 1;288:68-69. doi: 10.1016/j.ijcard.2019.04.040. Epub 2019 Apr 17. No abstract available.

PMID: 31029496

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  1. Initial experience with transcatheter pacemaker implantation for adults with congenital heart disease.

Russell MR, Galloti R, Moore JP.

J Cardiovasc Electrophysiol. 2019 Aug;30(8):1362-1366. doi: 10.1111/jce.13961. Epub 2019 Jun 17.

PMID: 31045294

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  1. Minimally invasive technique of placing a dual chamber permanent pacemaker in children.

Amanullah M, Razzaq S, Siddiqui AH, Khan FW.

J Pak Med Assoc. 2019 Aug;69(8):1119-1123.

PMID: 31431764 Free Article

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  1. Fetal Sinus Bradycardia Is Associated with Congenital Hypothyroidism: An Infant with Ectopic Thyroid Tissue.

Nakanomori A, Nagano N, Seimiya A, Okahashi A, Morioka I.

Tohoku J Exp Med. 2019 Aug;248(4):307-311. doi: 10.1620/tjem.248.307.

PMID: 31462599 Free Article

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  1. Impact of Ethnicity on the Prevalence of Early Repolarization Pattern in Children: Comparison Between Caucasian and African Populations.

Creta A, Arigliani M, di Gioia G, Lapenna R, Quintarelli F, Fittipaldi M, Antinolfi V, Bettini R, Costanzo D, Cruciani A, Di Berardino S, Giorgino R, Satriano U, Mangiameli G, Sut D, Caricato M, Cogo P, Proclemer A, Mottini G, Lambiase PD, Providência R.

Pediatr Cardiol. 2019 Aug 24. doi: 10.1007/s00246-019-02185-1. [Epub ahead of print]

PMID: 31446474

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  1. Long QT Syndrome: Genetics and Future Perspective.

Wallace E, Howard L, Liu M, O’Brien T, Ward D, Shen S, Prendiville T.

Pediatr Cardiol. 2019 Aug 22. doi: 10.1007/s00246-019-02151-x. [Epub ahead of print] Review.

PMID: 31440766

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  1. Antenatal Therapy for Fetal Supraventricular Tachyarrhythmias: Multicenter Trial.

Miyoshi T, Maeno Y, Hamasaki T, Inamura N, Yasukochi S, Kawataki M, Horigome H, Yoda H, Taketazu M, Nii M, Hagiwara A, Kato H, Shimizu W, Shiraishi I, Sakaguchi H, Ueda K, Katsuragi S, Yamamoto H, Sago H, Ikeda T; Japan Fetal Arrhythmia Group.

J Am Coll Cardiol. 2019 Aug 20;74(7):874-885. doi: 10.1016/j.jacc.2019.06.024.

PMID: 31416531

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  1. Automated external defibrillator use in a previously healthy 31-day-old infant with out-of-hospital cardiac arrest due to ventricular fibrillation.

Hoyt WJ Jr, Fish FA, Kannankeril PJ.

J Cardiovasc Electrophysiol. 2019 Aug 20. doi: 10.1111/jce.14125. [Epub ahead of print]

PMID: 31432598

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  1. Development of a Novel Risk Prediction Model for Sudden Cardiac Death in Childhood Hypertrophic Cardiomyopathy (HCM Risk-Kids).

Norrish G, Ding T, Field E, Ziólkowska L, Olivotto I, Limongelli G, Anastasakis A, Weintraub R, Biagini E, Ragni L, Prendiville T, Duignan S, McLeod K, Ilina M, Fernández A, Bökenkamp R, Baban A, Kubuš P, Daubeney PEF, Sarquella-Brugada G, Cesar S, Marrone C, Bhole V, Medrano C, Uzun O, Brown E, Gran F, Castro FJ, Stuart G, Vignati G, Barriales-Villa R, Guereta LG, Adwani S, Linter K, Bharucha T, Garcia-Pavia P, Rasmussen TB, Calcagnino MM, Jones CB, De Wilde H, Toru-Kubo J, Felice T, Mogensen J, Mathur S, Reinhardt Z, O’Mahony C, Elliott PM, Omar RZ, Kaski JP.

JAMA Cardiol. 2019 Aug 14. doi: 10.1001/jamacardio.2019.2861. [Epub ahead of print]

PMID: 31411652

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Select item 31414158

 

  1. Type 8 long QT syndrome: pathogenic variants in CACNA1C-encoded Cav1.2 cluster in STAC protein binding site.

Mellor GJ, Panwar P, Lee AK, Steinberg C, Hathaway JA, Bartels K, Christian S, Balaji S, Roberts JD, Simpson CS, Boczek NJ, Tester DJ, Radbill AE, Mok NS, Hamilton RM, Kaufman ES, Eugenio PL, Weiss R, January C, McDaniel GM, Leather RA, Erickson C, Falik S, Behr ER, Wilde AAM, Sanatani S, Ackerman MJ, Van Petegem F, Krahn AD, Laksman Z.

Europace. 2019 Aug 13. pii: euz215. doi: 10.1093/europace/euz215. [Epub ahead of print]

PMID: 31408100

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  1. Findings of Uncertain Significance and a Family History of Sudden Death: Worth the FUSs?

Ackerman MJ, Giudicessi JR.

J Am Coll Cardiol. 2019 Aug 13;74(6):771-773. doi: 10.1016/j.jacc.2019.06.042. No abstract available.

PMID: 31395127

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Select item 31395126

 

  1. Cardiac Evaluation of Children With a Family History of Sudden Death.

Webster G, Olson R, Schoppen ZJ, Giancola N, Balmert LC, Cherny S, George AL Jr.

J Am Coll Cardiol. 2019 Aug 13;74(6):759-770. doi: 10.1016/j.jacc.2019.05.062.

PMID: 31395126

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Select item 31419439

 

  1. Junctional beats and pure His bundle pacing: Surface ECG appraisal in an atypical preexcitation variant.

Ali H, Foresti S, Mariucci E, Cappato R.

J Electrocardiol. 2019 Aug 8;57:35-38. doi: 10.1016/j.jelectrocard.2019.08.009. [Epub ahead of print] No abstract available.

PMID: 31473478

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Select item 31402138

 

  1. Pediatric Post-Cardiac Arrest Care: A Scientific Statement From the American Heart Association.

Topjian AA, de Caen A, Wainwright MS, Abella BS, Abend NS, Atkins DL, Bembea MM, Fink EL, Guerguerian AM, Haskell SE, Kilgannon JH, Lasa JJ, Hazinski MF.

Circulation. 2019 Aug 6;140(6):e194-e233. doi: 10.1161/CIR.0000000000000697. Epub 2019 Jun 27.

PMID: 31242751

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Select item 31387383

 

  1. Heart rate response during exercise predicts exercise tolerance in adults with transposition of the great arteries and atrial switch operation.

Iriart X, Le Quellenec S, Pillois X, Jaussaud J, Jalal Z, Roubertie F, Douard H, Cochet H, Thambo JB.

Int J Cardiol. 2019 Aug 6. pii: S0167-5273(18)36647-6. doi: 10.1016/j.ijcard.2019.07.054. [Epub ahead of print]

PMID: 31405586

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Select item 31379252

 

  1. Clinical features and arrhythmic complications of patients with pediatric-onset arrhythmogenic right ventricular dysplasia.

Sevinç Şengül F, Tunca Şahin G, Özgür S, Kafalı HC, Akıncı O, Güzeltaş A, Ergül Y.

Anatol J Cardiol. 2019 Aug;22(2):60-67. doi: 10.14744/AnatolJCardiol.2019.56985.

PMID: 31375646 Free Article

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Select item 31375645

 

  1. Successful treatment of electrical storm in a child with early repolarization syndrome with orciprenaline and radiofrequency ablation.

Ergül Y, Kafalı HC, Gülgün M.

Anatol J Cardiol. 2019 Aug;22(2):94-96. doi: 10.14744/AnatolJCardiol.2019.37085. No abstract available.

PMID: 31375645 Free Article

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Select item 30974093

 

  1. Evaluation After Sudden Death in the Young.

Gray B, Ackerman MJ, Semsarian C, Behr ER.

Circ Arrhythm Electrophysiol. 2019 Aug;12(8):e007453. doi: 10.1161/CIRCEP.119.007453. Epub 2019 Aug 19.

PMID: 31422686

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Select item 31401855

 

 

 

  1. Clinical and Electrophysiological Correlates of Incessant Ivabradine-Sensitive Atrial Tachycardia.

Banavalikar B, Shenthar J, Padmanabhan D, Valappil SP, Singha SI, Kottayan A, Ghadei M, Ali M.

Circ Arrhythm Electrophysiol. 2019 Aug;12(8):e007387. doi: 10.1161/CIRCEP.119.007387. Epub 2019 Jul 26.

PMID: 31345093

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Select item 31412722

 

  1. Characterization of the CACNA1C-R518C Missense Mutation in the Pathobiology of Long-QT Syndrome Using Human Induced Pluripotent Stem Cell Cardiomyocytes Shows Action Potential Prolongation and L-Type Calcium Channel Perturbation.

Estes SI, Ye D, Zhou W, Dotzler SM, Tester DJ, Bos JM, Kim CSJ, Ackerman MJ.

Circ Genom Precis Med. 2019 Aug;12(8):e002534. doi: 10.1161/CIRCGEN.119.002534. Epub 2019 Aug 20.

PMID: 31430211

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Select item 31309613

 

  1. Minimally invasive percutaneous epicardial placement of a prototype miniature pacemaker with a leadlet under direct visualization: A feasibility study in an infant porcine model.

Kumthekar RN, Opfermann JD, Mass P, Clark BC, Moak JP, Sherwin ED, Whitman T, Marshall M, Berul CI.

Heart Rhythm. 2019 Aug;16(8):1261-1267. doi: 10.1016/j.hrthm.2019.02.033. Epub 2019 Mar 1.

PMID: 30826423

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Select item 30763784

 

  1. Exercise testing oversights underlie missed and delayed diagnosis of catecholaminergic polymorphic ventricular tachycardia in young sudden cardiac arrest survivors.

Giudicessi JR, Ackerman MJ.

Heart Rhythm. 2019 Aug;16(8):1232-1239. doi: 10.1016/j.hrthm.2019.02.012. Epub 2019 Feb 11.

PMID: 30763784

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Select item 30863899

 

  1. Evaluating the response to cardiac resynchronization therapy performed with a new ventricular morphology-based strategy for congenital heart disease.

Miyazaki A, Negishi J, Hayama Y, Baba S, Matsumura Y, Shima Y, Tsuda E, Sakaguchi H, Hoashi T, Kagisaki K, Noda T, Doi H, Ichikawa H, Ohuchi H.

Heart Vessels. 2019 Aug;34(8):1340-1350. doi: 10.1007/s00380-019-01369-2. Epub 2019 Mar 12.

PMID: 30863899

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  1. Prediction of postnatal arrhythmia in fetuses with cardiac rhabdomyoma.

Ide T, Miyoshi T, Katsuragi S, Neki R, Kurosaki KI, Shiraishi I, Yoshimatsu J, Ikeda T.

J Matern Fetal Neonatal Med. 2019 Aug;32(15):2463-2468. doi: 10.1080/14767058.2018.1438402. Epub 2018 Feb 20.

PMID: 29415597

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Select item 31391750

 

  1. Ventricular Tachycardia in a Fetus: Benign Course of a Malignant Arrhythmia.

Saileela R, Sachdeva S, Saggu DK, Koneti NR.

J Obstet Gynaecol India. 2019 Aug;69(4):383-386. doi: 10.1007/s13224-018-1147-z. Epub 2018 Jun 29.

PMID: 31391750

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Select item 31176455

 

  1. A large deletion in RYR2 exon 3 is associated with nadolol and flecainide refractory catecholaminergic polymorphic ventricular tachycardia.

Kohli U, Aziz Z, Beaser AD, Nayak HM.

Pacing Clin Electrophysiol. 2019 Aug;42(8):1146-1154. doi: 10.1111/pace.13668. Epub 2019 Apr 17.

PMID: 30912151

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Select item 31372681

 

  1. Ivabradine in Post-operative Junctional Ectopic Tachycardia (JET): Breaking New Ground.

Krishna MR, Kunde MF, Kumar RK, Balaji S.

Pediatr Cardiol. 2019 Aug;40(6):1284-1288. doi: 10.1007/s00246-019-02149-5. Epub 2019 Jul 18.

PMID: 31317219

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ACHD Interventional Cardiology Featured Articles

CHD Interventions August 2019

 

A Low Residual Pressure Gradient Yields Excellent Long-Term Outcome After Percutaneous Pulmonary Valve Implantation.
Georgiev S, Ewert P, Tanase D, Hess J, Hager A, Cleuziou J, Meierhofer C, Eicken A.
JACC Cardiovasc Interv. 2019 Aug 26;12(16):1594-1603. doi: 10.1016/j.jcin.2019.03.037. Epub 2019 Jun 12.
PMID: 31202951
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Select item 31444883

Take Home Points:
• TPVI is first line therapy for treating residual RVOT disease. TPVi achieves not only short-term success but also durable results.
• Pre-stenting prior to Melody valve implantation is important to ensure long-term valve function.
• It is essential to be aggressive in relieving RVOT obstruction as leaving the lab with significant residual stenosis is a risk factor for early valve failure.

Commentary from Dr. Ryan Romans (Kansas City KS), section editor of Congenital Heart Disease Interventions Journal Watch: Persistent RVOT dysfunction is common following surgical treatment of many forms of congenital heart disease. Transcatheter pulmonary valve implantation (TPVI) was first performed in 2000 and has become the first line option for treating patients with RVOT obstruction and pulmonary insufficiency. Multiple studies have shown excellent short- and mid-term outcomes with the Melody valve and short-term outcomes with the Sapien valve. Longer term data are not yet available. Additionally, in the early experience with the Melody valve, the conduit was not routinely pre-stented. It is now standard practice to stent the RV to PA conduit or RVOT prior to Melody valve implantation as the stent the Melody valve is mounted on does not have adequate radial strength to protect the valve.
Georgiev et al report on their single center experience with TPVi. Data was collected over an 11-year period (2006-2017) on all patients who underwent TPVI, with follow up data obtained prospectively. There were 236 patients who underwent TPVi, with a median age of 18 years (range 4-78 years) and weight of 59 kg (range 19-118 kg). The majority of patients had tetralogy of Fallot (51%). The RV to PA conduits were mostly pulmonary homografts (69%), with 20% of patients having other types of valved conduits. 11% of patients had no conduit (such as in tetralogy of Fallot s/p transannular patch). The indication for TPVI was pulmonary stenosis in 42%, pulmonary insufficiency in 16%, and mixed disease (PS and PI) in 42%. Pre-stenting was performed in all but 8 patients. Melody valves were implanted in 220/236 patients (93%). Post-dilation with a high-pressure balloon was performed in 63% of patients. The mean residual RVOT gradient was 10 mmHg (range 0-39 mmHg). The large majority of patients had no residual PI, 42 had trivial PI, and 5 patients mild PI immediately post procedure.
Follow up data was obtained on 226 patients (96%), with a median of 3.9 years (range 2 months to 11 years). Overall survival was 96% at 5 years and 92% at 10 years. There was a total of 7 deaths during the study period. Two patients died due to procedural related complications (uncontained conduit rupture, left coronary artery compression) and the other 5 were thought to most likely be to arrhythmias. Surgery free survival was 92% at 5 years and 83% at 10 years. At the end of the study period, 17 patients had suffered valve failure (10 with stenosis after infective endocarditis, 7 with progressive stenosis). Of these, 11 patients had surgical valve replacement and 6 were treated with transcatheter valve in valve procedures. More than mild PI was seen in only 1 patient at 5 years and 2 patients at 10 years. Cox regression analysis was performed and showed that patients who were treated with a pre stent and left the cath lab with RVOT gradients <15 mmHg were more likely to survive with their original valve at 10 years (88% vs. 56%). Exercise testing was performed in 163 patients prior to TPVI, 150 patients 6 months after TPVi, and 68 patients 5 years after TPVi. This showed slightly improved exercise capacity immediately after TPVi. This was maintained at 5 year follow up.
TPVi is now first line therapy for treating residual RVOT disease. This study adds to the growing literature showing that the valves offer a durable result. Infective endocarditis remains a concern and is the primary reason for valve failure. The annualized risk of infective endocarditis was 1.9%. The authors highlight the importance of pre-stenting prior to TPVi with the Melody valve and ensuring minimal residual RVOT gradient to maximize valve longevity.

Use of 65 cm large caliber Dryseal sheaths to facilitate delivery of the Edwards SAPIEN valve to dysfunctional right ventricular outflow tracts.
Kenny D, Morgan GJ, Murphy M, AlAlwi K, Giugno L, Zablah J, Carminati M, Walsh K.
Catheter Cardiovasc Interv. 2019 Aug 13. doi: 10.1002/ccd.28409. [Epub ahead of print]
PMID: 31408262

Take Home Points:
• Implantation of the Sapien XT or S3 valve carries a significant (6-7.5%) risk of tricuspid valve injury.
• Use of the large diameter 65cm DrySeal sheath facilitates advancement of the Sapien valve to the right ventricular outflow tract and may decrease the incidence of tricuspid valve injury.

Commentary from Dr. Konstantin Averin (Edmonton), catheterization section editor of Pediatric Cardiology Journal Watch: The Sapien XT and S3 valves have been a welcome addition to the interventional armamentarium for the treatment of dysfunctional right ventricular outflow tracts (RVOT) allowing for treatment of a larger variety of anatomies. However, as the Sapien system was designed for trans-catheter aortic valve implant, the valve is uncovered to allow for a smaller delivery profile and has been associated with a significant risk (6-7.5%) of tricuspid valve injury during delivery to the RVOT. The authors sought to describe their experience using the large diameter 65cm Gore Dryseal Sheath to facilitate delivery of the Sapien XT and Sapien 3 valves to dysfunctional RVOTs.

Thirty patients at 3 large congenital heart centers underwent Sapien 3 (29) or XT (1) implants using the Gore Dryseal sheath. Sheath sizes ranged from 22F to 26 F (see table below for sizing). The valve was mounted directly onto the balloon in 29 cases. Seventeen of the patients were female with a median age of 17.5 years (8-72) and median weight of 60 kg (23.8-128). Most patients had a native RVOT (20/30) with 7 having a bioprosthetic valve and 3 having a conduit.

The valve was delivered successfully in all patients with 1 requiring a second valve and ultimately requiring surgery secondary to an RVOT gradient related to a complex RVOT membrane. No patients had increase in tricuspid valve regurgitation severity related to valve delivery. There were no vascular injuries even though 2 patients who were just over 30kg had a 26F sheath successfully used. All patients had the venotomy closed by a suture placed at the beginning of the procedure or using a figure-of-eight stitch. The short term outcomes were favorable with low post-procedure RVOT gradients and no significant pulmonary valve insufficiency.

The authors conclude that use of the large diameter 65 cm Gore Dryseal sheath facilitates delivery of the Sapien 3 and XT valves to dysfunctional RVOTs with no obvious tricuspid valve injury related to valve delivery. One of the main disadvantages to use of the Sapien valves in dysfunctional RVOTs is the risk of tricuspid valve injury, but using the technique described by Kenny et al, this risk can likely be eliminated making use of the Sapien valves much more appealing.


CHD Interventions Aug 2019

 

  1. Ductal closure in infants under 6 kg including premature infants using AmplatzerTM duct occluder type two additional sizes: a single-centre experience in South Africa.

Pepeta L, Greyling A, Nxele MF, Makrexeni Z, Jiyana S.

Cardiovasc J Afr. 2019 Aug 30;30:1-4. doi: 10.5830/CVJA-2019-044. [Epub ahead of print]

PMID: 31469384

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Select item 31471941

 

  1. Risk factors for infective endocarditis following transcatheter pulmonary valve replacement in patients with congenital heart disease.

Sadeghi S, Wadia S, Lluri G, Tarabay J, Fernando A, Salem M, Sinha S, Levi DS, Aboulhosn J.

Catheter Cardiovasc Interv. 2019 Aug 30. doi: 10.1002/ccd.28474. [Epub ahead of print]

PMID: 31471941

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Select item 31471939

 

  1. Initial experience with vascular plug devices for mechanical thrombectomy in symptomatic neonates and infants.

McGovern E, Qureshi AM, Goldstein BH.

Catheter Cardiovasc Interv. 2019 Aug 30. doi: 10.1002/ccd.28486. [Epub ahead of print]

PMID: 31471939

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Select item 31432698

 

  1. Intermediate outcomes of transcatheter pulmonary valve replacement with the Edwards Sapien 3 valve – German experience.

Lehner A, Dashkalova T, Ulrich S, Fernandez Rodriguez S, Mandilaras G, Jakob A, Dalla-Pozza R, Fischer M, Schneider H, Tarusinov G, Kampmann C, Hofbeck M, Dähnert I, Kanaan M, Haas NA.

Expert Rev Med Devices. 2019 Aug 30:1-6. doi: 10.1080/17434440.2019.1653180. [Epub ahead of print]

PMID: 31432698

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Select item 31480262

 

  1. Transapical Mitral Melody Valve-in-Valve Implantation in a Child: An Interesting Alternative for Failing Melody Valve.

Bautista-Rodriguez C, Michielon G, Di Salvo G, Aw TC, Butera G, Kempny A, Fraisse A.

JACC Cardiovasc Interv. 2019 Aug 26;12(16):e137-e138. doi: 10.1016/j.jcin.2019.06.005. Epub 2019 Jul 31. No abstract available.

PMID: 31377271

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Select item 31202951

 

  1. A Low Residual Pressure Gradient Yields Excellent Long-Term Outcome After Percutaneous Pulmonary Valve Implantation.

Georgiev S, Ewert P, Tanase D, Hess J, Hager A, Cleuziou J, Meierhofer C, Eicken A.

JACC Cardiovasc Interv. 2019 Aug 26;12(16):1594-1603. doi: 10.1016/j.jcin.2019.03.037. Epub 2019 Jun 12.

PMID: 31202951

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Select item 31444883

 

  1. Decompression of the thoracic duct: A novel transcatheter approach.

Smith CL, Hoffman TM, Dori Y, Rome JJ.

Catheter Cardiovasc Interv. 2019 Aug 24. doi: 10.1002/ccd.28446. [Epub ahead of print]

PMID: 31444883

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Select item 31455569

 

  1. Deep Tracheal Extubation Using Dexmedetomidine in Children With Congenital Heart Disease Undergoing Cardiac Catheterization: Advantages and Complications.

Gautam NK, Bober K, Pierre JA, Pawelek O, Griffin E.

Semin Cardiothorac Vasc Anesth. 2019 Aug 20:1089253219870628. doi: 10.1177/1089253219870628. [Epub ahead of print]

PMID: 31431142

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Select item 31431128

 

  1. Patient size parameters to guide use of the Impella device in pediatric patients.

Morray BH, Dimas VV, McElhinney DB, Puri K, Qureshi AM.

Catheter Cardiovasc Interv. 2019 Aug 19. doi: 10.1002/ccd.28456. [Epub ahead of print]

PMID: 31424167

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Select item 31424500

 

  1. Association between patient age at implant and outcomes after transcatheter pulmonary valve replacement in the multicenter Melody valve trials.

Armstrong AK, Berger F, Jones TK, Moore JW, Benson LN, Cheatham JP, Turner DR, Rhodes JF, Vincent JA, Zellers T, Lung TH, Eicken A, McElhinney DB.

Catheter Cardiovasc Interv. 2019 Aug 16. doi: 10.1002/ccd.28454. [Epub ahead of print]

PMID: 31419019

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Select item 31419027

 

  1. Use of 65 cm large caliber Dryseal sheaths to facilitate delivery of the Edwards SAPIEN valve to dysfunctional right ventricular outflow tracts.

Kenny D, Morgan GJ, Murphy M, AlAlwi K, Giugno L, Zablah J, Carminati M, Walsh K.

Catheter Cardiovasc Interv. 2019 Aug 13. doi: 10.1002/ccd.28409. [Epub ahead of print]

PMID: 31408262

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Select item 31428446

 

  1. Clinical outcomes after the endovascular treatments of pulmonary vein stenosis in patients with congenital heart disease.

Kurita Y, Baba K, Kondo M, Eitoku T, Kasahara S, Iwasaki T, Ohtsuki S, Tsukahara H.

Cardiol Young. 2019 Aug;29(8):1057-1065. doi: 10.1017/S1047951119001495. Epub 2019 Jul 9.

PMID: 31287033

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Select item 31244446

 

  1. Molding the shape of congenial and structural interventional cardiology: interviews with directors of major congresses.

Goreczny S, Hijazi ZM, Qureshi SA, Carminati M, Kenny D, Morgan GJ.

Cardiol Young. 2019 Aug;29(8):1009-1015. doi: 10.1017/S104795111900132X. Epub 2019 Jun 27.

PMID: 31244446

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Select item 31208473

 

  1. Comparison of drug eluting versus bare metal stents for pulmonary vein stenosis in childhood.

Khan A, Qureshi AM, Justino H.

Catheter Cardiovasc Interv. 2019 Aug 1;94(2):233-242. doi: 10.1002/ccd.28328. Epub 2019 May 8.

PMID: 31067002

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Select item 30926277

 

  1. Echocardiographic-fluoroscopic fusion imaging to guide device occlusion of a complex left ventricle-to-right atrium shunt.

Rodríguez-Zanella H, Sandoval JP, García-Montes JA, Zabal-Cerdeira C, Arias-Godínez JA.

Eur Heart J Cardiovasc Imaging. 2019 Aug 1;20(8):961. doi: 10.1093/ehjci/jez030. No abstract available.

PMID: 30824906

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Select item 30629127

 

  1. Giant coronary artery aneurysm in a patient with LEOPARD syndrome.

Bourgain M, Iriart X, Thambo JB, Cochet H.

Eur Heart J Case Rep. 2019 Aug 1. pii: ytz088. doi: 10.1093/ehjcr/ytz088. [Epub ahead of print] No abstract available.

PMID: 31369669

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Select item 30808198

 

  1. Percutaneous closure of a large atrial septal defect in a child with severe dextroscoliosis: A case report.

Linte A, Balanescu AR, Onorato E, Balanescu DV, Bojinca VC, Drakonaki E, Bojinca M, Balanescu SM.

Exp Ther Med. 2019 Aug;18(2):972-975. doi: 10.3892/etm.2018.6991. Epub 2018 Nov 19.

PMID: 31384332 Free PMC Article

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Select item 31423021

 

  1. Fenestration in the Fontan circulation as a strategy for chronic cardioprotection.

Saiki H, Kuwata S, Iwamoto Y, Ishido H, Taketazu M, Masutani S, Nishida T, Senzaki H.

Heart. 2019 Aug;105(16):1266-1272. doi: 10.1136/heartjnl-2018-314183. Epub 2019 Mar 2.

PMID: 30826770

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Select item 30054126

 

  1. Sudden death in transposition of the great arteries with atrial switch surgery: Autopsy evidence of acute myocardial ischemia despite normal coronary arteries.

Chaix MA, Chergui M, Leduc C, Khairy P.

Int J Cardiol. 2019 Aug 1;288:65-67. doi: 10.1016/j.ijcard.2019.02.026. Epub 2019 Feb 14.

PMID: 30808604

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Select item 31175525

 

  1. 3D-assessment of RVOT dimensions prior percutaneous pulmonary valve implantation: comparison of contrast-enhanced magnetic resonance angiography versus 3D steady-state free precession sequence.

Ebel S, Gottschling S, Buzan MTA, Grothoff M, Dähnert I, Wagner R, Gräfe D, Lurz P, Gutberlet M, Lücke C.

Int J Cardiovasc Imaging. 2019 Aug;35(8):1453-1463. doi: 10.1007/s10554-019-01578-w. Epub 2019 Apr 1.

PMID: 30937683 Free PMC Article

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Select item 31147145

 

  1. A novel braided biodegradable stent for use in congenital heart disease: Short-term results in porcine iliac artery.

Sun J, Sun K, Bai K, Chen S, Wang F, Zhao F, Hong N, Hu H.

J Biomed Mater Res A. 2019 Aug;107(8):1667-1677. doi: 10.1002/jbm.a.36682. Epub 2019 Apr 12.

PMID: 30917407

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Select item 30910389

 

 

  1. 3D printing and biocompatibility study of a new biodegradable occluder for cardiac defect.

Sun Y, Zhang X, Li W, Di Y, Xing Q, Cao Q.

J Cardiol. 2019 Aug;74(2):182-188. doi: 10.1016/j.jjcc.2019.02.002. Epub 2019 Mar 23.

PMID: 30910389

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Select item 31045294

 

  1. Biventricular Impella Use in Pediatric Patients with Severe Graft Dysfunction from Acute Rejection After Heart Transplantation.

Ankola AA, McAllister J, Turner ME, Zuckerman WA, Richmond ME, Addonizio LJ, Lee TM, Law SP.

Artif Organs. 2019 Aug 20. doi: 10.1111/aor.13558. [Epub ahead of print]

PMID: 31429943

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Select item 31482076

 

  1. Device Closure of Perimembranous Ventricular Septal Defect: Choosing Between Amplatzer Occluders.

Haddad RN, Daou L, Saliba Z.

Front Pediatr. 2019 Aug 16;7:300. doi: 10.3389/fped.2019.00300. eCollection 2019.

PMID: 31475122 Free PMC Article

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Select item 31248590

 

  1. Thrombosis after umbilical venous catheterisation: prospective study with serial ultrasound.

Dubbink-Verheij GH, Visser R, Roest AA, van Ommen CH, Te Pas AB, Lopriore E.

Arch Dis Child Fetal Neonatal Ed. 2019 Aug 7. pii: fetalneonatal-2018-316762. doi: 10.1136/archdischild-2018-316762. [Epub ahead of print]

PMID: 31391204

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Select item 31391347

 

  1. Endovascular coil embolization of a complex aortic arch pseudoaneurysm following arch stenting.

Meijs TA, Krings GJ, Molenschot MMC, Voskuil M.

Catheter Cardiovasc Interv. 2019 Aug 7. doi: 10.1002/ccd.28424. [Epub ahead of print]

PMID: 31389117

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Select item 31392837

 

  1. Percutaneous ASD closure of children weighing less than 10 kg.

Narin N, Baspinar O, Pamukcu O, Sunkak S, Tuncay A, Tasci O, Baykan A.

Acta Cardiol. 2019 Aug 3:1-6. doi: 10.1080/00015385.2019.1648711. [Epub ahead of print]

PMID: 31379261

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Select item 31377699

 

  1. Use of Near-Infrared Spectroscopy to Monitor Lower Extremity Perfusion in Pediatric Patients Undergoing Cardiac Catheterization.

Herbert CE, Leshko J, Morelli D, Amankwah E, Hanson J, Stapleton GE.

Pediatr Cardiol. 2019 Aug 2. doi: 10.1007/s00246-019-02179-z. [Epub ahead of print]

PMID: 31375852

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Select item 31373865

 

  1. Gradient over Melody valve in left AV valve position reduces with beta blockade.

Krasemann T, van de Woestijne P, van den Berg G.

Cardiol Young. 2019 Aug;29(8):1110-1111. doi: 10.1017/S1047951119001616. Epub 2019 Jul 23.

PMID: 31331407

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Select item 31304897

 

  1. Role of cardiovascular magnetic resonance end-systolic 3D-SSFP sequence in repaired tetralogy of Fallot patients eligible for transcatheter pulmonary valve implantation.

Leonardi B, Secinaro A, Perrone MA, Curione D, Napolitano C, Gagliardi MG.

Int J Cardiovasc Imaging. 2019 Aug;35(8):1525-1533. doi: 10.1007/s10554-019-01630-9. Epub 2019 Jun 3.

PMID: 31161492

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Select item 30937683

 

  1. Transthoracic Device Closure, Transcatheter Device Closure, and Surgical Repair via Right Submammary Thoracotomy for Restrictive Ventricular Septal Defect, a Respective Comparative Study.

Chen Q, Wu WX, Huang JS, Chen LW, Fang GH.

J Invest Surg. 2019 Aug 1:1-6. doi: 10.1080/08941939.2019.1645247. [Epub ahead of print]

PMID: 31366250

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Select item 30804174

 

  1. Percutaneous transcatheter closure of an aorto-cardiac fistula in a six-year-old Warmblood mare with atrial fibrillation.

Vernemmen I, De Clercq D, Decloedt A, Schauvliege S, Taeymans Y, De Wolf D, van Loon G.

J Vet Cardiol. 2019 Aug;24:78-84. doi: 10.1016/j.jvc.2019.06.003. Epub 2019 Jun 20.

PMID: 31405558

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Select item 31378242

 

  1. Retraction Note to: Primary Draining Vein Stenting for Obstructive Total Anomalous Pulmonary Venous Connection in Neonates with Right Atrial Isomerism and Functional Single Ventricle Improves Outcome.

Kitano M, Hoashi T, Kakuta T, Fujimoto K, Miyake A, Kurosaki KI, Ichikawa H, Shiraishi I.

Pediatr Cardiol. 2019 Aug;40(6):1322. doi: 10.1007/s00246-019-02131-1.

PMID: 31218372

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Select item 31214731

 

  1. Relationship Between Time to Left Atrial Decompression and Outcomes in Patients Receiving Venoarterial Extracorporeal Membrane Oxygenation Support: A Multicenter Pediatric Interventional Cardiology Early-Career Society Study.

Zampi JD, Alghanem F, Yu S, Callahan R, Curzon CL, Delaney JW, Gray RG, Herbert CE, Leahy RA, Lowery R, Pasquali SK, Patel PM, Porras D, Shahanavaz S, Thiagarajan RR, Trucco SM, Turner ME, Veeram Reddy SR, West SC, Whiteside W, Goldstein BH.

Pediatr Crit Care Med. 2019 Aug;20(8):728-736. doi: 10.1097/PCC.0000000000001936.

PMID: 30985609

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Select item 31373121

 

 

ACHD Surgery

Congenital Heart Surgery Reviews of August 2019 Manuscripts

 

Adult Congenital Heart Disease: Current Early Expectations after Cardiac Transplantation.
Riggs KW, Zafar F, Radzi Y, Yu PJ, Bryant R 3rd, Morales DL.
Ann Thorac Surg. 2019 Aug 10. pii: S0003-4975(19)31167-1. doi: 10.1016/j.athoracsur.2019.06.067. [Epub ahead of print]
PMID: 31408642
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Select item 31493728

Take-Home Points:
• This large study of the UNOS database compared early outcomes after cardiac transplantation for patients with and without adult congenital heart disease.
• Post-transplant outcomes for ACHD patients have improved over the past decade despite ACHD patients having relatively more risk factors than non-ACHD patients.
• ACHD patients with few risk factors had comparable survival up to 5 years as non-ACHD patients.
• Further long-term follow-up may determine whether post-transplant survival in ACHD patients surpasses that of nACHD patients given the relatively younger age of ACHD at the time of transplantation.

Commentary from Dr. Jeremy Herrmann (Indianapolis), section editor of Congenital Heart Surgery Journal Watch: The authors sampled the United Network of Organ Sharing (UNOS) database for patients >17 years old with or without adult congenital heart disease (ACHD) who underwent cardiac transplantation between 2000-2018 and primarily evaluated 1-year post-transplant survival. A possible era effect was analyzed by grouping patients from 2000-2008 (early) and 2009-2018 (late) then comparing the late era with the non-adult congenital heart disease (nACHD) group.

Over 35,000 nACHD patients and over 1,100 ACHD patients were included in the analyses. It is unclear whether ACHD patients who underwent heart-liver transplants were included, but this is typically a very small proportion of heart transplant patients. Late era patients were slightly older (32 versus 37 years), slightly heavier (67.1 versus 71.3 kg), more often sensitized (23% versus 38%), and had longer waitlist times (95 versus 149 days). However, the late era group exhibited better 1-year and overall survival. Compared to nACHD patients, ACHD patients were younger (37 versus 57 years), more likely to be female (38% versus 26%), had fewer ventricular assist devices (14% versus 46%), greater incidence of sensitization 38% versus 29%), and longer waitlist times (149 versus 104 days). Multivariable analysis revealed risk factors for 1-year mortality in ACHD patients included decreased renal function, body mass index >25 kg/m2, total bilirubin >1.2 mg/dL, and graft ischemic time.

When comparing ACHD patients with nACHD patients, ACHD patients who had less than two risk factors had similar 1-year survival as nACHD patients. Moreover, ACHD patients with preserved renal and liver function had similar overall survival as all nACHD patients and possibly trending superior survival beyond 5 years post-transplant (Figure).

These findings demonstrate improved ACHD transplant outcomes over the past decade, which is even more remarkable especially considering the greater association of risk factors during that interval. Unfortunately, granular details such as inotrope use and aspects of other medical management are lacking in this large study. However, it is also interesting that ACHD patients (who are relatively younger) may have better long-term outcomes compared to the older nACHD patients. Hopefully, this finding may help instruct future revisions of UNOS listing criteria for ACHD patients. Finally, the authors postulate that wider utilitization of VADs in ACHD patients may help to mitigate preoperative risk factors and improve post-transplant outcomes.


CHD Surgery August 2019

 

 

  1. Parental emotional and hands-on work-Experiences of parents with a newborn undergoing congenital heart surgery: A qualitative study.

Thomi M, Pfammatter JP, Spichiger E.

J Spec Pediatr Nurs. 2019 Aug 30:e12269. doi: 10.1111/jspn.12269. [Epub ahead of print]

PMID: 31468697

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Select item 31471627

 

  1. Patent foramen ovale-related complications in left ventricular assist device patients: a reappraisal for cardiovascular professionals.

Bacich D, Fiorencis A, Braggion G, Zuin M, Rigatelli G.

J Artif Organs. 2019 Aug 28. doi: 10.1007/s10047-019-01128-0. [Epub ahead of print] Review.

PMID: 31463532

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Select item 31456467

 

  1. Translational value of partial resection of the pulmonary artery wall for congenital heart disease-induced bronchial compression.

Wu X, Zhu J, Liu H, Chen W, Wei Y, Guan X, Zhang Y, Tao P, Gao B.

J Int Med Res. 2019 Aug 28:300060519863964. doi: 10.1177/0300060519863964. [Epub ahead of print] No abstract available.

PMID: 31456467

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Select item 31455124

 

  1. Use of vasoactive agents in postoperative pediatric cardiac patients: Insights from a national database.

Loomba RS, Flores S.

Congenit Heart Dis. 2019 Aug 27. doi: 10.1111/chd.12837. [Epub ahead of print]

PMID: 31454161

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Select item 31439217

 

  1. Thromboembolic Risk After Atriopulmonary, Lateral Tunnel, and Extracardiac Conduit Fontan Surgery.

Deshaies C, Hamilton RM, Shohoudi A, Trottier H, Poirier N, Aboulhosn J, Broberg CS, Cohen S, Cook S, Dore A, Fernandes SM, Fournier A, Kay J, Mondésert B, Mongeon FP, Opotowsky AR, Proietti A, Ting J, Zaidi A, Khairy P; Alliance for Adult Research in Congenital Cardiology (AARCC).

J Am Coll Cardiol. 2019 Aug 27;74(8):1071-1081. doi: 10.1016/j.jacc.2019.06.051.

PMID: 31439217

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Select item 31452428

 

  1. The role of cardiac surgeons in online prenatal counselling for congenital heart disease.

Zhu Y, Zhang Y, Ding N, Zhao Y, Ye Z, Fan X, Liu Y, Shen L, Yi H, Li Z.

J Int Med Res. 2019 Aug 27:300060519869079. doi: 10.1177/0300060519869079. [Epub ahead of print] No abstract available.

PMID: 31452428

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Select item 31141490

 

  1. Aortic valve replacement for infective endocarditis in an adult with uncorrected tetralogy of Fallot and pulmonary atresia.

Toba S, Ito H, Futsuki A, Yamamoto N, Konuma T, Takao M, Ogihara Y, Shimpo H.

Gen Thorac Cardiovasc Surg. 2019 Aug 26. doi: 10.1007/s11748-019-01193-5. [Epub ahead of print]

PMID: 31452054

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Select item 31449703

 

  1. Repair of anomalous origin of left coronary artery without intramural course using an ultrasonic scalpel.

Nam LL, Zimmerman SL, Sekar P, Hibino N.

J Card Surg. 2019 Aug 26. doi: 10.1111/jocs.14213. [Epub ahead of print] No abstract available.

PMID: 31449693

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Select item 31449687

 

  1. Three-dimensional printing for surgical planning in complex congenital heart disease.

Vettukattil JJ, Mohammad Nijres B, Gosnell JM, Samuel BP, Haw MP.

J Card Surg. 2019 Aug 26. doi: 10.1111/jocs.14180. [Epub ahead of print]

PMID: 31449687

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Select item 31451536

 

  1. Postoperative Inhaled Nitric Oxide Does Not Decrease Length of Stay in Pediatric Cardiac Surgery Admissions.

Wong J, Loomba RS, Evey L, Bronicki RA, Flores S.

Pediatr Cardiol. 2019 Aug 24. doi: 10.1007/s00246-019-02187-z. [Epub ahead of print]

PMID: 31446473

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Select item 31444268

 

  1. Survival and Cardiopulmonary Resuscitation Hemodynamics Following Cardiac Arrest in Children With Surgical Compared to Medical Heart Disease.

Yates AR, Sutton RM, Reeder RW, Meert KL, Berger JT, Fernandez R, Wessel D, Newth CJ, Carcillo JA, McQuillen PS, Harrison RE, Moler FW, Pollack MM, Carpenter TC, Notterman DA, Dean JM, Nadkarni VM, Berg RA; Eunice Kennedy Shriver National Institute of Child Health and Human Development Collaborative Pediatric Critical Care Research Network.

Pediatr Crit Care Med. 2019 Aug 23. doi: 10.1097/PCC.0000000000002088. [Epub ahead of print]

PMID: 31453988

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Select item 31286753

 

  1. Cardiac CT in the Preoperative Diagnostics of Neonates with Congenital Heart Disease: Radiation Dose Optimization by Omitting Test Bolus or Bolus Tracking.

Schindler P, Kehl HG, Wildgruber M, Heindel W, Schülke C.

Acad Radiol. 2019 Aug 20. pii: S1076-6332(19)30368-X. doi: 10.1016/j.acra.2019.07.019. [Epub ahead of print]

PMID: 31444109 Free Article

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Select item 31434778

 

  1. Anesthesia for Pediatric Heart Transplantation: Are Patients With a Failing Hemi-Fontan- or Fontan-Physiology Different?

Mueller MF, Paul AC, Mann V, Koerner CM, Valeske K, Thul J, Mazhari N, Bauer J, Schranz D, Akintuerk H.

Semin Cardiothorac Vasc Anesth. 2019 Aug 20:1089253219870635. doi: 10.1177/1089253219870635. [Epub ahead of print]

PMID: 31431128

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Select item 31424167

 

  1. First pediatric HeartMate 3 implantation: US experience.

Bansal A, Akhtar F, Zwintscher NP, Young T, Patel R, Desai S.

J Card Surg. 2019 Aug 17. doi: 10.1111/jocs.14216. [Epub ahead of print]

PMID: 31421654

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Select item 31421653

 

  1. Aortic recoarctation and pseudoaneurysm five decades after repair.

Lim B, Forest SJ, Schultz ML, Lipsitz E, Michler RE.

J Card Surg. 2019 Aug 17. doi: 10.1111/jocs.14201. [Epub ahead of print]

PMID: 31421653

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Select item 31418527

 

  1. Ventricular assist device implantation in patients with a failing systemic right ventricle: a call to expand current practice.

Zandstra TE, Palmen M, Hazekamp MG, Meyns B, Beeres SLMA, Holman ER, Kiès P, Jongbloed MRM, Vliegen HW, Egorova AD, Schalij MJ, Tops LF.

Neth Heart J. 2019 Aug 16. doi: 10.1007/s12471-019-01314-y. [Epub ahead of print] Review.

PMID: 31420818

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Select item 31303246

 

  1. Study protocol: NITric oxide during cardiopulmonary bypass to improve Recovery in Infants with Congenital heart defects (NITRIC trial): a randomised controlled trial.

Schlapbach LJ, Horton SB, Long DA, Beca J, Erickson S, Festa M, d’Udekem Y, Alphonso N, Winlaw D, Johnson K, Delzoppo C, van Loon K, Gannon B, Fooken J, Blumenthal A, Young P, Jones M, Butt W, Schibler A; NITRIC Study Group, the Australian and New Zealand Intensive Care Society Clinical Trials Group (ANZICS CTG), the Paediatric Critical Care Research group (PCCRG) and the ANZICS Paediatric Study Group (PSG).

BMJ Open. 2019 Aug 15;9(8):e026664. doi: 10.1136/bmjopen-2018-026664.

PMID: 31420383 Free PMC Article

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Select item 31070841

 

  1. Contemporary Mid-term Outcomes in Pediatric Patients undergoing Vascular Ring Repair.

Binsalamah ZM, Ibarra C, John R, Zea-Vera R, Adachi I, Imamura M, McKenzie ED, Fraser CD Jr, Mery CM, Heinle JS.

Ann Thorac Surg. 2019 Aug 14. pii: S0003-4975(19)31177-4. doi: 10.1016/j.athoracsur.2019.06.076. [Epub ahead of print]

PMID: 31421105

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Select item 31421949

 

  1. Ventricular Dysfunction is a Critical Determinant of Mortality in Congenital Diaphragmatic Hernia.

Patel N, Lally PA, Kipfmueller F, Massolo AC, Luco M, Van Meurs KP, Lally KP, Harting MT; Congenital Diaphragmatic Hernia Study Group.

Am J Respir Crit Care Med. 2019 Aug 13. doi: 10.1164/rccm.201904-0731OC. [Epub ahead of print]

PMID: 31409095

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Select item 31408262

 

  1. Sub-acute neonatal hemochromatosis in an infant with hypoplastic left heart syndrome on ventricular assist device awaiting transplantation.

Tadros HJ, Gupta D, Childress M, Beasley G, Rubrecht AE, Shenoy A, Philip J, Bleiweis MS, Machado DS.

Pediatr Transplant. 2019 Aug 13:e13567. doi: 10.1111/petr.13567. [Epub ahead of print]

PMID: 31407854

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Select item 31462948

 

  1. Impact of preoperative management with subatmospheric therapy using nitrogen in neonates with congenital heart disease.

Rodríguez-Fanjul J, Bobillo-Pérez S, Girona-Alarcón M, Sánchez-de-Toledo J.

Rev Esp Cardiol (Engl Ed). 2019 Aug 13. pii: S1885-5857(19)30215-4. doi: 10.1016/j.rec.2019.07.002. [Epub ahead of print] English, Spanish. No abstract available.

PMID: 31420306

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Select item 31407139

 

  1. Adult Congenital Heart Disease: Current Early Expectations after Cardiac Transplantation.

Riggs KW, Zafar F, Radzi Y, Yu PJ, Bryant R 3rd, Morales DL.

Ann Thorac Surg. 2019 Aug 10. pii: S0003-4975(19)31167-1. doi: 10.1016/j.athoracsur.2019.06.067. [Epub ahead of print]

PMID: 31408642

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Select item 31493728

 

  1. Impact of congenital heart disease on outcomes after primary repair of esophageal atresia: a retrospective observational study using a nationwide database in Japan.

Ishimaru T, Fujiogi M, Michihata N, Matsui H, Fushimi K, Kawashima H, Fujishiro J, Yasunaga H.

Pediatr Surg Int. 2019 Aug 8. doi: 10.1007/s00383-019-04542-w. [Epub ahead of print]

PMID: 31396739

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Select item 31390945

 

  1. Outcomes associated with unplanned interstage cardiac interventions following Norwood palliation.

Castellanos DA, Ocampo EC, Gooden A, Wang Y, Qureshi AM, Heinle JS, Mery CM, Hill GD, Ghanayem NS.

Ann Thorac Surg. 2019 Aug 7. pii: S0003-4975(19)31088-4. doi: 10.1016/j.athoracsur.2019.06.041. [Epub ahead of print]

PMID: 31400339

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Select item 31400328

 

  1. Prognostic Value of a New Lung Ultrasound Score To Predict Intensive Care Unit Stay in Pediatric Cardiac Surgery.

Cantinotti M, Giordano R, Scalese M, Marchese P, Franchi E, Viacava C, Molinaro S, Assanta N, Koestenberger M, Kutty S, Gargani L, Ait-Ali L.

Ann Thorac Surg. 2019 Aug 7. pii: S0003-4975(19)31105-1. doi: 10.1016/j.athoracsur.2019.06.057. [Epub ahead of print]

PMID: 31400328

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Select item 31391105

 

  1. The quest for precision medicine: Unmeasured patient factors and mortality after congenital heart surgery.

Pasquali SK, Gaies M, Banerjee M, Zhang W, Donohue J, Russell M, Gaynor JW.

Ann Thorac Surg. 2019 Aug 6. pii: S0003-4975(19)31078-1. doi: 10.1016/j.athoracsur.2019.06.031. [Epub ahead of print]

PMID: 31398358

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Select item 31385565

 

  1. Corticosteroids for Congenital Heart Surgery: When Is a Negative Trial Not a Negative Trial?

Schwartz SM.

J Am Coll Cardiol. 2019 Aug 6;74(5):669-671. doi: 10.1016/j.jacc.2019.06.019. No abstract available.

PMID: 31370959

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Select item 31370958

 

 

  1. Corticosteroid Therapy in Neonates Undergoing Cardiopulmonary Bypass: Randomized Controlled Trial.

Graham EM, Martin RH, Buckley JR, Zyblewski SC, Kavarana MN, Bradley SM, Alsoufi B, Mahle WT, Hassid M, Atz AM.

J Am Coll Cardiol. 2019 Aug 6;74(5):659-668. doi: 10.1016/j.jacc.2019.05.060.

PMID: 31370958

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Select item 31333075

 

 

  1. Combined interventional procedure and cardiopulmonary bypass surgery in a dog with cor triatriatum dexter, patent foramen ovale, and pulmonary stenosis.

Marchesotti F, Rondelli V, Pesaresi M, Nicoli S, Vezzosi T, Auriemma E, Lanzillo G, Cuccio A, Khouri T, Dejong A, Domenech O.

J Vet Intern Med. 2019 Aug 5. doi: 10.1111/jvim.15580. [Epub ahead of print]

PMID: 31380593 Free Article

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Select item 31385861

 

  1. Effect of internal fixation of the sternum using bioabsorbable pins in small children.

Ando M.

J Card Surg. 2019 Aug 2. doi: 10.1111/jocs.14174. [Epub ahead of print]

PMID: 31374584

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Select item 31374583

 

  1. Arteriovenous fistula creation for hypoxia after single ventricle palliation: A single-institution experience and literature review.

Spearman AD, Kindel SJ, Woods RK, Ginde S.

Congenit Heart Dis. 2019 Aug 1. doi: 10.1111/chd.12828. [Epub ahead of print]

PMID: 31368206

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Select item 31260138

 

  1. Mixed reality holograms for heart surgery planning: first user experience in congenital heart disease.

Brun H, Bugge RAB, Suther LKR, Birkeland S, Kumar R, Pelanis E, Elle OJ.

Eur Heart J Cardiovasc Imaging. 2019 Aug 1;20(8):883-888. doi: 10.1093/ehjci/jey184.

PMID: 30534951

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Select item 31369669

 

  1. The Evolution of the Minimally Invasive Approach and Conventional Median Sternotomy for Coronary Artery Fistula Correction.

Song L, Dong Y, Wang B, Li J, Qi X, Gao X, Hua Z, Tao C, He B, Tao L.

Heart Lung Circ. 2019 Aug;28(8):1277-1282. doi: 10.1016/j.hlc.2018.06.1052. Epub 2018 Jul 18.

PMID: 30054126

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Select item 30863899

 

  1. Mid-term outcomes of individualized surgeries in patients with Ebstein’s anomaly.

Zhu J, Zhang L, Bao C, Xu F, Ding F, Mei J.

Heart Vessels. 2019 Aug;34(8):1332-1339. doi: 10.1007/s00380-019-01358-5. Epub 2019 Mar 8.

PMID: 30848337

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Select item 31402156

 

  1. Surgical results of unifocalization revision.

Mainwaring RD, Patrick WL, Rosenblatt TR, Ma M, Kamra K, Arunamata A, Hanley FL.

J Thorac Cardiovasc Surg. 2019 Aug;158(2):534-545.e1. doi: 10.1016/j.jtcvs.2018.09.135. Epub 2018 Nov 23.

PMID: 30982588

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Select item 30954300

 

  1. Pediatric Ventricular Assist Device.

Shin YR, Park YH, Park HK.

Korean Circ J. 2019 Aug;49(8):678-690. doi: 10.4070/kcj.2019.0163. Epub 2019 Jul 3. Review.

PMID: 31347320 Free PMC Article

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Select item 31372826

 

  1. Aspiration After Congenital Heart Surgery.

Raulston JEB, Smood B, Moellinger A, Heinemann A, Smith N, Borasino S, Law MA, Alten JA.

Pediatr Cardiol. 2019 Aug;40(6):1296-1303. doi: 10.1007/s00246-019-02153-9. Epub 2019 Jul 24.

PMID: 31342114

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Select item 31309235

 

  1. Oral Triiodothyronine Supplementation Decreases Low Cardiac Output Syndrome After Pediatric Cardiac Surgery.

Marwali EM, Caesa P, Darmaputri S, Sani AA, Roebiono PS, Fakhri D, Djer MM, Munasir ZM, Batubara JRL, Satroasmoro S, Portman MA, Haas NA.

Pediatr Cardiol. 2019 Aug;40(6):1238-1246. doi: 10.1007/s00246-019-02143-x. Epub 2019 Jul 15.

PMID: 31309235

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Select item 31240370

 

  1. Predicting Post-Fontan Length of Stay: The Limits of Measured Variables.

Martin BJ, McBrien A, Marchak BE, Atallah J, Al Aklabi M, Mackie AS.

Pediatr Cardiol. 2019 Aug;40(6):1208-1216. doi: 10.1007/s00246-019-02134-y. Epub 2019 Jun 22.

PMID: 31230092

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Select item 31177302

 

  1. Ventricular-Arterial Coupling in Children and Infants With Congenital Heart Disease After Cardiopulmonary Bypass Surgery: Observational Study.

Marinari E, Rizza A, Iacobelli R, Iodice F, Favia I, Romagnoli S, Di Chiara L, Ricci Z.

Pediatr Crit Care Med. 2019 Aug;20(8):753-758. doi: 10.1097/PCC.0000000000001982.

PMID: 31169761

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Select item 31162368

 

  1. Characteristics and Outcomes of Pediatric Patients Supported With Ventricular Assist Device-A Multi-Institutional Analysis.

Puri K, Anders MM, Tume SC, Cabrera AG, Heinle JS, Causey JC, Wang Y, Moffett BS, Shekerdemian LS.

Pediatr Crit Care Med. 2019 Aug;20(8):744-752. doi: 10.1097/PCC.0000000000001966.

PMID: 31162368

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Select item 31074070

 

 

  1. Berlin Heart EXCOR® pediatric ventricular assist device in a patient with Sotos syndrome: a case report.

Gravino R, Limongelli G, Petraio A, Masarone D, Russo MG, Maiello C, Verrengia M, De Paulis D, Pacileo G.

J Med Case Rep. 2019 Aug 31;13(1):286. doi: 10.1186/s13256-019-2190-9.

PMID: 31470900 Free PMC Article

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Select item 31473799

 

  1. Prophylactic Opening of the Pleural Cavity for Postoperative Drainage is a Risk Factor for Prolonged Pleural Effusion After a Fontan Operation.

Masaki N, Masahiro M, Matsuo S, Sai S.

Pediatr Cardiol. 2019 Aug 29. doi: 10.1007/s00246-019-02194-0. [Epub ahead of print]

PMID: 31468062

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Select item 31468061

 

  1. Repair of Superior Sinus Venosus Atrial Septal Defect Using a Modified Two-patch Technique.

Elzein C, Abdulkarim M, Abbas U, Vricella L, Ilbawi M.

Ann Thorac Surg. 2019 Aug 28. pii: S0003-4975(19)31246-9. doi: 10.1016/j.athoracsur.2019.07.023. [Epub ahead of print]

PMID: 31472131

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Select item 31463801

 

  1. Incidental finding of type A aortic dissection in a paediatric heart transplant recipient.

D’Addese L, Komarlu R, Zahka K.

Cardiol Young. 2019 Aug 27:1-3. doi: 10.1017/S1047951119001811. [Epub ahead of print]

PMID: 31451126

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Select item 31291775

 

  1. Long‑term outcome after surgical repair of anomalous origin of the left coronary artery from the pulmonary artery: 24 years of experience.

Kwiatkowska J, Herrador Rey A, Meyer-Szary J, Dorniak K, Ostrowska K, Wałdoch A, Kozłowski D, Dąbrowska-Kugacka A.

Kardiol Pol. 2019 Aug 23;77(7-8):716-718. doi: 10.33963/KP.14816. Epub 2019 Apr 29. No abstract available.

PMID: 31066728 Free Article

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Select item 31451394

 

  1. Percutaneous obliteration of the right ventricle to avoid coronary damage by sinusoids in patients with pulmonary atresia intact ventricular septum during staged single ventricle palliation.

Hubrechts J, Cools B, Brown SC, Eyskens B, Heying R, Boshoff D, Gewillig M.

Catheter Cardiovasc Interv. 2019 Aug 21. doi: 10.1002/ccd.28457. [Epub ahead of print]

PMID: 31433549

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Select item 31432626

 

  1. Risk Factors for Prolonged Pleural Effusion After Extracardiac Fontan Operation.

Kim G, Ko H, Byun JH, Lee HD, Kim H, Sung SC, Choi KH.

Pediatr Cardiol. 2019 Aug 21. doi: 10.1007/s00246-019-02183-3. [Epub ahead of print]

PMID: 31435694

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Select item 31444109

 

  1. Thoracotomy versus sternotomy for patent ductus arteriosus closure in preterm neonates.

Verhaegh AJFP, Accord RE, Kooi EMW, Arrigoni SC, Bos AF, Berger RMF, Ebels T.

Ann Thorac Surg. 2019 Aug 10. pii: S0003-4975(19)31168-3. doi: 10.1016/j.athoracsur.2019.06.068. [Epub ahead of print]

PMID: 31408645

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Select item 31401720

 

  1. Sex-Specific Differences in Ventricular Dimensions in Repaired Tetralogy of Fallot: A Retrospective Study.

Pettit KA, Francois CJ, Aggarwal NR, Hess TM, Bartlett HL.

Pediatr Cardiol. 2019 Aug 10. doi: 10.1007/s00246-019-02181-5. [Epub ahead of print]

PMID: 31401720

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Select item 31493728

 

  1. Early and Mid-term Outcomes in High-risk Single Ventricle Patients: Hybrid versus Norwood Palliation.

Sower CT, Romano JC, Yu S, Lowery R, Pasquali SK, Zampi JD.

Ann Thorac Surg. 2019 Aug 9. pii: S0003-4975(19)31161-0. doi: 10.1016/j.athoracsur.2019.06.061. [Epub ahead of print]

PMID: 31404546

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Select item 31399780

 

  1. Safety and efficacy of vasopressin following Fontan completion: A randomized pilot study.

Bigelow AM, Ghanayem NS, Thompson NE, Scott JP, Cassidy LD, Woods KJ, Woods RK, Mitchell ME, Hraŝka V, Hoffman GM.

Ann Thorac Surg. 2019 Aug 7. pii: S0003-4975(19)31101-4. doi: 10.1016/j.athoracsur.2019.06.053. [Epub ahead of print]

PMID: 31400337

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Select item 31400328

 

  1. The quest for precision medicine: Unmeasured patient factors and mortality after congenital heart surgery.

Pasquali SK, Gaies M, Banerjee M, Zhang W, Donohue J, Russell M, Gaynor JW.

Ann Thorac Surg. 2019 Aug 6. pii: S0003-4975(19)31078-1. doi: 10.1016/j.athoracsur.2019.06.031. [Epub ahead of print]

PMID: 31398358

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Select item 31383839

 

  1. Surgical Repair of Ebstein’s Anomaly Utilizing A Bicuspidization Approach.

Mainwaring RD, Rosenblatt TR, Lui GK, Ma M, Hanley FL.

Ann Thorac Surg. 2019 Aug 5. pii: S0003-4975(19)31071-9. doi: 10.1016/j.athoracsur.2019.06.026. [Epub ahead of print]

PMID: 31394091

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Select item 31379312

 

  1. Retrospective Comparison of the Supported and Unsupported Bovine Jugular Vein Conduit in Children.

Lueth ET, Gist KM, Burkett DA, Landeck BF, Brinton JT, Meier MR, Coffin JM, Schafer M, Jaggers J, Mitchell MB.

Ann Thorac Surg. 2019 Aug;108(2):567-573. doi: 10.1016/j.athoracsur.2019.03.021. Epub 2019 Apr 8.

PMID: 30974093

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Select item 30928547

 

  1. Early Insight Into In Vivo Recellularization of Cell-Free Allogenic Heart Valves.

Sarikouch S, Theodoridis K, Hilfiker A, Boethig D, Laufer G, Andreas M, Cebotari S, Tudorache I, Bobylev D, Neubert L, Teiken K, Robertus JL, Jonigk D, Beerbaum P, Haverich A, Horke A.

Ann Thorac Surg. 2019 Aug;108(2):581-589. doi: 10.1016/j.athoracsur.2019.02.058. Epub 2019 Mar 28.

PMID: 30928547 Free Article

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Select item 30710524

 

  1. Truncus Arteriosus With Major Aortopulmonary Collateral Arteries.

Fujiwara K, Yoshizawa K, Kato O, Sakazaki H.

Ann Thorac Surg. 2019 Aug;108(2):e105-e106. doi: 10.1016/j.athoracsur.2018.12.051. Epub 2019 Jan 30.

PMID: 30710524

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Select item 31189430

 

  1. Predicting the pressure of the total cavopulmonary connection: clinical testing of a mathematical equation.

Di Molfetta A, Iacobelli R, Rotella S, Gagliardi MG, Amodeo A, Formigari R, Pasquini L, Iorio SF, Guccione P.

Cardiol Young. 2019 Aug;29(8):1066-1071. doi: 10.1017/S1047951119001513. Epub 2019 Jul 23.

PMID: 31331409

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Select item 31331407

 

  1. Biomarkers improve prediction of 30-day unplanned readmission or mortality after paediatric congenital heart surgery.

Brown JR, Stabler ME, Parker DM, Vricella L, Pasquali S, Leyenaar JK, Bohm AR, MacKenzie T, Parikh C, Jacobs ML, Jacobs JP, Everett AD.

Cardiol Young. 2019 Aug;29(8):1051-1056. doi: 10.1017/S1047951119001471. Epub 2019 Jul 10.

PMID: 31290383

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Select item 31288876

 

  1. True aneurysmal dilatation of a valved bovine jugular vein conduit after right ventricular outflow tract reconstruction: a rare complication.

Yoldaş T, Örün UA, Tak S.

Cardiol Young. 2019 Aug;29(8):1097-1098. doi: 10.1017/S1047951119001422. Epub 2019 Jul 8.

PMID: 31280726

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Select item 31250782

 

  1. Engineering Functional Cardiac Tissues for Regenerative Medicine Applications.

Tomov ML, Gil CJ, Cetnar A, Theus AS, Lima BJ, Nish JE, Bauser-Heaton HD, Serpooshan V.

Curr Cardiol Rep. 2019 Aug 1;21(9):105. doi: 10.1007/s11886-019-1178-9. Review.

PMID: 31367922

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Select item 31385382

 

  1. Ascending aorta and aortic root replacement (with or without valve sparing) in early childhood: surgical strategies and long-term outcomes.

Moreau de Bellaing A, Pontailler M, Bajolle F, Gaudin R, Murtuza B, Haydar A, Vouhé P, Bonnet D, Raisky O.

Eur J Cardiothorac Surg. 2019 Aug 1. pii: ezz210. doi: 10.1093/ejcts/ezz210. [Epub ahead of print]

PMID: 31369065

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Select item 31100109

 

  1. Valve-sparing aortic root and aortic arch replacement in a 5-year-old boy with Loeys-Dietz syndrome.

Ajmi H, Arifa N, Boughzela E, Ben Mime L.

Eur J Cardiothorac Surg. 2019 Aug 1;56(2):409-411. doi: 10.1093/ejcts/ezy446.

PMID: 30608517

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Select item 31486517

 

  1. Impact of pediatric cardiac surgery regionalization on health care utilization and mortality.

Sakai-Bizmark R, Mena LA, Kumamaru H, Kawachi I, Marr EH, Webber EJ, Seo HH, Friedlander SIM, Chang RR.

Health Serv Res. 2019 Aug;54(4):890-901. doi: 10.1111/1475-6773.13137. Epub 2019 Mar 27.

PMID: 30916392

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Select item 30826770

 

  1. Serial Changes in Right Ventricular Systolic Function Among Rejection-Free Children and Young Adults After Heart Transplantation.

Harrington JK, Richmond ME, Woldu KL, Pasumarti N, Kobsa S, Freud LR.

J Am Soc Echocardiogr. 2019 Aug;32(8):1027-1035.e2. doi: 10.1016/j.echo.2019.04.413. Epub 2019 Jun 13.

PMID: 31202590

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Select item 31147145

 

  1. Toward Opioid-Free Fast Track for Pediatric Congenital Cardiac Surgery.

Esfahanian M, Caruso TJ, Lin C, Kuan C, Purkey NJ, Maeda K, Tsui BCH.

J Cardiothorac Vasc Anesth. 2019 Aug;33(8):2362-2363. doi: 10.1053/j.jvca.2019.02.003. Epub 2019 Feb 10. No abstract available.

PMID: 30852093

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Select item 31045294

 

  1. The Konno aortoventriculoplasty after the Bentall procedure.

Nakamura Y, Aldoss O, Ricci M.

J Thorac Cardiovasc Surg. 2019 Aug;158(2):e49-e50. doi: 10.1016/j.jtcvs.2019.03.025. Epub 2019 Mar 22. No abstract available.

PMID: 31014666

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Select item 31005299

 

  1. Surgical results of unifocalization revision.

Mainwaring RD, Patrick WL, Rosenblatt TR, Ma M, Kamra K, Arunamata A, Hanley FL.

J Thorac Cardiovasc Surg. 2019 Aug;158(2):534-545.e1. doi: 10.1016/j.jtcvs.2018.09.135. Epub 2018 Nov 23.

PMID: 30982588

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Select item 30954300

 

  1. A long-term mechanical cavopulmonary support device for patients with Fontan circulation.

Granegger M, Thamsen B, Hubmann EJ, Choi Y, Beck D, Valsangiacomo Buechel E, Voutat M, Schweiger M, Meboldt M, Hübler M.

Med Eng Phys. 2019 Aug;70:9-18. doi: 10.1016/j.medengphy.2019.06.017. Epub 2019 Jun 29.

PMID: 31266678

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Select item 31441878

 

  1. Fetal Echocardiographic Parameters and Surgical Outcomes in Congenital Left-Sided Cardiac Lesions.

Edwards LA, Arunamata A, Maskatia SA, Quirin A, Bhombal S, Maeda K, Tacy TA, Punn R.

Pediatr Cardiol. 2019 Aug;40(6):1304-1313. doi: 10.1007/s00246-019-02155-7. Epub 2019 Jul 23.

PMID: 31338561

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Select item 31338560

 

  1. Procalcitonin Concentration Measured Within the First Days of Cardiac Surgery Is Predictive of Postoperative Infections in Neonates: A Case-Control Study.

Aryafar A, Di Marzio A, Guillard O, Pontailler M, Vicca S, Bojan M.

Pediatr Cardiol. 2019 Aug;40(6):1289-1295. doi: 10.1007/s00246-019-02150-y. Epub 2019 Jul 16.

PMID: 31312866

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  1. Impact of Left Atrial Decompression on Patient Outcomes During Pediatric Venoarterial Extracorporeal Membrane Oxygenation: A Case-Control Study.

Alghanem F, Balasubramanian S, Zampi JD.

Pediatr Cardiol. 2019 Aug;40(6):1266-1274. doi: 10.1007/s00246-019-02147-7. Epub 2019 Jun 27.

PMID: 31250046

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  1. Improved Left Ventricular Strain and Dyssynchrony After Pulmonary Artery Banding in an Infant with End-Stage Dilated Cardiomyopathy: Insights from Three-Dimensional Speckle Tracking.

Liu YH, Chen YS, Lin MT, Chen CA.

Pediatr Cardiol. 2019 Aug;40(6):1317-1319. doi: 10.1007/s00246-019-02138-8. Epub 2019 Jun 25.

PMID: 31240369

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  1. Right Atrial Appendage Aneurysm Resection to Cure Aneurysm-Related Atrial Tachyarrhythmia.

Zhang Y, Li XM, Jiang H, Jin YQ, Zhang FQ, Liu HJ, Ge HY.

Pediatr Cardiol. 2019 Aug;40(6):1144-1150. doi: 10.1007/s00246-019-02117-z. Epub 2019 May 31.

PMID: 31152184

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  1. A Quality Bundle to Support High-Risk Pediatric Ventricular Assist Device Implantation.

Knoll C, Chen S, Murray JM, Dykes JC, Yarlagadda VV, Rosenthal DN, Almond CS, Maeda K, Shin AY.

Pediatr Cardiol. 2019 Aug;40(6):1159-1164. doi: 10.1007/s00246-019-02123-1. Epub 2019 May 13.

PMID: 31087144

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  1. Ventricular Assist Devices in Pediatric Patients-Stasis or Progress?

Mazwi M, Schwartz SM, Jeewa A.

Pediatr Crit Care Med. 2019 Aug;20(8):784-785. doi: 10.1097/PCC.0000000000001994. No abstract available.

PMID: 31397813

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  1. Renal injury and recovery in pediatric patients after ventricular assist device implantation and cardiac transplant.

Hollander SA, Cantor RS, Sutherland SM, Koehl DA, Pruitt E, McDonald N, Kirklin JK, Ravekes WJ, Ameduri R, Chrisant M, Hoffman TM, Lytrivi ID, Conway J.

Pediatr Transplant. 2019 Aug;23(5):e13477. doi: 10.1111/petr.13477. Epub 2019 May 24.

PMID: 31124590

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  1. Ecthyma gangrenosum in a 3-year-old boy post-heart transplantation.

Fukui KO, Shoji K, Nagai Y, Shindo T, Hikosaka M, Kuwahara K, Ishiguro A, Miyairi I.

Transpl Infect Dis. 2019 Aug;21(4):e13131. doi: 10.1111/tid.13131. Epub 2019 Jun 30.

PMID: 31216602

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Fetal Cardiology Featured Articles

Fetal Cardiology Reviews of August 2019 Manuscripts

 

Congenital Heart Disease: Prenatal Diagnosis and Genetic Associations.
Hopkins MK, Dugoff L, Kuller JA.
Obstet Gynecol Surv. 2019 Aug;74(8):497-503. doi: 10.1097/OGX.0000000000000702.
PMID: 31418452
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Take Home Points:
• If congenital heart disease (CHD) is suspected on prenatal testing, parents should be referred for genetic counselling and/or genetic testing.
• There are several maternal risk factors for fetal CHD including advanced maternal age, diabetes mellitus, obesity and exposures (ex: alcohol and cocaine).
• Common genetic conditions associated with a prenatal diagnosis of CHD include chromosomal abnormalities and single-gene defect disorders.

Commentary from Dr. Charlotte Van Dorn (Rochester, MN), section editor of Pediatric Cardiology Journal Watch: Congenital heart disease (CHD) remains the most common birth defect (approximately 4-50 per 1000 live births) and is associated with several genetic syndromes. The early detection of CHD can allow for appropriate perinatal referrals and can improve survival in infants; early detection can also provide information regarding post-natal prognosis.
Risk factors for CHD include a family history of CHD, coexisting maternal disease (ex: diabetes mellitus), teratogen exposure (ex: lithium), advanced maternal age, monochorionic twinning, maternal obesity, maternal alcohol and drug use (ex: cocaine) and in vitro fertilization. Fetal echocardiography should be obtained if there is concern for an abnormal cardiac screening ultrasound (US) and/or predisposition to genetic CHD. The detection of other structural abnormalities by prenatal US increases the risk of genetic syndromes associated with CHD.
Chromosomal disorders (trisomy 13, 18 and 21) make up 8-10% of CHD. These conditions, especially trisomy 21, can be associated with advanced maternal age. Approximately 50% of infants with trisomy 21 will have CHD, while up to 85% of infants with trisomy 13 and up to 94% of infants with trisomy 18 will have CHD. More common defects include atrial and ventricular septal defects as well as patent ductus arteriosus. One third of patients with trisomy 13 and up to 24% of patients with trisomy 18 will have complex CHD.

Turner syndrome, involving complete or partial absence of one X chromosome, has a CHD incidence of 23-50%. This most commonly involves left-sided obstructive lesions such as bicuspid aortic valve (12-18%) and coarctation of the aorta (7-18%). CHD is also common in DiGeorge syndrome (22q11.2 deletion syndrome) occurring in up to 81% of patients. Infants born with conotruncal defects have a 50% likelihood of having DiGeorge Syndrome.
Single-gene defect disorders account for 3-5% of CHD and can often be associated with noncardiac malformations. Common single-gene defect disorders include Noonan Syndrome, Alagille Syndrome, and Holt-Oram Syndrome.
Perinatal genetic testing options include karyotype, chromosomal microarray (CMA) and amniocentesis. These tests do not detect every genetic disease or syndrome and for single-gene defects, specific gene panels and/or whole exome sequencing may be required. Genetic testing should not be performed without pretest genetic counselling.

Fetal cardiology Aug 2019

 

 

1. Umbilical Cord Blood Gas in Newborns with Prenatal Diagnosis of Congenital Heart Disease: Insight into In-Utero and Delivery Hemodynamics.

Adams AD, Aggarwal N, Iqbal SN, Tague L, Skurow-Todd K, McCarter R, Donofrio MT.

Pediatr Cardiol. 2019 Aug 30. doi: 10.1007/s00246-019-02189-x. [Epub ahead of print]

PMID: 31471626

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2. The accuracy of prenatal diagnosis of major congenital heart disease is increasing.

Lytzen R, Vejlstrup N, Bjerre J, Bjørn Petersen O, Leenskjold S, Keith Dodd J, Stener Jørgensen F, Søndergaard L.

J Obstet Gynaecol. 2019 Aug 28:1-8. doi: 10.1080/01443615.2019.1621814. [Epub ahead of print]

PMID: 31455124

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3. Strain and dyssynchrony in fetuses with congenital heart disease compared to normal controls using speckle tracking echocardiography (STE).

Drop MV, Möllers M, Hammer K, Oelmeier de Murcia K, Falkenberg MK, Braun J, Eveslage M, Köster HA, Klockenbusch W, Steinhard J, Schmitz R.

J Perinat Med. 2019 Aug 27;47(6):598-604. doi: 10.1515/jpm-2019-0073.

PMID: 31141490

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4. Fetal Complex Congenital Heart Disease Diagnosed Using Prenatal Ultrasound and Corrosion Casting for Large Vessels: A Report for Authentic Teaching by True Representation

An P, Wang Y, Xing LM, Feng W.

Balkan Med J. 2019 Aug 22;36(5):296-297. doi: 10.4274/balkanmedj.galenos.2019.2019.6.13. Epub 2019 Jul 9. No abstract available.

PMID: 31286753 Free PMC Article

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5. Genetic and genomics in congenital heart disease: a clinical review.

Saliba A, Figueiredo ACV, Baroneza JE, Afiune JY, Pic-Taylor A, Oliveira SF, Mazzeu JF.

J Pediatr (Rio J). 2019 Aug 14. pii: S0021-7557(19)30443-7. doi: 10.1016/j.jped.2019.07.004. [Epub ahead of print] Review.

PMID: 31421069 Free Article

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6. Endothelial to mesenchymal transition in the cardiogenesis and cardiovascular diseases.

Anbara T, Sharifi M, Aboutaleb N.

Curr Cardiol Rev. 2019 Aug 7. doi: 10.2174/1573403X15666190808100336. [Epub ahead of print]

PMID: 31393254

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7. Echocardiographic and pathomorphological features in fetuses with ductal-dependent congenital heart diseases.

Jiang H, Tang Q, Jiang Y, Li N, Tang X, Xia H.

Echocardiography. 2019 Aug 7. doi: 10.1111/echo.14452. [Epub ahead of print]

PMID: 31389092

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8. Alkylglycerol monooxygenase, a heterotaxy candidate gene, regulates left-right patterning via Wnt signaling.

Duncan AR, González DP, Del Viso F, Robson A, Khokha MK, Griffin JN.

Dev Biol. 2019 Aug 6. pii: S0012-1606(18)30809-1. doi: 10.1016/j.ydbio.2019.07.019. [Epub ahead of print]

PMID: 31398317

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9. Prenatal diagnosis of congenital heart defects: experience of the first Fetal Cardiology Unit in Mexico.

Cruz-Lemini M, Nieto-Castro B, Luna-Garcia J, Juarez-Martinez I, Martínez-Rivera M, Bermudez-Rojas ML, Rebolledo-Fernández C, Cruz-Martinez R.

J Matern Fetal Neonatal Med. 2019 Aug 6:1-6. doi: 10.1080/14767058.2019.1638905. [Epub ahead of print]

PMID: 31257961

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10. Akap12beta supports asymmetric heart development via modulating the Kupffer’s vesicle formation in zebrafish.

Kim JG, Kim HH, Bae SJ.

BMB Rep. 2019 Aug;52(8):525-530.

PMID: 31383248 Free Article

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11. DGCR8 expression is altered in children with congenital heart defects.

Guo Z, Li B, Tian P, Li D, Zhang Y, Li Q, Fan T, Yue J, Guo Y.

Clin Chim Acta. 2019 Aug;495:25-28. doi: 10.1016/j.cca.2019.03.1619. Epub 2019 Mar 26.

PMID: 30926277

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12. New Aspects in the Diagnosis and Therapy of Fetal Hypoplastic Left Heart Syndrome.

Graupner O, Enzensberger C, Axt-Fliedner R.

Geburtshilfe Frauenheilkd. 2019 Aug;79(8):863-872. doi: 10.1055/a-0828-7968. Epub 2019 Aug 12.

PMID: 31423021 Free PMC Article

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13. Mitochondrial Network State Scales mDNA Genetic Dynamics.

Aryaman J, Bowles C, Jones NS, Johnston IG.

Genetics. 2019 Aug;212(4):1429-1443. doi: 10.1534/genetics.119.302423. Epub 2019 Jun 28.

PMID: 31253641 Free PMC Article

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14. Proteomics analysis indicated the protein expression pattern related to the development of fetal conotruncal defects.

Wu Y, Zhang J, Wang M, Yang L, Wang Y, Hu T, Liu A, Cheng Q, Fu Z, Zhang P, Cao L.

J Cell Physiol. 2019 Aug;234(8):13544-13556. doi: 10.1002/jcp.28033. Epub 2019 Jan 12.

PMID: 30635921

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15. Can Ultrasound in Early Gestation Improve Visualization of Fetal Cardiac Structures in Obese Pregnant Women?

Majeed A, Abuhamad A, Romary L, Sinkovskaya E.

J Ultrasound Med. 2019 Aug;38(8):2057-2063. doi: 10.1002/jum.14895. Epub 2018 Dec 18.

PMID: 30561065

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16. Clinical analysis of prenatal ultrasound diagnosis of fetal cardiovascular malformations in the first and second trimesters of pregnancy: A CARE-compliant article.

Han B, Li Y, Tang Y, Qu X, Wang F, Song H, Xu Y.

Medicine (Baltimore). 2019 Aug;98(33):e16822. doi: 10.1097/MD.0000000000016822.

PMID: 31415400 Free Article

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17. Single-cell analysis of cardiogenesis reveals basis for organ-level developmental defects.

de Soysa TY, Ranade SS, Okawa S, Ravichandran S, Huang Y, Salunga HT, Schricker A, Del Sol A, Gifford CA, Srivastava D.

Nature. 2019 Aug;572(7767):120-124. doi: 10.1038/s41586-019-1414-x. Epub 2019 Jul 24.

PMID: 31341279

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18. Congenital Heart Disease: Prenatal Diagnosis and Genetic Associations.

Hopkins MK, Dugoff L, Kuller JA.

Obstet Gynecol Surv. 2019 Aug;74(8):497-503. doi: 10.1097/OGX.0000000000000702.

PMID: 31418452

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19. Fetal cardiac abnormalities: Genetic etiologies to be considered.

Petracchi F, Sisterna S, Igarzabal L, Wilkins-Haug L.

Prenat Diagn. 2019 Aug;39(9):758-780. doi: 10.1002/pd.5480. Epub 2019 Jul 29.

PMID: 31087396

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20. Variation in a Left Ventricle-Specific Hand1 Enhancer Impairs GATA Transcription Factor Binding and Disrupts Conduction System Development and Function.

Vincentz JW, Firulli BA, Toolan KP, Arking DE, Sotoodehnia N, Wan J, Chen PS, de Gier-de Vries C, Christoffels VM, Rubart-von der Lohe M, Firulli AB.

Circ Res. 2019 Aug 30;125(6):575-589. doi: 10.1161/CIRCRESAHA.119.315313. Epub 2019 Aug 1.

PMID: 31366290

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21. Severe Pulmonary Stenosis or Atresia with Intact Ventricular Septum in the Fetus: The Natural History.

Gottschalk I, Strizek B, Menzel T, Herberg U, Breuer J, Brockmeier K, Geipel A, Gembruch U, Berg C.

Fetal Diagn Ther. 2019 Aug 27:1-9. doi: 10.1159/000502178. [Epub ahead of print]

PMID: 31454806

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22. An In-depth Perspective of Aortic Arch Branching in Fetal Vascular Rings Using Spatiotemporal Image Correlation Combined With High-definition Flow Imaging: Report of 4 Cases.

Tseng JJ, Peng HW, Jan SL.

J Ultrasound Med. 2019 Aug;38(8):2217-2224. doi: 10.1002/jum.14891. Epub 2018 Dec 11.

PMID: 30536443

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23. Feasibility of Non-invasive Fetal Electrocardiographic Interval Measurement in the Outpatient Clinical Setting.

Doshi AN, Mass P, Cleary KR, Moak JP, Funamoto K, Kimura Y, Khandoker AH, Krishnan A.

Pediatr Cardiol. 2019 Aug;40(6):1175-1182. doi: 10.1007/s00246-019-02128-w. Epub 2019 Jun 6.

PMID: 31172229

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Congenital Cardiovascular Anesthesia and Critical Care Featured Articles

CHD anesthesia and intensive care August 2019

 

 

1. Anesthesia for Pediatric Heart Transplantation: Are Patients With a Failing Hemi-Fontan- or Fontan-Physiology Different?

Mueller MF, Paul AC, Mann V, Koerner CM, Valeske K, Thul J, Mazhari N, Bauer J, Schranz D, Akintuerk H.

Semin Cardiothorac Vasc Anesth. 2019 Aug 20:1089253219870635. doi: 10.1177/1089253219870635. [Epub ahead of print]

PMID: 31431128

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2. Selection of cuffed endotracheal tube for children with congenital heart disease based on an ultrasound-based linear regression formula.

Zhang K, Ma RJ, Zheng JJ, Chen YQ, Zhang MZ.

J Clin Monit Comput. 2019 Aug;33(4):687-694. doi: 10.1007/s10877-018-0203-7. Epub 2018 Sep 28.

PMID: 30264220

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3. Comparison of intranasal midazolam, intranasal ketamine, and oral chloral hydrate for conscious sedation during paediatric echocardiography: results of a prospective randomised study.

Alp H, Elmacı AM, Alp EK, Say B.

Cardiol Young. 2019 Aug 27:1-7. doi: 10.1017/S1047951119001835. [Epub ahead of print]

PMID: 31451130

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4. Use of vasoactive agents in postoperative pediatric cardiac patients: Insights from a national database.

Loomba RS, Flores S.

Congenit Heart Dis. 2019 Aug 27. doi: 10.1111/chd.12837. [Epub ahead of print]

PMID: 31454161

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5. Postoperative Pain Management in Pediatric Patients Undergoing Cardiac Surgery: Where Are We Heading?

Pollak U, Bronicki RA, Achuff BJ, Checchia PA.

J Intensive Care Med. 2019 Aug 25:885066619871432. doi: 10.1177/0885066619871432. [Epub ahead of print]

PMID: 31446831

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6. Detection of early incomplete heparin reversal following congenital cardiac surgery: A single-center retrospective observational study.

Magunia H, Schenk S, Schlensak C, Icheva V, Rosenberger P, Straub A, Nowak-Machen M.

Thromb Res. 2019 Aug 18;182:33-38. doi: 10.1016/j.thromres.2019.08.008. [Epub ahead of print]

PMID: 31445451

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The CHIP Network Journal Watch Team

Konstantin Averin, MD, MS is an Associate Professor of Pediatrics at the University of Alberta and an Interventional Pediatric Cardiologist at the Stollery Children’s Hospital in Edmonton, Alberta. He received his medical degree from the Feinberg School of Medicine at Northwestern University in Chicago, IL. After medical school, he completed pediatrics residency, pediatric cardiology fellowship and sub-specialty training in pediatric and adult interventional cardiology at the Cincinnati Children’s Hospital in Cincinnati, OH. His clinical and research interests are focused on the percutaneous treatment of pediatric patients with congenital and acquired heart disease with a focus on patients with single ventricle physiology, transcatheter pulmonary valves, and pulmonary hypertension.

Dr. Leong Ming Chern “MC” is an adult congenital heart disease specialist at the National Heart Institute, Kuala Lumpur, Malaysia. He received his medical training at the University of Malaya and pediatric cardiology training at the National Heart Institute. His area of interest includes treatment of adult patients with congenital heart disease and pulmonary hypertension in congenital heart disease.

Dr. Damien Cullington, MBChB MRCP MD FESC is a consultant adult congenital cardiologist who works at Leeds General Infirmary, UK. In summer 2019, he will move over to the newly commissioned North West ACHD Service based in Liverpool, UK. Damien qualified in 2002 from the University of Liverpool and became a substantive consultant in 2016. Prior to this, he worked throughout the North of England and Yorkshire as a cardiology trainee. Damien was awarded a doctorate in medicine (MD) from the University of Hull in 2013 for his work in heart rate in patients with heart failure. He is a member of the Royal College of Physicians (London), Fellow of the European Society of Cardiology and honorary senior lecturer for the University of Leeds. His ACHD subspecialty clinical interests are heart failure, imaging and palliative care. He is regional organiser for ACHD training at Leeds and clinical governance lead for the Leeds congenital cardiac unit. His research interests and wide and far but particularly epidemiology, chronic heart failure in ACHD patients in all its guises, the systemic RV and the univentricle

Dr. Blanche Cupido is a consultant adult cardiologist working at Groote Schuur Hospital, UCT Private Academic Hospital and the University of Cape Town(UCT), South Africa. She completed her physician training in 2009 and her cardiology subspecialist training in 2013. She recently returned to SA after doing a Fellowship in Adult Congenital Heart Disease in Leeds, United Kingdom under the guidance of Dr Kate English. She has established a dedicated unit for Grown Up Congenital Heart Disease in Cape Town, South Africa. Her aim is to grow ACHD services in Sub-Saharan Africa and embark on GUCH research on the African continent.

Dr. Jeremy L. Herrmann is an Assistant Professor of Surgery in the Division of Thoracic and Cardiovascular Surgery at Indiana University. He specializes in pediatric and adult congenital cardiac surgery, and his clinical interests also include heart transplantation and mechanical circulatory support. His hospital affiliations include Indiana University Health Riley Hospital for Children and Methodist Hospital as well as Peyton Manning Children’s Hospital at St. Vincent Hospital in Indianapolis

Maan Jokhadar is a cardiologist and associate professor of medicine at Emory University in Atlanta, Georgia. He is board certified in internal medicine, cardiovascular disease, advanced heart failure/transplantation, adult congenital heart disease, and echocardiography. He is fellowship director for the Emory Adult Congenital Heart Disease training program and Core Curriculum Director for the Emory general cardiology fellowship program. Dr Jokhadar graduated from the University Damascus School of Medicine in Syria and then went to Mayo Clinic in Rochester, Minnesota for internal medicine residency. He then completed cardiology and subspecialty training at Emory University, where he currently on faculty. Dr. Jokhadar has been the recipient of numerous teaching awards. He is married with 3 children.

Michael Ma, MD is an Assistant Professor in Cardiothoracic Surgery in the Division of Pediatric Cardiac Surgery at Stanford University. He specializes in pediatric and adult congenital cardiac surgery, with an emphasis on neonates, complex biventricular repair, and pulmonary artery reconstruction. His research lab investigates ex and in vivo translational models for complex congenital heart disease, to optimize future surgical and endovascular repair strategies.

Jeremy P. Moore MD MS FHRS is the Director of Clinical Research and faculty in Pediatric Cardiology and Adult Congenital Heart Disease at the University of California, Los Angeles. Dr. Moore received his medical degree from the Medical College of Virginia in 2003. He completed residency and fellowship at UCLA before pursuing his subspecialty training in Pediatric Electrophysiology at Vanderbilt University in 2009. Dr. Moore has been faculty at UCLA since 2010 and has since published numerous research manuscripts dealing with electrophysiologic aspects pertinent to congenital heart disease. Dr. Moore’s primary interest is the study of mechanisms of arrhythmia, and the development of novel electrophysiologic techniques for management of the adult patient with congenital heart disease

Dr. Mehul Patel MD, is a structural and adult congenital heart disease specialist and an interventional cardiologist. Dr. Patel earned his undergraduate and medical education from the Mumbai University, India. After completing his post-graduate training in Internal Medicine and Cardiology, he further trained in interventional cardiology at the Mount Sinai Medical Center, NYC, NY and Adult Congenital Heart Disease at the Texas Children’s Hospital, Texas Heart Institute, Baylor College of Medicine, Houston, TX. Dr. Patel worked as Chief of adult congenital heart disease, Assistant Professor at the Michigan State University, Grand Rapids, MI where he not only expanded the program, performing complex interventions and device implantations but also established the percutaneous pulmonary valve implantation (Melody Valve) Program. Due to his passion for treating structurally abnormal hearts, he did a dedicated year of Structural Heart Disease fellowship at Henry Ford Hospital, Detroit, MI where he worked with pioneers in this field before moving to North Carolina. He is proficient in performing transcatheter aortic valve replacement (TAVR), MitraClip, Watchman device implantation, percutaneous Mitral, Tricuspid and Pulmonary valve replacements along with a variety of interventions on congenital heart disease and pulmonary hypertension. Dr. Patel is ABIM board certified in Internal Medicine, Cardiology, Interventional cardiology and Adult Congenital Heart Disease. Dr. Patel has more than 50 peer reviewed publications and numerous abstracts to his credit. He serves as a Co-Editor-in-Chief for the CHiP Network journal watch. His wife, Khyati is a pediatric cardiac Electrophysiologist and they have a 9-year-old daughter. Dr. Patel is also an artist, likes music, yoga and plays badminton. His clinical areas of expertise and interests are: 1) Transcatheter therapies for Structural and Adult Congenital heart disease. 2) Complex device implantations.

Dr. Timothy Pirolli is an Assistant Professor of Surgery in the Division of Pediatric Cardiothoracic Surgery at University of Texas Southwestern Medical Center. He specializes in pediatric and adult congenital cardiac surgery. His hospital affiliations include Children’s Medical Center in Dallas, Parkland Memorial Hospital, and Clements University Hospital (UTSW).

Dr. Inga Voges, M.D. Consultant in Pediatric Cardiology, Lead Consultant Cardiovascular MRI. I trained in General Pediatrics and Pediatric Cardiology in Rostock (Germany) and Kiel (Germany) from 2002-2010 and did additional training in Adult Congenital Heart Disease (ACHD) in Kiel (Germany) which I finished in 2014. I specialized in Cardiovascular Magnetic Resonance Imaging (CMR) and have a further special interest in cardiomyopathies. Currently, I am working as a consultant pediatric and ACHD cardiologist at the University Hospital Schleswig-Holstein (Kiel, Germany) where I am responsible for the CMR imaging program in pediatric and ACHD patients and contribute to the care of patients with acquired and congenital heart disease. I received my MD from the Medical University Luebeck in 2006 (Germany) and finished my “Habilitation” (PhD equivalent; University Hospital Kiel, Germany) in 2014. Since 2016, I am the secretary of the Association for European Paediatric and Congenital Cardiology Imaging Working Group.

Dr. Gary Webb, M.D. is an Emeritus Professor of Pediatrics and Internal Medicine at the University of Cincinnati College of Medicine and,
from 2009-2016, the Director of the Adult Congenital Heart Program at Cincinnati Children’s Hospital Heart Institute. A graduate of McGill
University in Montréal, he interned at the Royal Victoria Hospital, and then trained in internal medicine and cardiology at the University of Toronto. From 1980-2004, he was co-director and then director of the Toronto Congenital Cardiac Center for Adults at Toronto General Hospital. He is a Fellow of the Royal College of Physicians and Surgeons of Canada in both internal medicine and cardiology. From 2004-2009, he was director of the Philadelphia Adult Congenital Heart Center at the University of Pennsylvania. Since 2016, he has been a consultant to Cincinnati Children’s Hospital, and has been responsible for the ACHD Learning Center, the Cardiology Fellow Testing Center, and the Congenital Heart Professionals International (CHIP) Network. Since 2017, he has resumed seeing patients on a part-time basis at the Toronto Congenital Cardiac Centre for Adults.

Wendy Whiteside, MD Wendy is Assistant Professor of Pediatrics and Associate Director of Interventional Pediatric Cardiology at the University of Michigan Congenital Heart Center, C.S. Mott Children’s Hospital. She obtained her medical degree from Albert Einstein College of Medicine in 2006 then completed pediatric residency at Children’s Hospital Oakland in Oakland, CA in 2009. She received
both her categorical and interventional pediatric cardiology training at the University of Michigan in Ann Arbor, MI. Her clinical and research interests include single ventricle physiology, transcatheter
pulmonary valves, and quality improvement within the cardiac catheterization laboratory.

About the Congenital Heart and Pediatric Cardiac Journal Watch

Congenital heart and pediatric cardiac Journal Watch was designed to make it easier for congenital heart and pediatric cardiac professionals to keep up with the literature in 6 subsections of congenital heart disease abstracts on a monthly basis: pediatric cardiology; congenital heart surgery; congenital  heart interventions; congenital/pediatric electrophysiology; fetal cardiology; and adult congenital heart disease.

We encourage your continued support as well as your valuable comments and feedback.

Learn More

Sincerely,

Dr. Gary Webb, MD and Dr. Mehul Patel
CHiP Network
Congenital Heart and Pediatic Cardiac Journal Watch Editorial Board

The Chip Network, the Congenital Heart International Professionals Network, aims to develop a single global list of all congenital and pediatric cardiac professionals.

We invite you to share this with your colleagues.